(Q59383537)

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:17189993%20AND%20SRC:MED&resulttype=core&format=json

23 December 2019

title

Severe endothelial dysfunction in the aorta of a mouse model of Fabry disease; partial prevention by N-butyldeoxynojirimycin treatment (English)

1 reference

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23 December 2019

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9

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23 December 2019

Frances Platt

10

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23 December 2019

author name string

T Heare

1

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23 December 2019

N J Alp

2

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23 December 2019

D A Priestman

3

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23 December 2019

A B Kulkarni

4

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23 December 2019

P Qasba

5

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23 December 2019

T D Butters

6

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23 December 2019

R A Dwek

7

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23 December 2019

K Clarke

8

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23 December 2019

publication date

25 December 2006

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Journal of Inherited Metabolic Disease

23 December 2019

published in

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23 December 2019

volume

30

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23 December 2019

issue

1

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23 December 2019

page(s)

79-87

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https://scigraph.springernature.com/pub.10.1007/s10545-006-0473-y

23 December 2019

exact match

0 references

cites work

Extensive Glycosphingolipid Depletion in the Liver and Lymphoid Organs of Mice Treated withN-Butyldeoxynojirimycin

1 reference

12 December 2020

Alpha-galactosidase A deficiency accelerates atherosclerosis in mice with apolipoprotein E deficiency

1 reference

12 December 2020

Fabrazyme--recombinant protein treatment for Fabry's disease

1 reference

12 December 2020

Enhanced endothelium-dependent vasodilation in Fabry disease

1 reference

12 December 2020

Novel oral treatment of Gaucher's disease with N-butyldeoxynojirimycin (OGT 918) to decrease substrate biosynthesis.

1 reference

12 December 2020

Increased glycosphingolipid levels in serum and aortae of apolipoprotein E gene knockout mice

1 reference

12 December 2020

Angiokeratoma corporis diffusum. A clinical study of eight affected families

1 reference

12 December 2020

N-butyldeoxynojirimycin is a novel inhibitor of glycolipid biosynthesis.

1 reference

12 December 2020

Regional cerebral hyperperfusion and nitric oxide pathway dysregulation in Fabry disease: reversal by enzyme replacement therapy

1 reference

12 December 2020

Reduction of globotriaosylceramide in Fabry disease mice by substrate deprivation

1 reference

12 December 2020

Critical role for glycosphingolipids in Niemann-Pick disease type C.

1 reference

12 December 2020

Role of endogenous bradykinin in human coronary vasomotor control

1 reference

12 December 2020

Prevention of lysosomal storage in Tay-Sachs mice treated with N-butyldeoxynojirimycin

1 reference

12 December 2020

Arterial wall properties and Womersley flow in Fabry disease

1 reference

12 December 2020

Profile of endothelial and leukocyte activation in Fabry patients

1 reference

12 December 2020

High-performance liquid chromatography analysis of ganglioside carbohydrates at the picomole level after ceramide glycanase digestion and fluorescent labeling with 2-aminobenzamide

1 reference

12 December 2020

Local and global cerebral blood flow and glucose utilization in the alpha-galactosidase A knockout mouse model of Fabry disease

1 reference

12 December 2020

Differential distribution of beta-adrenergic receptor subtypes in blood vessels of knockout mice lacking beta(1)- or beta(2)-adrenergic receptors

1 reference

12 December 2020

Arginine restores cholinergic relaxation of hypercholesterolemic rabbit thoracic aorta

1 reference

12 December 2020

Delayed symptom onset and increased life expectancy in Sandhoff disease mice treated with N-butyldeoxynojirimycin.

1 reference

12 December 2020

Aging accentuates and bone marrow transplantation ameliorates metabolic defects in Fabry disease mice

1 reference

12 December 2020

Contribution of bradykinin receptor dysfunction to abnormal coronary vasomotion in humans

1 reference

12 December 2020

Selective loss of microvascular endothelial function in human hypercholesterolemia

1 reference

12 December 2020

Amelioration by L-arginine of a dysfunctional arginine/nitric oxide pathway in diabetic endothelium

1 reference

12 December 2020

Enzyme replacement therapy in Fabry disease

1 reference

12 December 2020

Tetrahydrobiopterin restores endothelial function in hypercholesterolemia.

1 reference

12 December 2020

Mechanisms of increased vascular superoxide production in human diabetes mellitus: role of NAD(P)H oxidase and endothelial nitric oxide synthase

1 reference

12 December 2020

Cerebrovascular complications of Fabry's disease

1 reference

12 December 2020

Fabry disease in mice is associated with age-dependent susceptibility to vascular thrombosis

1 reference

12 December 2020

Non-invasive evaluation of arterial involvement in patients affected with Fabry disease

1 reference

12 December 2020

alpha-Galactosidase A deficient mice: a model of Fabry disease

1 reference

12 December 2020

Reversal by L-arginine of a dysfunctional arginine/nitric oxide pathway in the endothelium of the genetic diabetic BB rat

1 reference

12 December 2020

Enzyme replacement for lysosomal diseases

1 reference

12 December 2020

Endothelial markers and homocysteine in patients with classic Fabry disease.

1 reference

12 December 2020

10.1007/S10545-006-0473-Y

Identifiers

DOI

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23 December 2019

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