(Q45868213)

17 December 2017

title

Cystic fibrosis clinical trials (English)

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17 December 2017

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Alton E

1

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17 December 2017

Geddes D

series ordinal

2

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17 December 2017

language of work or name

English

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publication date

1 March 1998

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17 December 2017

Advanced Drug Delivery Reviews

published in

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17 December 2017

volume

30

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17 December 2017

issue

1-3

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17 December 2017

page(s)

205-217

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17 December 2017

Defective intracellular transport and processing of CFTR is the molecular basis of most cystic fibrosis

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7 January 2021

Mutations in CFTR associated with mild-disease-form Cl- channels with altered pore properties.

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7 January 2021

Increased bioelectric potential difference across respiratory epithelia in cystic fibrosis

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7 January 2021

Comparison of adherence of Pseudomonas aeruginosa to respiratory epithelial cells from cystic fibrosis patients and healthy subjects

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7 January 2021

Role of mutant CFTR in hypersusceptibility of cystic fibrosis patients to lung infections.

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7 January 2021

Cystic fibrosis airway epithelia fail to kill bacteria because of abnormal airway surface fluid.

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7 January 2021

Acute and long-term amiloride inhalation in cystic fibrosis lung disease. A rational approach to cystic fibrosis therapy

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7 January 2021

A pilot study of aerosolized amiloride for the treatment of lung disease in cystic fibrosis

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7 January 2021

Regulation of transepithelial ion transport and intracellular calcium by extracellular ATP in human normal and cystic fibrosis airway epithelium

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7 January 2021

Activation by extracellular nucleotides of chloride secretion in the airway epithelia of patients with cystic fibrosis

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7 January 2021

Submucosal glands are the predominant site of CFTR expression in the human bronchus

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7 January 2021

Expression of the cystic fibrosis gene in adult human lung

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7 January 2021

Immunocytochemical localization of the cystic fibrosis gene product CFTR

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7 January 2021

Long-term survival of the exon 10 insertional cystic fibrosis mutant mouse is a consequence of low level residual wild-type Cftr gene expression

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7 January 2021

Efficiency of gene transfer for restoration of normal airway epithelial function in cystic fibrosis

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7 January 2021

Transcriptional elements from the human SP-C gene direct expression in the primordial respiratory epithelium of transgenic mice

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7 January 2021

Non-invasive liposome-mediated gene delivery can correct the ion transport defect in cystic fibrosis mutant mice

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7 January 2021

Gene therapy for cystic fibrosis

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7 January 2021

Cystic fibrosis. Vehicles for gene therapy.

1 reference

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7 January 2021

Gene transfer to freshly isolated human respiratory epithelial cells in vitro using a replication-deficient adenovirus containing the human cystic fibrosis transmembrane conductance regulator cDNA.

1 reference

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7 January 2021

Safety and efficacy of repetitive adenovirus-mediated transfer of CFTR cDNA to airway epithelia of primates and cotton rats.

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7 January 2021

Adenovirus-mediated transfer of the CFTR gene to lung of nonhuman primates: toxicity study

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7 January 2021

In vivo transfer of the human cystic fibrosis transmembrane conductance regulator gene to the airway epithelium

1 reference

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7 January 2021

Inactivation of E2a in recombinant adenoviruses improves the prospect for gene therapy in cystic fibrosis.

1 reference

https://api.crossref.org/works/10.1016%2FS0169-409X%2897%2900117-8

7 January 2021

High-efficiency receptor-mediated delivery of small and large (48 kilobase gene constructs using the endosome-disruption activity of defective or chemically inactivated adenovirus particles.

1 reference

https://api.crossref.org/works/10.1016%2FS0169-409X%2897%2900117-8

7 January 2021

Increased expression of DNA cointroduced with nuclear protein in adult rat liver

1 reference

https://api.crossref.org/works/10.1016%2FS0169-409X%2897%2900117-8

7 January 2021

Systemic gene expression after intravenous DNA delivery into adult mice

1 reference

https://api.crossref.org/works/10.1016%2FS0169-409X%2897%2900117-8

7 January 2021

Relative ion permeability of normal and cystic fibrosis nasal epithelium

1 reference

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7 January 2021

Nasal application of the cationic liposome DC-Chol:DOPE does not alter ion transport, lung function or bacterial growth

1 reference

https://api.crossref.org/works/10.1016%2FS0169-409X%2897%2900117-8

7 January 2021

In vitro bioelectric properties of bronchial epithelium from transplanted lungs in recipients with cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0169-409X%2897%2900117-8

7 January 2021

Whole-cell chloride conductances in cultured brushed human nasal epithelial cells

1 reference

https://api.crossref.org/works/10.1016%2FS0169-409X%2897%2900117-8

7 January 2021

Development and biological applications of chloride-sensitive fluorescent indicators

1 reference

https://api.crossref.org/works/10.1016%2FS0169-409X%2897%2900117-8

7 January 2021

Defective acidification of intracellular organelles in cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0169-409X%2897%2900117-8

7 January 2021

Regulation of plasma membrane recycling by CFTR.

