(Q73117534)

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:9053546%20AND%20SRC:MED&resulttype=core&format=json

1 November 2019

title

Measurement of peroxisomal fatty acid beta-oxidation in cultured human skin fibroblasts (English)

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:9053546%20AND%20SRC:MED&resulttype=core&format=json

1 November 2019

author name string

R J Wanders

1

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:9053546%20AND%20SRC:MED&resulttype=core&format=json

1 November 2019

S Denis

2

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:9053546%20AND%20SRC:MED&resulttype=core&format=json

1 November 2019

J P Ruiter

3

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:9053546%20AND%20SRC:MED&resulttype=core&format=json

1 November 2019

R B Schutgens

4

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:9053546%20AND%20SRC:MED&resulttype=core&format=json

1 November 2019

C W van Roermund

5

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:9053546%20AND%20SRC:MED&resulttype=core&format=json

1 November 2019

B S Jacobs

6

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:9053546%20AND%20SRC:MED&resulttype=core&format=json

1 November 2019

publication date

1 January 1995

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:9053546%20AND%20SRC:MED&resulttype=core&format=json

Journal of Inherited Metabolic Disease

1 November 2019

published in

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:9053546%20AND%20SRC:MED&resulttype=core&format=json

1 November 2019

volume

18 Suppl 1

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:9053546%20AND%20SRC:MED&resulttype=core&format=json

1 November 2019

page(s)

113-124

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:9053546%20AND%20SRC:MED&resulttype=core&format=json

https://scigraph.springernature.com/pub.10.1007/bf00711434

1 November 2019

exact match

0 references

cites work

Direct demonstration that the deficient oxidation of very long chain fatty acids in X-linked adrenoleukodystrophy is due to an impaired ability of peroxisomes to activate very long chain fatty acids

1 reference

12 December 2020

Topographical localization of peroxisomal acyl-CoA ligases: differential localization of palmitoyl-CoA and lignoceroyl-CoA ligases

1 reference

12 December 2020

Purification and properties of acyl-CoA oxidase from rat liver

1 reference

12 December 2020

Peroxisomal chain-shortening of thromboxane B2: evidence for impaired degradation of thromboxane B2 in Zellweger syndrome

1 reference

12 December 2020

Identity of long-chain acyl-coenzyme A synthetase of microsomes, mitochondria, and peroxisomes in rat liver

1 reference

12 December 2020

Neonatal seizures and severe hypotonia in a male infant suffering from a defect in peroxisomal beta-oxidation

1 reference

12 December 2020

Lignoceric acid is oxidized in the peroxisome: implications for the Zellweger cerebro-hepato-renal syndrome and adrenoleukodystrophy

1 reference

12 December 2020

A new peroxisomal disorder with fetal and neonatal adrenal insufficiency

1 reference

12 December 2020

A bifunctional protein with deficient enzymic activity: identification of a new peroxisomal disorder using novel methods to measure the peroxisomal beta-oxidation enzyme activities

1 reference

12 December 2020

First prenatal diagnosis of acyl-CoA oxidase deficiency

1 reference

12 December 2020

Peroxisomal bifunctional enzyme deficiency

1 reference

12 December 2020

Neonatal seizures and retardation in a girl with biochemical features of X-linked adrenoleukodystrophy: a possible new peroxisomal disease entity

1 reference

12 December 2020

Identification of pristanoyl-CoA oxidase as a distinct, clofibrate non-inducible enzyme in rat liver peroxisomes

1 reference

12 December 2020

Beta-oxidation of the carboxyl side chain of prostaglandin E2 in rat liver peroxisomes and mitochondria

1 reference

12 December 2020

Peroxisomal very long-chain fatty acid beta-oxidation in human skin fibroblasts: activity in Zellweger syndrome and other peroxisomal disorders

1 reference

12 December 2020

Characteristics and subcellular localization of pristanoyl-CoA synthetase in rat liver

1 reference

12 December 2020

Conclusive evidence that very-long-chain fatty acids are oxidized exclusively in peroxisomes in human skin fibroblasts

1 reference

12 December 2020

A comparative study of straight chain and branched chain fatty acid oxidation in skin fibroblasts from patients with peroxisomal disorders

