(Q43833824)

27 November 2017

Substrate-reduction therapy enhances the benefits of bone marrow transplantation in young mice with globoid cell leukodystrophy (English)

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27 November 2017

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Sangita Biswas

1

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27 November 2017

Steven M LeVine

series ordinal

2

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27 November 2017

language of work or name

English

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publication date

1 January 2002

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27 November 2017

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27 November 2017

51

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27 November 2017

1

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27 November 2017

40-47

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https://scigraph.springernature.com/pub.10.1203/00006450-200201000-00009

27 November 2017

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cites work

Cloning and expression of cDNA encoding human galactocerebrosidase, the enzyme deficient in globoid cell leukodystrophy

1 reference

https://api.crossref.org/works/10.1203%2F00006450-200201000-00009

Globoid cell leukodystrophy: Additional deficiency of psychosine galactosidase

21 January 2018

1 reference

https://api.crossref.org/works/10.1203%2F00006450-200201000-00009

Krabbe disease: genetic aspects and progress toward therapy

21 January 2018

1 reference

https://api.crossref.org/works/10.1203%2F00006450-200201000-00009

The future for treatment by bone marrow transplantation for adrenoleukodystrophy, metachromatic leukodystrophy, globoid cell leukodystrophy and Hurler syndrome

21 January 2018

1 reference

https://api.crossref.org/works/10.1203%2F00006450-200201000-00009

Neuropsychological outcomes of several storage diseases with and without bone marrow transplantation

21 January 2018

1 reference

https://api.crossref.org/works/10.1203%2F00006450-200201000-00009

Distribution and characterization of GFP(+) donor hematogenous cells in Twitcher mice after bone marrow transplantation

21 January 2018

1 reference

https://api.crossref.org/works/10.1203%2F00006450-200201000-00009

Molecular cloning and expression of cDNA for murine galactocerebrosidase and mutation analysis of the twitcher mouse, a model of Krabbe's disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1203%2F00006450-200201000-00009

The twitcher mouse: a model for Krabbe disease and for experimental therapies

21 January 2018

1 reference

https://api.crossref.org/works/10.1203%2F00006450-200201000-00009

Hematopoietic cell transplantation in murine globoid cell leukodystrophy (the twitcher mouse): effects on levels of galactosylceramidase, psychosine, and galactocerebrosides

21 January 2018

1 reference

https://api.crossref.org/works/10.1203%2F00006450-200201000-00009

Effect of bone marrow transplantation on enzyme levels and clinical course in the neurologically affected twitcher mouse

21 January 2018

1 reference

https://api.crossref.org/works/10.1203%2F00006450-200201000-00009

Donor-derived cells in the central nervous system of twitcher mice after bone marrow transplantation.

21 January 2018

1 reference

https://api.crossref.org/works/10.1203%2F00006450-200201000-00009

Chemotherapy by slowing glucosphingolipid synthesis

21 January 2018

1 reference

https://api.crossref.org/works/10.1203%2F00006450-200201000-00009

Glycosyltransferases of rat brain that make cerebrosides: substrate specificity, inhibitors, and abnormal products

21 January 2018

1 reference

https://api.crossref.org/works/10.1203%2F00006450-200201000-00009

Treating glucosphingolipid disorders by chemotherapy: use of approved drugs and over-the-counter remedies

21 January 2018

1 reference

https://api.crossref.org/works/10.1203%2F00006450-200201000-00009

Delayed symptom onset and increased life expectancy in Sandhoff disease mice treated with N-butyldeoxynojirimycin.

21 January 2018

1 reference

https://api.crossref.org/works/10.1203%2F00006450-200201000-00009

New therapeutic prospects for the glycosphingolipid lysosomal storage diseases.

21 January 2018

1 reference

https://api.crossref.org/works/10.1203%2F00006450-200201000-00009

Novel oral treatment of Gaucher's disease with N-butyldeoxynojirimycin (OGT 918) to decrease substrate biosynthesis.

21 January 2018

1 reference

https://api.crossref.org/works/10.1203%2F00006450-200201000-00009

Cycloserine-induced decrease of cerebroside in myelin.

21 January 2018

1 reference

https://api.crossref.org/works/10.1203%2F00006450-200201000-00009

Biochemistry and neuropathology of mice doubly deficient in synthesis and degradation of galactosylceramide.

21 January 2018

1 reference

https://api.crossref.org/works/10.1203%2F00006450-200201000-00009

Enhanced survival in Sandhoff disease mice receiving a combination of substrate deprivation therapy and bone marrow transplantation.

21 January 2018

1 reference

https://api.crossref.org/works/10.1203%2F00006450-200201000-00009

IL-6 deficiency allows for enhanced therapeutic value after bone marrow transplantation across a minor histocompatibility barrier in the twitcher (globoid cell leukodystrophy) mouse.

21 January 2018

1 reference

https://api.crossref.org/works/10.1203%2F00006450-200201000-00009

Prolonged survival and remyelination after hematopoietic cell transplantation in the twitcher mouse.

21 January 2018

1 reference

https://api.crossref.org/works/10.1203%2F00006450-200201000-00009

Hematopoietic cell transplantation after administration of high-dose busulfan in murine globoid cell leukodystrophy (the twitcher mouse).

21 January 2018

1 reference

https://api.crossref.org/works/10.1203%2F00006450-200201000-00009

The turnover of myelin phospholipids in the adult and developing rat brain

21 January 2018

1 reference

https://api.crossref.org/works/10.1203%2F00006450-200201000-00009

The turnover of myelin phosphatidylcholine and sphingomyelin in the adult rat brain.

21 January 2018

1 reference

https://api.crossref.org/works/10.1203%2F00006450-200201000-00009

Bone marrow transplantation for globoid cell leukodystrophy, adrenoleukodystrophy, metachromatic leukodystrophy, and Hurler syndrome

21 January 2018

1 reference

https://api.crossref.org/works/10.1203%2F00006450-200201000-00009

Bone marrow transplantation as effective treatment of central nervous system disease in globoid cell leukodystrophy, metachromatic leukodystrophy, adrenoleukodystrophy, mannosidosis, fucosidosis, aspartylglucosaminuria, Hurler, Maroteaux-Lamy, and S

21 January 2018

1 reference

https://api.crossref.org/works/10.1203%2F00006450-200201000-00009

Late-Onset Krabbe Disease (Globoid Cell Leukodystrophy): Clinical and Biochemical Features of 15 Cases

21 January 2018

1 reference

https://api.crossref.org/works/10.1203%2F00006450-200201000-00009

Molecular heterogeneity of Krabbe disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1203%2F00006450-200201000-00009

10.1203/00006450-200201000-00009

21 January 2018

Identifiers

DOI

1 reference

Dimensions Publication ID

27 November 2017

0 references

1 reference