1 reference

https://api.crossref.org/works/10.1016%2FS0169-409X%2897%2900117-8

7 January 2021

Pseudomonas aeruginosa pili bind to asialoGM1 which is increased on the surface of cystic fibrosis epithelial cells

1 reference

https://api.crossref.org/works/10.1016%2FS0169-409X%2897%2900117-8

7 January 2021

Increased adherence of Staphylococcus aureus from cystic fibrosis lungs to airway epithelial cells

1 reference

https://api.crossref.org/works/10.1016%2FS0169-409X%2897%2900117-8

7 January 2021

Epithelial respiratory cells from cystic fibrosis patients do not possess specific Pseudomonas aeruginosa-adhesive properties

1 reference

https://api.crossref.org/works/10.1016%2FS0169-409X%2897%2900117-8

7 January 2021

Correction of the cystic fibrosis defect in vitro by retrovirus-mediated gene transfer

1 reference

https://api.crossref.org/works/10.1016%2FS0169-409X%2897%2900117-8

7 January 2021

Expression of cystic fibrosis transmembrane conductance regulator corrects defective chloride channel regulation in cystic fibrosis airway epithelial cells

1 reference

https://api.crossref.org/works/10.1016%2FS0169-409X%2897%2900117-8

7 January 2021

Defective regulation of outwardly rectifying Cl- channels by protein kinase A corrected by insertion of CFTR

1 reference

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7 January 2021

Expression of the human cystic fibrosis transmembrane conductance regulator gene in the mouse lung after in vivo intratracheal plasmid-mediated gene transfer

1 reference

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7 January 2021

Direct gene transfer of human CFTR into human bronchial epithelia of xenografts with E1-deleted adenoviruses.

1 reference

https://api.crossref.org/works/10.1016%2FS0169-409X%2897%2900117-8

7 January 2021

Human cystic fibrosis transmembrane conductance regulator directed to respiratory epithelial cells of transgenic mice

1 reference

https://api.crossref.org/works/10.1016%2FS0169-409X%2897%2900117-8

7 January 2021

Correction of the ion transport defect in cystic fibrosis transgenic mice by gene therapy

1 reference

https://api.crossref.org/works/10.1016%2FS0169-409X%2897%2900117-8

7 January 2021

Adenovirus-mediated transfer of the CFTR gene to lung of nonhuman primates: biological efficacy study.

1 reference

https://api.crossref.org/works/10.1016%2FS0169-409X%2897%2900117-8

7 January 2021

Lung gene therapy: in vivo adenovirus-mediated gene transfer to rhesus monkey airway epithelium

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7 January 2021

A novel cationic liposome reagent for efficient transfection of mammalian cells

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7 January 2021

Direct gene transfer with DNA-liposome complexes in melanoma: expression, biologic activity, and lack of toxicity in humans

1 reference

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7 January 2021

Cell-specific localization of CFTR mRNA shows developmentally regulated expression in human fetal tissues

1 reference

https://api.crossref.org/works/10.1016%2FS0169-409X%2897%2900117-8

7 January 2021

Expression of the cystic fibrosis gene in human foetal tissues

1 reference

https://api.crossref.org/works/10.1016%2FS0169-409X%2897%2900117-8

7 January 2021

Adenovirus-mediated gene transfer transiently corrects the chloride transport defect in nasal epithelia of patients with cystic fibrosis.

1 reference

https://api.crossref.org/works/10.1016%2FS0169-409X%2897%2900117-8

7 January 2021

Administration of an adenovirus containing the human CFTR cDNA to the respiratory tract of individuals with cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0169-409X%2897%2900117-8

7 January 2021

A controlled study of adenoviral-vector-mediated gene transfer in the nasal epithelium of patients with cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0169-409X%2897%2900117-8

7 January 2021

Liposome-mediated CFTR gene transfer to the nasal epithelium of patients with cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0169-409X%2897%2900117-8

7 January 2021

Evidence for safety and efficacy of DOTAP cationic liposome mediated CFTR gene transfer to the nasal epithelium of patients with cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0169-409X%2897%2900117-8

7 January 2021

A placebo-controlled study of liposome-mediated gene transfer to the nasal epithelium of patients with cystic fibrosis.

1 reference

https://api.crossref.org/works/10.1016%2FS0169-409X%2897%2900117-8

7 January 2021

Designing trials for gene therapy

1 reference

https://api.crossref.org/works/10.1016%2FS0169-409X%2897%2900117-8

7 January 2021

10.1016/S0169-409X(97)00117-8

Identifiers

DOI

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17 December 2017

release_hqskfq6c2bb7lpasvijkdc4dxq

Fatcat ID

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Fatcat

https://api.fatcat.wiki/v0/release/hqskfq6c2bb7lpasvijkdc4dxq

24 November 2022

mapped directly with Wikidata item

1 reference

17 December 2017