(Q71065676)

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:7327554%20AND%20SRC:MED&resulttype=core&format=json

15 October 2019

title

Multiple molecular forms of lysosomal enzymes in mucolipidosis II (English)

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:7327554%20AND%20SRC:MED&resulttype=core&format=json

15 October 2019

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?resulttype=core&format=json&query=SRC%3AMED%20AND%20EXT_ID%3A7327554

7 May 2024

author name string

D. F. Farrell

series ordinal

1

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?resulttype=core&format=json&query=SRC%3AMED%20AND%20EXT_ID%3A7327554

7 May 2024

M. P. MacMartin

series ordinal

2

1 reference

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7 May 2024

language of work or name

English

1 reference

National Center for Biotechnology Information

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/esummary.fcgi?db=pubmed&retmode=json&id=7327554

7 May 2024

publication date

1 January 1981

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:7327554%20AND%20SRC:MED&resulttype=core&format=json

full work available at URL

15 October 2019

http://link.springer.com/content/pdf/10.1007/BF00294931.pdf

file format

Portable Document Format

1 reference

http://link.springer.com/article/10.1007/BF00294931/fulltext.html

7 May 2024

1 reference

http://link.springer.com/content/pdf/10.1007/BF00294931

7 May 2024

1 reference

7 May 2024

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:7327554%20AND%20SRC:MED&resulttype=core&format=json

15 October 2019

volume

58

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:7327554%20AND%20SRC:MED&resulttype=core&format=json

15 October 2019

issue

3

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:7327554%20AND%20SRC:MED&resulttype=core&format=json

15 October 2019

page(s)

317-321

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:7327554%20AND%20SRC:MED&resulttype=core&format=json

https://scigraph.springernature.com/pub.10.1007/bf00294931

15 October 2019

exact match

0 references

cites work

"I-cell" disease: leakage of lysosomal enzymes into extracellular fluids

1 reference

12 December 2020

Multiple lysosomal enzyme deficiency due to enzyme leakage?

1 reference

12 December 2020

Clinical, biochemical, and ultrastructural studies in a case of chondrodystrophy presenting the I-cell phenotype in tissue culture.

1 reference

12 December 2020

Recognition and receptor-mediated uptake of a lysosomal enzyme, alpha-l-iduronidase, by cultured human fibroblasts

1 reference

12 December 2020

I-cell disease: Isoelectric focusing, concanavalin asepharose 4B binding and kinetic properties of human lier acid β-d-galactosidases

1 reference

12 December 2020

Catabolism of Desialylated Ceruloplasmin in the Liver

1 reference

12 December 2020

Enzymatic phosphorylation of lysosomal enzymes in the presence of UDP-N-acetylglucosamine. Absence of the activity in I-cell fibroblasts

1 reference

12 December 2020

Effects of tunicamycin on the biosynthesis of procollagen by human fibroblasts

1 reference

12 December 2020

Abnormal lysosomal hydrolases excreted by cultured fibroblasts in I-cell disease (mucolipidosis II)

1 reference

12 December 2020

Phosphohexosyl recognition is a general characteristic of pinocytosis of lysosomal glycosidases by human fibroblasts

1 reference

12 December 2020

Mutant enzymatic and cytological phenotypes in cultured human fibroblasts

1 reference

12 December 2020

Autolysis of glycoproteins in rat kidney lysosomes in vitro. Effects on the isoelectric focusing behaviour of glycoproteins, arylsulphatase and beta-glucuronidase

1 reference

12 December 2020

Biosynthesis of lysosomal enzymes in fibroblasts. Phosphorylation of mannose residues

1 reference

12 December 2020

Multiple molecular forms of arylsulfatase A in different forms of metachromatic leukodystrophy (MLD)

1 reference

12 December 2020

Studies of the mechanism of tunicamycin in hibition of IgA and IgE secretion by plasma cells

1 reference

12 December 2020

Enveloped virus acquires membrane defect when passaged in fibroblasts from I-cell disease patients

1 reference

12 December 2020

Globoid cell (Krabbe's) leukodystrophy: heterozygote detection in cultured skin fibroblasts

1 reference

12 December 2020

Processing of high mannose oligosaccharides to form complex type oligosaccharides on the newly synthesized polypeptides of the vesicular stomatitis virus G protein and the IgG heavy chain

1 reference

12 December 2020

Phosphohexosyl components of a lysosomal enzyme are recognized by pinocytosis receptors on human fibroblasts

1 reference

12 December 2020

The synthesis of complex-type oligosaccharides. III. Identification of an alpha-D-mannosidase activity involved in a late stage of processing of complex-type oligosaccharides

1 reference

12 December 2020

Multiple molecular forms of certain lysosomal enzymes separated by isoelectric focusing on cellulose acetate membranes

1 reference

12 December 2020

The binding of desialylated glycoproteins by plasma membranes of rat liver

1 reference

12 December 2020

Isoelectric focusing of acid hydrolases in human liver and serum. Findings in sera from one patient with I-cell disease phenotype

1 reference

12 December 2020

I-cell disease: Deficiency of extracellular hydrolase phosphorylation

1 reference

12 December 2020

Protein measurement with the Folin phenol reagent

1 reference

12 December 2020

Physicochemical modifications of lysosomal hydrolases during intracellular transport

1 reference

12 December 2020

Biosynthetic intermediates of beta-glucuronidase contain high mannose oligosaccharides with blocked phosphate residues

1 reference

12 December 2020

Effect of tunicamycin on the biosynthesis of the major human red cell sialoglycoprotein, glycophorin A, in the leukemia cell line K562

1 reference

12 December 2020

The synthesis of complex-type oligosaccharides. II. Characterization of the processing intermediates in the synthesis of the complex oligosaccharide units of the vesicular stomatitis virus G protein

1 reference

12 December 2020

A hypothesis for I-cell disease: defective hydrolases that do not enter lysosomes

1 reference

12 December 2020

The synthesis of complex-type oligosaccharides. I. Structure of the lipid-linked oligosaccharide precursor of the complex-type oligosaccharides of the vesicular stomatitis virus G protein

1 reference

12 December 2020

Proceedings of the National Academy of Sciences of the United States of America

25

73

2433

WS Sly

1976

1 reference

The New England Journal of Medicine

7 May 2024

31

284

109

UN Wiesmann

1971

1 reference

The New England Journal of Medicine

7 May 2024

32

285

1090

U Wiesmann

1971

1 reference

7 May 2024

Identifiers

DOI

10.1007/BF00294931

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:7327554%20AND%20SRC:MED&resulttype=core&format=json

15 October 2019

1 reference