(Q50656936)

20 June 2018

title

Pyrophosphate Supplementation Prevents Chronic and Acute Calcification in ABCC6-Deficient Mice. (English)

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20 June 2018

author

Jeanette Erdmann

13

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20 June 2018

author name string

Viola Pomozi

1

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20 June 2018

Christopher Brampton

2

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20 June 2018

Koen van de Wetering

3

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20 June 2018

Janna Zoll

4

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20 June 2018

Bianca Calio

5

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20 June 2018

Kevin Pham

6

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20 June 2018

Jesse B Owens

7

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20 June 2018

Joel Marh

8

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20 June 2018

Stefan Moisyadi

9

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20 June 2018

András Váradi

10

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20 June 2018

Ludovic Martin

11

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20 June 2018

Carolin Bauer

12

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20 June 2018

Zouhair Aherrahrou

14

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20 June 2018

Olivier Le Saux

15

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20 June 2018

language of work or name

English

0 references

publication date

14 April 2017

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20 June 2018

The American Journal of Pathology

published in

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20 June 2018

volume

187

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20 June 2018

issue

6

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20 June 2018

page(s)

1258-1272

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20 June 2018

describes a project that uses

ImageJ

1 reference

11 June 2022

https://www.ebi.ac.uk/europepmc/webservices/rest/PMC5455066/fullTextXML

inferred from PubMed Central ID database lookup

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22 June 2018

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22 June 2018

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22 June 2018

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22 June 2018

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22 June 2018

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22 June 2018

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22 June 2018

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22 June 2018

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22 June 2018

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A spectrum of ABCC6 mutations is responsible for pseudoxanthoma elasticum

22 June 2018

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Inorganic pyrophosphate generation and disposition in pathophysiology

22 June 2018

1 reference

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Inclusion of the hepatic locus control region, an intron, and untranslated region increases and stabilizes hepatic factor IX gene expression in vivo but not in vitro

22 June 2018

1 reference

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Mutations in ABCC6 cause pseudoxanthoma elasticum

22 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5455066

Mutations in a gene encoding an ABC transporter cause pseudoxanthoma elasticum

22 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5455066

Inorganic pyrophosphate in plasma in normal persons and in patients with hypophosphatasia, osteogenesis imperfecta, and other disorders of bone

22 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5455066

Functional Rescue of ABCC6 Deficiency by 4-Phenylbutyrate Therapy Reduces Dystrophic Calcification in Abcc6-/- Mice.

22 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5455066

ABCC6-mediated ATP secretion by the liver is the main source of the mineralization inhibitor inorganic pyrophosphate in the systemic circulation-brief report.

14 August 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5455066

Defective extracellular pyrophosphate metabolism promotes vascular calcification in a mouse model of Hutchinson-Gilford progeria syndrome that is ameliorated on pyrophosphate treatment

14 August 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5455066

Severe skeletal toxicity from protracted etidronate therapy for generalized arterial calcification of infancy.

14 August 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5455066

Quantification of the calcification phenotype of Abcc6-deficient mice with microcomputed tomography

14 August 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5455066

Daily peritoneal administration of sodium pyrophosphate in a dialysis solution prevents the development of vascular calcification in a mouse model of uraemia.

14 August 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5455066

Phosphate-induced vascular calcification: role of pyrophosphate and osteopontin

14 August 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5455066

Isolation from urine of pyrophosphate, a calcification inhibitor

14 August 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5455066

Mechanism of calcification: inhibitory role of pyrophosphate

14 August 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5455066

The distribution of Abcc6 in normal mouse tissues suggests multiple functions for this ABC transporter.

14 August 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5455066

Hydrodynamics-based transfection in animals by systemic administration of plasmid DNA.

14 August 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5455066

An Alternative Splice Variant inAbcc6, the Gene Causing Dystrophic Calcification, Leads to Protein Deficiency in C3H/He Mice

14 August 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5455066

New Dyscalc loci for myocardial cell necrosis and calcification (dystrophic cardiac calcinosis) in mice

30 November 2018

1 reference

12 December 2020

Acquired Pseudoxanthoma elasticum-like syndrome in beta-thalassaemia patients

1 reference

12 December 2020

Histochemical methods for calcium

1 reference

12 December 2020

Dysregulation of gene expression in ABCC6 knockdown HepG2 cells

1 reference

12 December 2020

Applied Pathology for Interventions of Coronary Chronic Total Occlusion.

1 reference

12 December 2020

Etidronate prevents, but does not reverse, ectopic mineralization in a mouse model of pseudoxanthoma elasticum (Abcc6-/- )

1 reference

12 December 2020

Inhibition of calcium oxalate monohydrate (COM) crystal growth by pyrophosphate, citrate and rat urine

1 reference

12 December 2020

10.1016/J.AJPATH.2017.02.009

Identifiers

DOI

1 reference

20 June 2018

PMC publication ID

5455066

1 reference

20 June 2018

PubMed publication ID

28416300

1 reference

20 June 2018