(Q46202551)

20 December 2017

title

Human prion protein (PrP) 219K is converted to PrPSc but shows heterozygous inhibition in variant Creutzfeldt-Jakob disease infection (English)

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20 December 2017

Creutzfeldt-Jakob disease

main subject

prion protein family

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5

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20 December 2017

author name string

Masaki Hizume

1

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20 December 2017

Atsushi Kobayashi

2

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20 December 2017

Kenta Teruya

3

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20 December 2017

Hiroaki Ohashi

4

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20 December 2017

Shirou Mohri

6

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20 December 2017

Tetsuyuki Kitamoto

7

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20 December 2017

language of work or name

English

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publication date

10 December 2008

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20 December 2017

Journal of Biological Chemistry

published in

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20 December 2017

volume

284

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20 December 2017

issue

6

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20 December 2017

page(s)

3603-3609

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20 December 2017

Degenerative disease of the central nervous system in New Guinea; the endemic occurrence of kuru in the native population

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1 reference

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A new variant of Creutzfeldt-Jakob disease in the UK.

21 January 2018

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Molecular biology and genetics of prion diseases

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Genetic predisposition to iatrogenic Creutzfeldt-Jakob disease

21 January 2018

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Homozygous prion protein genotype predisposes to sporadic Creutzfeldt–Jakob disease

21 January 2018

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Predictors of survival in sporadic Creutzfeldt-Jakob disease and other human transmissible spongiform encephalopathies.

21 January 2018

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Balancing selection at the prion protein gene consistent with prehistoric kurulike epidemics

21 January 2018

1 reference

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Codon 219 Lys allele of PRNP is not found in sporadic Creutzfeldt-Jakob disease

21 January 2018

1 reference

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Evidence for protein X binding to a discontinuous epitope on the cellular prion protein during scrapie prion propagation

21 January 2018

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Dominant-negative inhibition of prion replication in transgenic mice

21 January 2018

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The dominant-negative effect of the Q218K variant of the prion protein does not require protein X.

21 January 2018

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vCJD prion acquires altered virulence through trans-species infection

21 January 2018

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Follicular dendritic cell of the knock-in mouse provides a new bioassay for human prions

21 January 2018

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Novel missense variants of prion protein in Creutzfeldt-Jakob disease or Gerstmann-Sträussler syndrome

21 January 2018

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Humanized knock-in mice expressing chimeric prion protein showed varied susceptibility to different human prions

21 January 2018

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N-terminal sequence of prion protein is also integrated into kuru plaques in patients with Gerstmann-Sträussler syndrome.

21 January 2018

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Predicting susceptibility and incubation time of human-to-human transmission of vCJD.

21 January 2018

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Dissociation of pathological and molecular phenotype of variant Creutzfeldt-Jakob disease in transgenic human prion protein 129 heterozygous mice

21 January 2018

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Sensitive detection of pathological prion protein by cyclic amplification of protein misfolding

21 January 2018

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In vitro amplification and detection of variant Creutzfeldt-Jakob disease PrPSc.

21 January 2018

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Abbreviated incubation times for human prions in mice expressing a chimeric mouse-human prion protein transgene

21 January 2018

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Pathway complexity of prion protein assembly into amyloid

21 January 2018

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Soluble dimeric prion protein binds PrP(Sc) in vivo and antagonizes prion disease.

21 January 2018

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Scrapie prion liposomes and rods exhibit target sizes of 55,000 Da.

21 January 2018

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Cell-free formation of protease-resistant prion protein.

21 January 2018

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Models of amyloid seeding in Alzheimer's disease and scrapie: mechanistic truths and physiological consequences of the time-dependent solubility of amyloid proteins

21 January 2018

1 reference

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Vaccination with an attenuated Creutzfeldt-Jakob disease strain prevents expression of a virulent agent

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M809254200

Prion interference is due to a reduction in strain-specific PrPSc levels

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M809254200

21 January 2018

Identifiers

DOI

10.1074/JBC.M809254200

1 reference

20 December 2017

1 reference

20 December 2017