(Q46970707)

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:16510442%20AND%20SRC:MED&resulttype=core&format=json

17 January 2020

title

Manganese is the link between frataxin and iron-sulfur deficiency in the yeast model of Friedreich ataxia (English)

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:16510442%20AND%20SRC:MED&resulttype=core&format=json

17 January 2020

1 reference

5

1 reference

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17 January 2020

author name string

Verónica Irazusta

1

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:16510442%20AND%20SRC:MED&resulttype=core&format=json

17 January 2020

Elisa Cabiscol

2

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:16510442%20AND%20SRC:MED&resulttype=core&format=json

17 January 2020

Gemma Reverter-Branchat

3

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:16510442%20AND%20SRC:MED&resulttype=core&format=json

17 January 2020

Joaquim Ros

4

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:16510442%20AND%20SRC:MED&resulttype=core&format=json

17 January 2020

language of work or name

English

0 references

publication date

1 March 2006

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:16510442%20AND%20SRC:MED&resulttype=core&format=json

Journal of Biological Chemistry

17 January 2020

published in

1 reference

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17 January 2020

volume

281

1 reference

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17 January 2020

issue

18

1 reference

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17 January 2020

page(s)

12227-12232

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:16510442%20AND%20SRC:MED&resulttype=core&format=json

Friedreich's ataxia: autosomal recessive disease caused by an intronic GAA triplet repeat expansion

17 January 2020

cites work

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M511649200

Molecular insights into Friedreich's ataxia and antioxidant-based therapies

21 January 2018

1 reference

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An interaction between frataxin and Isu1/Nfs1 that is crucial for Fe/S cluster synthesis on Isu1.

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M511649200

Iron-sulfur cluster biosynthesis. Characterization of frataxin as an iron donor for assembly of [2Fe-2S] clusters in ISU-type proteins

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M511649200

Frataxin-mediated iron delivery to ferrochelatase in the final step of heme biosynthesis

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M511649200

Assembly of human frataxin is a mechanism for detoxifying redox-active iron

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M511649200

The expression of human mitochondrial ferritin rescues respiratory function in frataxin-deficient yeast.

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M511649200

Frataxin interacts functionally with mitochondrial electron transport chain proteins

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M511649200

Frataxin acts as an iron chaperone protein to modulate mitochondrial aconitase activity

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M511649200

Reversible redox-dependent modulation of mitochondrial aconitase and proteolytic activity during in vivo cardiac ischemia/reperfusion

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M511649200

Aconitase and mitochondrial iron-sulphur protein deficiency in Friedreich ataxia

21 January 2018

1 reference

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Mouse models for Friedreich ataxia exhibit cardiomyopathy, sensory nerve defect and Fe-S enzyme deficiency followed by intramitochondrial iron deposits

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M511649200

Regulation of mitochondrial iron accumulation by Yfh1p, a putative homolog of frataxin

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M511649200

Human frataxin maintains mitochondrial iron homeostasis in Saccharomyces cerevisiae.

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M511649200

Grx5 is a mitochondrial glutaredoxin required for the activity of iron/sulfur enzymes

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M511649200

Oxidative damage to specific proteins in replicative and chronological-aged Saccharomyces cerevisiae: common targets and prevention by calorie restriction

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M511649200

Asymmetric inheritance of oxidatively damaged proteins during cytokinesis

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M511649200

Saccharomyces cerevisiae has a single glutamate synthase gene coding for a plant-like high-molecular-weight polypeptide

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M511649200

Manganese superoxide dismutase in Saccharomyces cerevisiae acquires its metal co-factor through a pathway involving the Nramp metal transporter, Smf2p

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M511649200

Deletion of the yeast homologue of the human gene associated with Friedreich's ataxia elicits iron accumulation in mitochondria.

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M511649200

Mitochondrial control of iron homeostasis. A genome wide analysis of gene expression in a yeast frataxin-deficient strain

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M511649200

A non-essential function for yeast frataxin in iron-sulfur cluster assembly

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M511649200

Distinct physiological functions of thiol peroxidase isoenzymes in Saccharomyces cerevisiae

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M511649200

Superoxide radical and superoxide dismutases

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M511649200

Suppressors of superoxide dismutase (SOD1) deficiency in Saccharomyces cerevisiae. Identification of proteins predicted to mediate iron-sulfur cluster assembly

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M511649200

Dilated cardiomyopathy and neonatal lethality in mutant mice lacking manganese superoxide dismutase

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M511649200

Deletion of the mitochondrial carrier genes MRS3 and MRS4 suppresses mitochondrial iron accumulation in a yeast frataxin-deficient strain

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M511649200

Thioredoxin reductase system mediates iron binding in IscA and iron delivery for the iron-sulfur cluster assembly in IscU.

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M511649200

Mutations in PMR1 suppress oxidative damage in yeast cells lacking superoxide dismutase

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M511649200

Saccharomyces cerevisiae expresses three functionally distinct homologues of the nramp family of metal transporters

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M511649200

Activation of the iron regulon by the yeast Aft1/Aft2 transcription factors depends on mitochondrial but not cytosolic iron-sulfur protein biogenesis

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M511649200

Iron-sulfur clusters as biosensors of oxidants and iron

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M511649200

Aconitase couples metabolic regulation to mitochondrial DNA maintenance

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M511649200

Decreased expression of genes involved in sulfur amino acid metabolism in frataxin-deficient cells.

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M511649200

Actin glutathionylation increases in fibroblasts of patients with Friedreich's ataxia: a potential role in the pathogenesis of the disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M511649200

Friedreich ataxia: the oxidative stress paradox

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M511649200

Frataxin deficiency enhances apoptosis in cells differentiating into neuroectoderm

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M511649200

Friedreich's ataxia, no changes in mitochondrial labile iron in human lymphoblasts and fibroblasts: a decrease in antioxidative capacity?

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M511649200

Transition metal transport in yeast

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M511649200

Manganese action in brain function

21 January 2018

1 reference

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