(Q45781361)

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:1824846%20AND%20SRC:MED&resulttype=core&format=json

18 September 2019

title

The human GM2 activator protein. A substrate specific cofactor of beta-hexosaminidase A (English)

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:1824846%20AND%20SRC:MED&resulttype=core&format=json

18 September 2019

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)52375-9

3 December 2022

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)52375-9

3 December 2022

author name string

E. M. Meier

1

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?resulttype=core&format=json&query=SRC%3AMED%20AND%20EXT_ID%3A1824846

3 December 2022

G. Schwarzmann

2

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?resulttype=core&format=json&query=SRC%3AMED%20AND%20EXT_ID%3A1824846

3 December 2022

W. Fürst

3

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?resulttype=core&format=json&query=SRC%3AMED%20AND%20EXT_ID%3A1824846

3 December 2022

K. Sandhoff

4

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?resulttype=core&format=json&query=SRC%3AMED%20AND%20EXT_ID%3A1824846

3 December 2022

language of work or name

English

0 references

publication date

1 January 1991

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:1824846%20AND%20SRC:MED&resulttype=core&format=json

18 September 2019

25 January 1991

1 reference

National Center for Biotechnology Information

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/esummary.fcgi?db=pubmed&retmode=json&id=1824846

full work available at URL

3 December 2022

http://intl.jbc.org/cgi/content/abstract/266/3/1879

online access status

open access

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?resulttype=core&format=json&query=SRC%3AMED%20AND%20EXT_ID%3A1824846

https://api.elsevier.com/content/article/PII:S0021925818523759?httpAccept=text/xml

3 December 2022

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)52375-9

https://api.elsevier.com/content/article/PII:S0021925818523759?httpAccept=text/plain

3 December 2022

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)52375-9

Journal of Biological Chemistry

3 December 2022

published in

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:1824846%20AND%20SRC:MED&resulttype=core&format=json

18 September 2019

volume

266

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:1824846%20AND%20SRC:MED&resulttype=core&format=json

18 September 2019

issue

3

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:1824846%20AND%20SRC:MED&resulttype=core&format=json

18 September 2019

page(s)

1879-1887

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:1824846%20AND%20SRC:MED&resulttype=core&format=json

Characterization of the phospholipid requirement of a rat liver beta-glucosidase

18 September 2019

cites work

1

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)52375-9

A difference in the specificities of human liver N-acetyl-beta-hexosaminidases A and B detected by their activities towards glycosaminoglycan oligosaccharides

3 December 2022

2

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)52375-9

Subunit structure of human hexosaminidase verified: interconvertibility of hexosaminidase isozymes

3 December 2022

3

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)52375-9

A rapid and sensitive method for the quantitation of microgram quantities of protein utilizing the principle of protein-dye binding

3 December 2022

4

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)52375-9

Activating Proteins for Ganglioside GM2Degradation by β-Hexosaminidase Isoenzymes in Tissue Extracts from Different Species

3 December 2022

5

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)52375-9

Isolation of two forms of an activator protein for the enzymic sphingomyelin degradation from human Gaucher spleen

3 December 2022

6

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)52375-9

AB variant of infantile GM2 gangliosidosis: deficiency of a factor necessary for stimulation of hexosaminidase A-catalyzed degradation of ganglioside GM2 and glycolipid GA2

3 December 2022

7

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)52375-9

Purification and Characterization of an Activator Protein for the Degradation of Glycolipids GM2and GA2by Hexosaminidase A

3 December 2022

8

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)52375-9

Complexing of Glycolipids and Their Transfer between Membranes by the Activator Protein for Degradation of Lysosomal Ganglioside GM2

3 December 2022

9

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)52375-9

Analysis of gangliosides using fast atom bombardment mass spectrometry.

3 December 2022

13

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)52375-9

The Activator of Cerebroside Sulphatase. Purification from Human Liver and Identification as a Protein

3 December 2022

14

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)52375-9

The activator of cerebroside-sulphatase. A model of the activation

3 December 2022

15

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)52375-9

A simple method for the isolation and purification of total lipides from animal tissues

3 December 2022

16

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)52375-9

The structure of lipid bilayers and the effects of general anaesthetics. An x-ray and neutron diffraction study.

