(Q46320247)

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:18849497%20AND%20SRC:MED&resulttype=core&format=json

15 January 2020

title

Preventive but not late amiloride therapy reduces morbidity and mortality of lung disease in betaENaC-overexpressing mice (English)

1 reference

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15 January 2020

1 reference

1 reference

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7

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15 January 2020

author name string

Zhe Zhou

1

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:18849497%20AND%20SRC:MED&resulttype=core&format=json

15 January 2020

Diana Treis

2

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:18849497%20AND%20SRC:MED&resulttype=core&format=json

15 January 2020

Susanne C Schubert

3

1 reference

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15 January 2020

Maria Harm

4

1 reference

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15 January 2020

Jolanthe Schatterny

5

1 reference

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15 January 2020

Stephanie Hirtz

6

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:18849497%20AND%20SRC:MED&resulttype=core&format=json

15 January 2020

Richard C Boucher

8

1 reference

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15 January 2020

Marcus A Mall

9

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:18849497%20AND%20SRC:MED&resulttype=core&format=json

15 January 2020

language of work or name

English

0 references

publication date

10 October 2008

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:18849497%20AND%20SRC:MED&resulttype=core&format=json

American Journal of Respiratory and Critical Care Medicine

15 January 2020

published in

1 reference

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15 January 2020

volume

178

1 reference

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15 January 2020

issue

12

1 reference

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15 January 2020

page(s)

1245-1256

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Identification of the cystic fibrosis gene: genetic analysis

15 January 2020

cites work

1 reference

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Demonstration That CFTR Is a Chloride Channel by Alteration of Its Anion Selectivity

21 January 2018

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Amiloride-sensitive epithelial Na+ channel is made of three homologous subunits

21 January 2018

1 reference

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CFTR as a cAMP-dependent regulator of sodium channels

21 January 2018

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Wild type but not deltaF508 CFTR inhibits Na+ conductance when coexpressed in Xenopus oocytes.

21 January 2018

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Na+ transport in cystic fibrosis respiratory epithelia. Abnormal basal rate and response to adenylate cyclase activation

21 January 2018

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The amiloride-inhibitable Na+ conductance is reduced by the cystic fibrosis transmembrane conductance regulator in normal but not in cystic fibrosis airways.

21 January 2018

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Evidence for periciliary liquid layer depletion, not abnormal ion composition, in the pathogenesis of cystic fibrosis airways disease

21 January 2018

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Modelling dysregulated Na+ absorption in airway epithelial cells with mucosal nystatin treatment

21 January 2018

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Increased airway epithelial Na+ absorption produces cystic fibrosis-like lung disease in mice

21 January 2018

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Finally, mice with CF lung disease

21 January 2018

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Development of chronic bronchitis and emphysema in beta-epithelial Na+ channel-overexpressing mice.

21 January 2018

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Role of cilia, mucus, and airway surface liquid in mucociliary dysfunction: lessons from mouse models

21 January 2018

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Amiloride and its analogs as tools in the study of ion transport

21 January 2018

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Eradication of early Pseudomonas aeruginosa infection

21 January 2018

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Regional differences in quantities of histochemically detectable mucosubstances in nasal, paranasal, and nasopharyngeal epithelium of the bonnet monkey

21 January 2018

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How much is there really? Why stereology is essential in lung morphometry

21 January 2018

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Lung inflammation early in cystic fibrosis: bugs are indicted, but the defense is guilty.

21 January 2018

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Pathophysiology and Management of Pulmonary Infections in Cystic Fibrosis

21 January 2018

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Identification of a key pathway required for the sterile inflammatory response triggered by dying cells

21 January 2018

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Effect of aerosolized recombinant human DNase on exacerbations of respiratory symptoms and on pulmonary function in patients with cystic fibrosis. The Pulmozyme Study Group

21 January 2018

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Cystic fibrosis transmembrane conductance regulator is an epithelial cell receptor for clearance of Pseudomonas aeruginosa from the lung.

21 January 2018

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Misassembled mutant DeltaF508 CFTR in the distal secretory pathway alters cellular lipid trafficking

21 January 2018

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Ceramide accumulation mediates inflammation, cell death and infection susceptibility in cystic fibrosis

21 January 2018

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Fenretinide corrects newly found ceramide deficiency in cystic fibrosis

21 January 2018

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Small-molecule correctors of defective DeltaF508-CFTR cellular processing identified by high-throughput screening.

21 January 2018

1 reference

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PTC124 is an orally bioavailable compound that promotes suppression of the human CFTR-G542X nonsense allele in a CF mouse model

21 January 2018

1 reference

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Pharmacological Properties of N-(3,5-Diamino-6-chloropyrazine-2-carbonyl)-N'-4-[4-(2,3-dihydroxypropoxy)phenyl]butyl-guanidine Methanesulfonate (552-02), a Novel Epithelial Sodium Channel Blocker with Potential Clinical Efficacy for Cystic Fibrosis L

21 January 2018

1 reference

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Effects of topically delivered benzamil and amiloride on nasal potential difference in cystic fibrosis.

21 January 2018

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Evaluation of second generation amiloride analogs as therapy for cystic fibrosis lung disease

21 January 2018

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Viral induction of a chronic asthma phenotype and genetic segregation from the acute response

21 January 2018

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Acute and chronic airway responses to viral infection: implications for asthma and chronic obstructive pulmonary disease

21 January 2018

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CYSTIC FIBROSIS OF THE PANCREAS AND ITS RELATION TO CELIAC DISEASE

21 January 2018

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Potential impact of newborn screening for cystic fibrosis on child survival: a systematic review and analysis

21 January 2018

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21 January 2018

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21 January 2018

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In vitro determination of the optimal particle size for nebulized aerosol delivery to infants

21 January 2018

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Cystic fibrosis transmembrane conductance regulator function is suppressed in cigarette smokers.

21 January 2018

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Mucociliary clearance in the airways

21 January 2018

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21 January 2018

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10.1164/RCCM.200803-442OC

21 January 2018

Identifiers

DOI

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:18849497%20AND%20SRC:MED&resulttype=core&format=json

15 January 2020

1 reference