(Q44980713)

7 December 2017

Mechanistic similarities between cultured cell models of cystic fibrosis and niemann-pick type C. (English)

1 reference

7 December 2017

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Nicole M White

1

1 reference

PubMed ID

15256387

7 December 2017

Deborah A Corey

series ordinal

2

1 reference

PubMed ID

15256387

7 December 2017

Thomas J Kelley

series ordinal

3

1 reference

7 December 2017

15 July 2004

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American Journal of Respiratory Cell and Molecular Biology

7 December 2017

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7 December 2017

31

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7 December 2017

538-543

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7 December 2017

5

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Inducible nitric oxide synthase expression is reduced in cystic fibrosis murine and human airway epithelial cells

7 December 2017

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2004-0117OC

Lack of inducible nitric oxide synthase in bronchial epithelium: a possible mechanism of susceptibility to infection in cystic fibrosis

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2004-0117OC

Cystic fibrosis transmembrane conductance regulator-dependent regulation of epithelial inducible nitric oxide synthase expression

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2004-0117OC

Reduced Smad3 protein expression and altered transforming growth factor-beta1-mediated signaling in cystic fibrosis epithelial cells

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2004-0117OC

In vivo alterations of IFN regulatory factor-1 and PIAS1 protein levels in cystic fibrosis epithelium

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2004-0117OC

Impaired Innate Host Defense Causes Susceptibility to Respiratory Virus Infections in Cystic Fibrosis

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2004-0117OC

Niemann-Pick disease type C

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2004-0117OC

Niemann-Pick C1 disease gene: homology to mediators of cholesterol homeostasis

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2004-0117OC

The evolution of liver disease in cystic fibrosis.

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2004-0117OC

Niemann-Pick disease type C: spectrum of HE1 mutations and genotype/phenotype correlations in the NPC2 group

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2004-0117OC

Alterations in cholesterol metabolism in cultured fibroblasts from patients with Niemann-Pick disease type C.

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2004-0117OC

Quantified increases of cholesterol, total lipid and globotriaosylceramide in filipin-positive Niemann-Pick type C fibroblasts

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2004-0117OC

Effect of a peroxysomal proliferator agent on intracellular cholesterol accumulation in cultured fibroblasts from Niemann-Pick type C disease patients

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2004-0117OC

Host defense against Pseudomonas aeruginosa requires ceramide-rich membrane rafts

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2004-0117OC

ABCA1: regulation, trafficking and association with heteromeric proteins

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2004-0117OC

Accumulation of RhoA, RhoB, RhoG, and Rac1 in fibroblasts from Tangier disease subjects suggests a regulatory role of Rho family proteins in cholesterol efflux

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2004-0117OC

Cystic fibrosis transmembrane regulator regulates uptake of sphingoid base phosphates and lysophosphatidic acid: modulation of cellular activity of sphingosine 1-phosphate

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2004-0117OC

Rme-1 regulates the recycling of the cystic fibrosis transmembrane conductance regulator

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2004-0117OC

Plasma membrane CFTR regulates RANTES expression via its C-terminal PDZ-interacting motif

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2004-0117OC

Hyperacidification of cellubrevin endocytic compartments and defective endosomal recycling in cystic fibrosis respiratory epithelial cells

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2004-0117OC

Association of cystic fibrosis with abnormalities in fatty acid metabolism.

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2004-0117OC

Essential fatty acid deficiency in relation to genotype in patients with cystic fibrosis

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2004-0117OC

A membrane lipid imbalance plays a role in the phenotypic expression of cystic fibrosis in cftr(-/-) mice

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2004-0117OC

21 January 2018

Identifiers

DOI

10.1165/RCMB.2004-0117OC

1 reference

7 December 2017

1 reference

PubMed ID

15256387