3 December 2022

17

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)52375-9

Impaired degradation of keratan sulphate by Morquio A fibroblasts

3 December 2022

19

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)52375-9

Gaucher's disease: deficiency of 'acid' -glucosidase and reconstitution of enzyme activity in vitro

3 December 2022

20

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)52375-9

Immunological evidence for deficiency in an activator protein for sulfatide sulfatase in a variant form of metachromatic leukodystrophy

3 December 2022

21

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)52375-9

Ganglioside-composition of brain in Tay-Sachs disease: increased amounts of GD2 and N-acetyl-beta-D-galactosaminyl GD1a ganglioside

3 December 2022

23

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)52375-9

The cohydrolases in human spleen that stimulate glucosyl ceramide beta-glucosidase

3 December 2022

24

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)52375-9

Multilayers of Phospholipid Bimolecular Leaflets

3 December 2022

28

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)52375-9

A new variant of Type-AB GM2-gangliosidosis

3 December 2022

30

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)52375-9

Protein measurement with the Folin phenol reagent

3 December 2022

36

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)52375-9

Structure of full-length cDNA coding for sulfatide activator, a Co-beta-glucosidase and two other homologous proteins: two alternate forms of the sulfatide activator

3 December 2022

38

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)52375-9

Mutation in GM2-gangliosidosis B1 variant

3 December 2022

40

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)52375-9

Tay-Sachs Disease: Generalized Absence of a Beta-D- N -Acetylhexosaminidase Component

3 December 2022

41

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)52375-9

An evaluation of film detection methods for weak beta-emitters, particularly tritium

3 December 2022

43

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)52375-9

Composition of gangliosides and neutral glycosphingolipids of brain in classical Tay-Sachs and Sandhoff disease: more lyso-GM2 in Sandhoff disease?

3 December 2022

44

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)52375-9

Variation of beta-N-acetylhexosaminidase-pattern in Tay-Sachs disease

3 December 2022

45

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)52375-9

Enzyme alterations and lipid storage in three variants of Tay-Sachs disease

3 December 2022

47

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)52375-9

Specificity of human liver hexosaminidases A and B against glycosphingolipids GM2 and GA2. Purification of the enzymes by affinity chromatography employing specific elution

3 December 2022

48

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)52375-9

A simple and novel method for tritium labeling of gangliosides and other sphingolipids

3 December 2022

50

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)52375-9

Lysogangliosides: synthesis and use in preparing labeled gangliosides.

3 December 2022

51

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)52375-9

Incorporation of ganglioside analogs into fibroblast cell membranes. A spin-label study

3 December 2022

52

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)52375-9

Incorporation and metabolism of ganglioside GM2 in skin fibroblasts from normal and GM2 gangliosidosis subjects.

3 December 2022

53

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)52375-9

Genetic complementation in somatic cell hybrids of four variants of infantile GM2 gangliosidosis

3 December 2022

54

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)52375-9

Quantitative estimation of sialic acids. II. A colorimetric resorcinol-hydrochloric acid method

3 December 2022

55

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)52375-9

GM2-gangliosidosis B1 variant: a wide geographic and ethnic distribution of the specific beta-hexosaminidase alpha chain mutation originally identified in a Puerto Rican patient

3 December 2022

57

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)52375-9

N-acetyl-beta-hexosaminidase: role in the degradation of glycosaminoglycans

3 December 2022

60

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)52375-9

Release of Sphingomyelin Phosphodiesterase (Acid Sphingomyelinase) by Ammonium Chloride from CL 1D Mouse L-Cells and Human Fibroblasts. Partial Purification and Characterization of the Exported Enzymes

3 December 2022

61

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)52375-9

Calculation of the conformation of glycosphingolipids. 2. GM1- and GM2-gangliosides

3 December 2022

62

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)52375-9

Calculation of the conformation of glycosphingolipids. 1. Beta-D-glucosyl-N-(2-D-hydroxyoctadecanoyl)-D-dihydrosphingosine (glucosyl-ceramide) and alpha-D-N-acetylneuraminyl-(2----3)-beta-D-galactose

3 December 2022

63

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)52375-9

Characterization of some minor gangliosides in Tay-Sachs brains.

3 December 2022

64

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)52375-9

Neutron diffraction studies on phosphatidylcholine model membranes. II. Chain conformation and segmental disorder

3 December 2022

65

1 reference

https://api.crossref.org/works/10.1016/S0021-9258(18)52375-9

3 December 2022

Identifiers

1 reference