(Q53964474)

23 May 2018

title

High resolution respirometry of permeabilized skeletal muscle fibers in the diagnosis of neuromuscular disorders. (English)

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23 May 2018

author name string

W Sperl

1

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23 May 2018

D Skladal

2

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23 May 2018

E Gnaiger

3

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23 May 2018

M Wyss

4

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23 May 2018

U Mayr

5

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23 May 2018

J Hager

6

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23 May 2018

F N Gellerich

7

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23 May 2018

publication date

1 September 1997

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23 May 2018

Molecular and Cellular Biochemistry

published in

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23 May 2018

volume

174

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23 May 2018

issue

1-2

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23 May 2018

page(s)

71-78

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23 May 2018

https://scigraph.springernature.com/pub.10.1023/a:1006880529195

exact match

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cites work

A microspectrophotometric method for the determination of cytochrome oxidase.

1 reference

12 December 2020

The effect of oncotic pressure on heart muscle mitochondria

1 reference

12 December 2020

Variation in mitochondrial DNA levels in muscle from normal controls. Is depletion of mtDNA in patients with mitochondrial myopathy a distinct clinical syndrome

1 reference

12 December 2020

Is Kugelberg-Welander spinal muscular atrophy a fetal defect?

1 reference

12 December 2020

Fatty acid oxidation abnormalities in childhood-onset spinal muscular atrophy: primary or secondary defect(s)?

1 reference

12 December 2020

Carnitine deficiency, mitochondrial dysfunction and the heart. Identical defect of oxidative phosphorylation in muscle mitochondria in cardiomyopathy due to carnitine loss and in Duchenne muscular dystrophy

1 reference

12 December 2020

Secondary metabolic defects in spinal muscular atrophy type II

1 reference

12 December 2020

Measurement of totally activated pyruvate dehydrogenase complex activity in human muscle: evaluation of a useful assay

1 reference

12 December 2020

The gene for neuronal apoptosis inhibitory protein is partially deleted in individuals with spinal muscular atrophy

1 reference

12 December 2020

Clinical presentation of mitochondrial disorders in childhood.

1 reference

12 December 2020

A mitochondrial encephalomyopathy: the first case with an established defect at the level of coenzyme Q.

1 reference

12 December 2020

Mitochondrial oxidative phosphorylation in saponin-skinned human muscle fibers is stimulated by caffeine

1 reference

12 December 2020

Small scale preparation of skeletal muscle mitochondria, criteria of integrity, and assays with reference to tissue function.

1 reference

12 December 2020

Mitochondrial Myopathy Studies on Permeabilized Muscle Fibers1

1 reference

12 December 2020

Role of the mitochondrial DNA and calmitine in myopathies

1 reference

12 December 2020

Rapid isolation of muscle and heart mitochondria, the lability of oxidative phosphorylation and attempts to stabilize the process in vitro by taurine, carnitine and other compounds

1 reference

12 December 2020

Biochemical and molecular investigations in respiratory chain deficiencies

1 reference

12 December 2020

Down-regulation of mitochondrial mRNAs in the mdx mouse model for Duchenne muscular dystrophy

1 reference

12 December 2020

Activation of mitochondrial ATPase as evidence of loosely coupled oxidative phosphorylation in various skeletal muscle disorders. A histochemical fine-structural study

1 reference

12 December 2020

Investigation of mitochondrial metabolism in small human skeletal muscle biopsy specimens. Improvement of preparation procedure.

1 reference

12 December 2020

Polarographic studies of saponin-skinned muscle fibres in patients with mitochondrial myopathies

1 reference

12 December 2020

Mitochondrial respiratory parameters in cardiac tissue: a novel method of assessment by using saponin-skinned fibers

1 reference

12 December 2020

Functional characterization of mitochondrial oxidative phosphorylation in saponin-skinned human muscle fibers

1 reference

12 December 2020

Protein measurement with the Folin phenol reagent

1 reference

12 December 2020

The development of mitochondrial medicine

1 reference

12 December 2020

Brain abnormalities in Duchenne muscular dystrophy: phosphorus-31 magnetic resonance spectroscopy and neuropsychological study.

1 reference

12 December 2020

A respirometer for investigating oxidative cell metabolism: toward optimization of respiratory studies

1 reference

12 December 2020

Mitochondrial calcium overload: A general mechanism for cell-necrosis in muscle diseases

1 reference

12 December 2020

Importance of mitochondrial transmembrane processes in human mitochondriopathies

1 reference

12 December 2020

Identifiers

DOI

10.1023/A:1006880529195

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23 May 2018

Dimensions Publication ID

0 references

1 reference

23 May 2018