(Q46522856)

22 December 2017

title

Niemann-Pick C1 expression is not regulated by the amount of cholesterol flowing through cells in the mouse (English)

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22 December 2017

author name string

William S Garver

1

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22 December 2017

Chonglun Xie

2

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22 December 2017

Joyce J Repa

3

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22 December 2017

Stephen D Turley

4

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22 December 2017

John M Dietschy

5

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22 December 2017

publication date

1 June 2005

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22 December 2017

Journal of Lipid Research

published in

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22 December 2017

volume

46

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22 December 2017

issue

8

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22 December 2017

page(s)

1745-1754

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22 December 2017

Niemann-Pick C1 disease gene: homology to mediators of cholesterol homeostasis

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Mutations in NPC1 highlight a conserved NPC1-specific cysteine-rich domain

21 January 2018

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Niemann-Pick C1 disease: correlations between NPC1 mutations, levels of NPC1 protein, and phenotypes emphasize the functional significance of the putative sterol-sensing domain and of the cysteine-rich luminal loop

21 January 2018

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Cholesterol is sequestered in the brains of mice with Niemann-Pick type C disease but turnover is increased.

21 January 2018

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Site-specific phosphorylation of tau accompanied by activation of mitogen-activated protein kinase (MAPK) in brains of Niemann-Pick type C mice

21 January 2018

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Cholesterol accumulation in tissues of the Niemann-pick type C mouse is determined by the rate of lipoprotein-cholesterol uptake through the coated-pit pathway in each organ

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The intracellular transport of low density lipoprotein-derived cholesterol is defective in Niemann-Pick type C fibroblasts

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Impaired ABCA1-dependent lipid efflux and hypoalphalipoproteinemia in human Niemann-Pick type C disease

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The Niemann-Pick C1 protein resides in a vesicular compartment linked to retrograde transport of multiple lysosomal cargo

21 January 2018

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Late endosomal membranes rich in lysobisphosphatidic acid regulate cholesterol transport

21 January 2018

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Binding between the Niemann-Pick C1 protein and a photoactivatable cholesterol analog requires a functional sterol-sensing domain

21 January 2018

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Sterol-modulated glycolipid sorting occurs in niemann-pick C1 late endosomes

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Cessation of rapid late endosomal tubulovesicular trafficking in Niemann-Pick type C1 disease

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21 January 2018

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Role of the low density lipoprotein receptor in the flux of cholesterol through the plasma and across the tissues of the mouse

21 January 2018

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A radioiodinated, intracellularly trapped ligand for determining the sites of plasma protein degradation in vivo

21 January 2018

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Kinetic parameters for high density lipoprotein apoprotein AI and cholesteryl ester transport in the hamster

21 January 2018

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Dissociation of tissue uptake of cholesterol ester from that of apoprotein A-I of rat plasma high density lipoprotein: selective delivery of cholesterol ester to liver, adrenal, and gonad

21 January 2018

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Rates of receptor-dependent and -independent low density lipoprotein uptake in the hamster

21 January 2018

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21 January 2018

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Cleavage of Structural Proteins during the Assembly of the Head of Bacteriophage T4

21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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Regulation of 3-hydroxy-3-methylglutaryl coenzyme A reductase activity in human fibroblasts by lipoproteins

21 January 2018

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Regulation of the activity of the low density lipoprotein receptor in human fibroblasts

21 January 2018

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Caveolin mRNA levels are up-regulated by free cholesterol and down-regulated by oxysterols in fibroblast monolayers

21 January 2018

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The SREBP pathway: regulation of cholesterol metabolism by proteolysis of a membrane-bound transcription factor

21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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Topology of SREBP cleavage-activating protein, a polytopic membrane protein with a sterol-sensing domain

21 January 2018

1 reference

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Accelerated degradation of HMG CoA reductase mediated by binding of insig-1 to its sterol-sensing domain

21 January 2018

1 reference

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Direct binding of cholesterol to the purified membrane region of SCAP: mechanism for a sterol-sensing domain

21 January 2018

1 reference

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10.1194/JLR.M500130-JLR200

21 January 2018

Identifiers

DOI

1 reference

22 December 2017

1 reference

22 December 2017