(Q56094868)

Crossref

https://api.crossref.org/works/10.1007%2FS10545-007-0678-8

Ca(2+) and Na(+) dependence of 3-hydroxyglutarate-induced excitotoxicity in primary neuronal cultures from chick embryo telencephalons

21 January 2018

1 reference

Crossref

https://api.crossref.org/works/10.1007%2FS10545-007-0678-8

Role of mitochondria in the etiology and pathogenesis of Parkinson's disease

21 January 2018

1 reference

Crossref

https://api.crossref.org/works/10.1007%2FS10545-007-0678-8

3-Hydroxyglutaric acid moderately impairs energy metabolism in brain of young rats.

21 January 2018

1 reference

12 December 2020

Glutaric aciduria type I and kynurenine pathway metabolites: a modified hypothesis

1 reference

12 December 2020

3-Hydroxyglutaric acid induces oxidative stress and decreases the antioxidant defenses in cerebral cortex of young rats

1 reference

12 December 2020

Biochemical, pathologic and behavioral analysis of a mouse model of glutaric acidemia type I.

1 reference

12 December 2020

Guideline for the diagnosis and management of glutaryl-CoA dehydrogenase deficiency (glutaric aciduria type I)

1 reference

12 December 2020

Type I glutaric aciduria, part 2: a model of acute striatal necrosis

1 reference

12 December 2020

Neuropathological, biochemical and molecular findings in a glutaric acidemia type 1 cohort

1 reference

12 December 2020

Chemically induced hypoglycemia and anoxia: relationship to glutamate receptor-mediated toxicity in retina

1 reference

12 December 2020

Bioenergetics in glutaryl-coenzyme A dehydrogenase deficiency: a role for glutaryl-coenzyme A.

1 reference

12 December 2020

Glutaric acid administration impairs energy metabolism in midbrain and skeletal muscle of young rats.

1 reference

12 December 2020

Brain lesions in an infant rhesus monkey treated with monsodium glutamate

1 reference

12 December 2020

Natural history, outcome, and treatment efficacy in children and adults with glutaryl-CoA dehydrogenase deficiency

1 reference

12 December 2020

Preliminary attempts to establish a rat model of striatal injury in glutaric acidaemia type I.

1 reference

12 December 2020

1-Methyl-4-phenylpyridinium produces excitotoxic lesions in rat striatum as a result of impairment of oxidative metabolism.

1 reference

12 December 2020

Crystal structures of human glutaryl-CoA dehydrogenase with and without an alternate substrate: structural bases of dehydrogenation and decarboxylation reactions

1 reference

12 December 2020

Mutation analysis in glutaric aciduria type I.

1 reference

12 December 2020

Intracerebral accumulation of glutaric and 3-hydroxyglutaric acids secondary to limited flux across the blood-brain barrier constitute a biochemical risk factor for neurodegeneration in glutaryl-CoA dehydrogenase deficiency

1 reference

12 December 2020

Glutamate becomes neurotoxic via the N-methyl-D-aspartate receptor when intracellular energy levels are reduced

1 reference

12 December 2020

Hypothesis: a role for quinolinic acid in the neuropathology of glutaric aciduria type I.

1 reference

12 December 2020

Inhibition of α‐ketoglutarate dehydrogenase complex promotes cytochrome c release from mitochondria, caspase‐3 activation, and necrotic cell death

1 reference

12 December 2020

A G-to-T transversion at the +5 position of intron 1 in the glutaryl CoA dehydrogenase gene is associated with the island Lake variant of glutaric acidemia type I

1 reference

12 December 2020

Glutaryl-CoA dehydrogenase mutations in glutaric acidemia (type I): review and report of thirty novel mutations

1 reference

12 December 2020

Chronic treatment with glutaric acid induces partial tolerance to excitotoxicity in neuronal cultures from chick embryo telencephalons

1 reference

12 December 2020

Inhibition of energy production in vitro by glutaric acid in cerebral cortex of young rats

1 reference

12 December 2020

Late-onset neurologic disease in glutaryl-CoA dehydrogenase deficiency

1 reference

12 December 2020

Aminooxyacetic Acid Results in Excitotoxin Lesions by a Novel Indirect Mechanism

1 reference

12 December 2020

Outcome of the first 3-years of a DNA-based neonatal screening program for glutaric acidemia type 1 in Manitoba and northwestern Ontario, Canada

1 reference

12 December 2020

Correlation of genotype and phenotype in glutaryl-CoA dehydrogenase deficiency

1 reference

12 December 2020

Analysis of the expression of murine glutaryl-CoA dehydrogenase: in vitro and in vivo studies

1 reference

12 December 2020

Brain regional development of the activity of alpha-ketoglutarate dehydrogenase complex in the rat.

1 reference

12 December 2020

Pathomechanisms of neurodegeneration in glutaryl-CoA dehydrogenase deficiency

1 reference

12 December 2020

Glutaric aciduria type I: outcome in the Republic of Ireland

1 reference

12 December 2020

Transporter-mediated permeation of drugs across the blood-brain barrier

1 reference

12 December 2020

Glutaric aciduria type 1: biochemical investigations and postmortem findings

1 reference

12 December 2020

3-Hydroxyglutaric acid fails to affect the viability of primary neuronal rat cells

1 reference

12 December 2020

Type I glutaric aciduria, part 1: natural history of 77 patients

1 reference

12 December 2020

Clinical course, early diagnosis, treatment, and prevention of disease in glutaryl-CoA dehydrogenase deficiency

1 reference

12 December 2020

The mitochondrial permeability transition from in vitro artifact to disease target

1 reference

12 December 2020

Glutaric acid moderately compromises energy metabolism in rat brain

1 reference

12 December 2020

Glutaryl-CoA dehydrogenase deficiency: region-specific analysis of organic acids and acylcarnitines in post mortem brain predicts vulnerability of the putamen.

