(Q55070574)

16 June 2018

title

Utrophin A is essential in mediating the functional adaptations of mdx mouse muscle following chronic AMPK activation. (English)

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16 June 2018

1 reference

Hasanen Al-Rewashdy

1

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16 June 2018

Vladimir Ljubicic

2

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16 June 2018

Wei Lin

3

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16 June 2018

Jean-Marc Renaud

4

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16 June 2018

Bernard J Jasmin

5

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16 June 2018

publication date

16 October 2014

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16 June 2018

published in

Human Molecular Genetics

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16 June 2018

volume

24

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16 June 2018

issue

5

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16 June 2018

page(s)

1243-1255

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16 June 2018

Function and genetics of dystrophin and dystrophin-related proteins in muscle

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1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDU535

The dystrophin-glycoprotein complex, cellular signaling, and the regulation of cell survival in the muscular dystrophies

21 January 2018

1 reference

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Utrophin lacks the rod domain actin binding activity of dystrophin

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDU535

The dystrophin complex forms a mechanically strong link between the sarcolemma and costameric actin

21 January 2018

1 reference

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The structural and functional diversity of dystrophin

21 January 2018

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The membrane-cytoskeleton interface: the role of dystrophin and utrophin

21 January 2018

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Dystrophin protects the sarcolemma from stresses developed during muscle contraction

21 January 2018

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Diagnosis and management of Duchenne muscular dystrophy, part 1: diagnosis, and pharmacological and psychosocial management

21 January 2018

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Diagnosis and management of Duchenne muscular dystrophy, part 2: implementation of multidisciplinary care

21 January 2018

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Current status of pharmaceutical and genetic therapeutic approaches to treat DMD.

21 January 2018

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Fast muscle fibers are preferentially affected in Duchenne muscular dystrophy.

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDU535

An autosomal transcript in skeletal muscle with homology to dystrophin

21 January 2018

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Primary structure of dystrophin-related protein

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDU535

Microtubule binding distinguishes dystrophin from utrophin

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDU535

Prevention of pathology in mdx mice by expression of utrophin: analysis using an inducible transgenic expression system.

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDU535

Heregulin ameliorates the dystrophic phenotype in mdx mice

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDU535

Skeletal muscle-specific expression of a utrophin transgene rescues utrophin-dystrophin deficient mice.

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDU535

Immunolocalization and developmental expression of dystrophin related protein in skeletal muscle.

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDU535

Calcineurin-NFAT signaling, together with GABP and peroxisome PGC-1{alpha}, drives utrophin gene expression at the neuromuscular junction.

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDU535

Stimulation of calcineurin signaling attenuates the dystrophic pathology in mdx mice.

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDU535

Expression of utrophin A mRNA correlates with the oxidative capacity of skeletal muscle fiber types and is regulated by calcineurin/NFAT signaling

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDU535

Modulation of utrophin A mRNA stability in fast versus slow muscles via an AU-rich element and calcineurin signaling.

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDU535

Chronic AMPK activation evokes the slow, oxidative myogenic program and triggers beneficial adaptations in mdx mouse skeletal muscle

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDU535

AMP-activated protein kinase at the nexus of therapeutic skeletal muscle plasticity in Duchenne muscular dystrophy

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDU535

Chronic AMPK stimulation attenuates adaptive signaling in dystrophic skeletal muscle

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDU535

Pharmacological activation of PPARbeta/delta stimulates utrophin A expression in skeletal muscle fibers and restores sarcolemmal integrity in mature mdx mice

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDU535

Exercise training improves plantar flexor muscle function in mdx mice.

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDU535

E2F transcription factor-1 deficiency reduces pathophysiology in the mouse model of Duchenne muscular dystrophy through increased muscle oxidative metabolism

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDU535

Combined effect of AMPK/PPAR agonists and exercise training in mdx mice functional performance

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDU535

Resveratrol decreases inflammation and increases utrophin gene expression in the mdx mouse model of Duchenne muscular dystrophy

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDU535

PGC-1alpha regulates the neuromuscular junction program and ameliorates Duchenne muscular dystrophy.

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDU535

Metabolic remodeling agents show beneficial effects in the dystrophin-deficient mdx mouse model

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDU535

Muscle ERRγ mitigates Duchenne muscular dystrophy via metabolic and angiogenic reprogramming

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDU535

Rescue of dystrophic skeletal muscle by PGC-1α involves a fast to slow fiber type shift in the mdx mouse

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDU535

Wnt7a treatment ameliorates muscular dystrophy

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDU535

The therapeutic potential of skeletal muscle plasticity in Duchenne muscular dystrophy: phenotypic modifiers as pharmacologic targets

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDU535

Relationship between 5-aminoimidazole-4-carboxamide-ribotide and AMP-activated protein kinase activity in the perfused mouse heart

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDU535

AMPK activation stimulates autophagy and ameliorates muscular dystrophy in the mdx mouse diaphragm.

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDU535

Chronic AMP-activated protein kinase activation and a high-fat diet have an additive effect on mitochondria in rat skeletal muscle

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDU535

AMP kinase is required for mitochondrial biogenesis in skeletal muscle in response to chronic energy deprivation

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDU535

Influence of AMP-activated protein kinase and calcineurin on metabolic networks in skeletal muscle

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDU535

The calcineurin signal transduction pathway is essential for successful muscle regeneration in mdx dystrophic mice.

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDU535

Animal models for muscular dystrophy show different patterns of sarcolemmal disruption.

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDU535

Expression of full-length utrophin prevents muscular dystrophy in mdx mice

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDU535

Endurance capacity in maturing mdx mice is markedly enhanced by combined voluntary wheel running and green tea extract

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDU535

Quantitative evaluation of the beneficial effects in the mdx mouse of epigallocatechin gallate, an antioxidant polyphenol from green tea.

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDU535

Mitochondrial dysfunction in neuromuscular disorders

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDU535

Mitochondria in skeletal muscle: adaptable rheostats of apoptotic susceptibility

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDU535

The role of mitochondria in the pathophysiology of skeletal muscle insulin resistance

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDU535

Genetic and pharmacologic inhibition of mitochondrial-dependent necrosis attenuates muscular dystrophy

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDU535

Oxidative stress by monoamine oxidases is causally involved in myofiber damage in muscular dystrophy

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDU535

Post-natal induction of PGC-1α protects against severe muscle dystrophy independently of utrophin.

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDU535

Transcriptional co-activator PGC-1 alpha drives the formation of slow-twitch muscle fibres

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDU535

Activity-dependent signaling pathways controlling muscle diversity and plasticity

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDU535

Long-term AICAR administration and exercise prevents diabetes in ZDF rats

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDU535

Long-term AICAR administration reduces metabolic disturbances and lowers blood pressure in rats displaying features of the insulin resistance syndrome

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDU535

21 January 2018

Identifiers

DOI

10.1093/HMG/DDU535

1 reference

16 June 2018

1 reference

16 June 2018