(Q48546831)

12 February 2018

title

Inner ear pathology in the mucopolysaccharidosis VII mouse. (English)

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12 February 2018

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Kevin K Ohlemiller

1

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12 February 2018

Anne K Hennig

2

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12 February 2018

Jaclynn M Lett

3

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12 February 2018

Arnold F Heidbreder

4

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12 February 2018

Mark S Sands

5

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12 February 2018

publication date

1 July 2002

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12 February 2018

published in

Hearing Research

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12 February 2018

volume

169

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12 February 2018

issue

1-2

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12 February 2018

page(s)

69-84

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12 February 2018

Murine mucopolysaccharidosis type VII. Characterization of a mouse with beta-glucuronidase deficiency

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Tuning of the auditory brainstem OFF responses is complementary to tuning of the auditory brainstem ON response

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A single-base-pair deletion in the beta-glucuronidase gene accounts for the phenotype of murine mucopolysaccharidosis type VII

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The structural and functional consequences of acoustic injury in the cochlea and peripheral auditory system: a five year update

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7 January 2021

Beta glucuronidase deficiency: report of clinical, radiologic, and biochemical features of a new mucopolysaccharidosis

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7 January 2021

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7 January 2021

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7 January 2021

Degeneration of speech, language, and hearing in a patient with mucopolysaccharidosis VII.

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7 January 2021

10.1016/S0378-5955(02)00341-6

Identifiers

DOI

1 reference

12 February 2018

PubMed ID

12121741

1 reference

12 February 2018