1 reference

12 December 2020

Evidence that 3-hydroxyglutaric acid interacts with NMDA receptors in synaptic plasma membranes from cerebral cortex of young rats.

1 reference

12 December 2020

Glutaric acid and its metabolites cause apoptosis in immature oligodendrocytes: a novel mechanism of white matter degeneration in glutaryl-CoA dehydrogenase deficiency

1 reference

12 December 2020

Trafficking between glia and neurons of TCA cycle intermediates and related metabolites

1 reference

12 December 2020

Potentiation of 3-hydroxyglutarate neurotoxicity following induction of astrocytic iNOS in neonatal rat hippocampal cultures

1 reference

12 December 2020

Intrastriatal administration of 3-hydroxyglutaric acid induces convulsions and striatal lesions in rats

1 reference

12 December 2020

Mechanisms underlying initiation of excitotoxicity associated with metabolic inhibition

1 reference

12 December 2020

Structure, function, and genomic organization of human Na(+)-dependent high-affinity dicarboxylate transporter

1 reference

12 December 2020

Functional and molecular identification of sodium-coupled dicarboxylate transporters in rat primary cultured cerebrocortical astrocytes and neurons

1 reference

12 December 2020

Inhibition of brain glutamate decarboxylase by glutarate, glutaconate, and β-Hydroxyglutarate: Explanation of the symptoms in glutaric aciduria?

1 reference

12 December 2020

Glutaric aciduria: biochemical and morphologic considerations

1 reference

12 December 2020

Long-term follow-up, neurological outcome and survival rate in 28 Nordic patients with glutaric aciduria type 1.

1 reference

12 December 2020

Neonatal screening for glutaryl-CoA dehydrogenase deficiency

1 reference

12 December 2020

Endothelial effects of 3-hydroxyglutaric acid: implications for glutaric aciduria type I.

1 reference

12 December 2020

Cerebral metabolism of lactate in vivo: evidence for neuronal pyruvate carboxylation.

1 reference

12 December 2020

Inhibition of synaptosomal [3H]glutamate uptake and [3H]glutamate binding to plasma membranes from brain of young rats by glutaric acid in vitro

1 reference

12 December 2020

Contribution of reactive oxygen species to 3-hydroxyglutarate neurotoxicity in primary neuronal cultures from chick embryo telencephalons

1 reference

12 December 2020

An immunohistochemical study on alpha-ketoglutarate dehydrogenase complex in Parkinson's disease

1 reference

12 December 2020

CT and MR of the brain in glutaric acidemia type I: a review of 59 published cases and a report of 5 new patients

1 reference

12 December 2020

Energy metabolism is compromised in skeletal muscle of rats chronically-treated with glutaric acid.

1 reference

12 December 2020

Mice deficient in dihydrolipoamide dehydrogenase show increased vulnerability to MPTP, malonate and 3-nitropropionic acid neurotoxicity

1 reference

12 December 2020

Nerve cell lesions caused by 3-hydroxyglutaric acid: a possible mechanism for neurodegeneration in glutaric acidaemia I.

1 reference

12 December 2020

Maturation-dependent neurotoxicity of 3-hydroxyglutaric and glutaric acids in vitro: a new pathophysiologic approach to glutaryl-CoA dehydrogenase deficiency

1 reference

12 December 2020

The aetiology of neurological complications of organic acidaemias--a role for the blood-brain barrier

1 reference

12 December 2020

Glutaric aciduria type I: pathomechanisms of neurodegeneration.

1 reference

12 December 2020

Sensitivity and specificity of free and total glutaric acid and 3-hydroxyglutaric acid measurements by stable-isotope dilution assays for the diagnosis of glutaric aciduria type I

1 reference

12 December 2020

Neuroimaging findings in glutaric aciduria type 1

1 reference

12 December 2020

A diet-induced mouse model for glutaric aciduria type I.

1 reference

12 December 2020

Glutaric acidemia: a metabolic disorder causing progressive choreoathetosis

1 reference

12 December 2020

Glutaryl-CoA Dehydrogenase Deficiency in Spain: Evidence of Two Groups of Patients, Genetically, and Biochemically Distinct

1 reference

12 December 2020

Neuroradiological findings in glutaric aciduria type I (glutaryl-CoA dehydrogenase deficiency).

1 reference

12 December 2020

On the neurotoxicity of glutaric, 3-hydroxyglutaric, and trans-glutaconic acids in glutaric acidemia type 1.

1 reference

12 December 2020

Cerebral dicarboxylate transport and metabolism studied with isotopically labelled fumarate, malate and malonate

1 reference

12 December 2020

Amino acids as central nervous transmitters: the influence of ions, amino acid analogues, and ontogeny on transport systems for L-glutamic and L-aspartic acids and glycine into central nervous synaptosomes of the rat.

1 reference

12 December 2020