1 reference

12 December 2020

Subcellular distribution and characteristics of trihydroxycoprostanoyl-CoA synthetase in rat liver

1 reference

12 December 2020

Very long chain fatty acid beta-oxidation by rat liver mitochondria and peroxisomes

1 reference

12 December 2020

The CoA esters of 2-methyl-branched chain fatty acids and of the bile acid intermediates di- and trihydroxycoprostanic acids are oxidized by one single peroxisomal branched chain acyl-CoA oxidase in human liver and kidney

1 reference

12 December 2020

Peroxisomal chain-shortening of prostaglandin F2 alpha

1 reference

12 December 2020

Peroxisomal degradation of leukotrienes by beta-oxidation from the omega-end

1 reference

12 December 2020

A new peroxisomal disorder with enlarged peroxisomes and a specific deficiency of acyl-CoA oxidase (pseudo-neonatal adrenoleukodystrophy)

1 reference

12 December 2020

Latency of the peroxisomal enzyme acyl-CoA:dihydroxyacetonephosphate acyltransferase in digitonin-permeabilized fibroblasts: the effect of ATP and ATPase inhibitors

1 reference

12 December 2020

The microsomal dicarboxylyl-CoA synthetase

1 reference

12 December 2020

Studies on the urinary excretion of thromboxane B2 in Zellweger patients and control subjects: evidence for a major role for peroxisomes in the beta-oxidative chain-shortening of thromboxane B2.

1 reference

12 December 2020

Beta-oxidation of fatty acids in cultured human skin fibroblasts devoid of the capacity for oxidative phosphorylation

1 reference

12 December 2020

Formation of cholic acid from 3 alpha, 7 alpha, 12 alpha-trihydroxy-5 beta-cholestanoic acid by rat liver peroxisomes

1 reference

12 December 2020

Subcellular localization of 3 alpha, 7 alpha-dihydroxy- and 3 alpha,7 alpha,12 alpha-trihydroxy-5 beta-cholestanoyl-coenzyme A ligase(s) in rat liver

1 reference

12 December 2020

Biochemical abnormalities in rhizomelic chondrodysplasia punctata

1 reference

12 December 2020

Postnatal diagnosis of peroxisomal disorders: a biochemical approach

1 reference

12 December 2020

Metabolism of prostaglandin F2 alpha in Zellweger syndrome. Peroxisomal beta-oxidation is a major importance for in vivo degradation of prostaglandins in humans

1 reference

12 December 2020

Isolated defect of peroxisomal beta-oxidation in a 16-year-old patient.

1 reference

12 December 2020

Peroxisomal beta-oxidation. Purification of four novel 3-hydroxyacyl-CoA dehydrogenases from rat liver peroxisomes

1 reference

12 December 2020

Compartmentation of dicarboxylic acid beta-oxidation in rat liver: importance of peroxisomes in the metabolism of dicarboxylic acids

1 reference

12 December 2020

Bile acid analyses in "pseudo-Zellweger" syndrome; clues to the defect in peroxisomal beta-oxidation

1 reference

12 December 2020

Peroxisomal fatty acid beta-oxidation in relation to the accumulation of very long chain fatty acids in cultured skin fibroblasts from patients with Zellweger syndrome and other peroxisomal disorders

1 reference

12 December 2020

Lignoceroyl-CoA ligase activity in rat brain microsomal fraction: topographical localization and effect of detergents and alpha-cyclodextrin.

1 reference

12 December 2020

Hydroxyeicosatetraenoic acid metabolism in cultured human skin fibroblasts. Evidence for peroxisomal beta-oxidation

1 reference

12 December 2020

Topography of very-long-chain-fatty-acid-activating activity in peroxisomes from rat liver

1 reference

12 December 2020

Pseudo-Zellweger syndrome: deficiencies in several peroxisomal oxidative activities.

1 reference

12 December 2020

Zellweger-like phenotype in two siblings: a defect in peroxisomal beta-oxidation with elevated very long-chain fatty acids but normal bile acids

1 reference

12 December 2020

Bifunctional enzyme deficiency: identification of a new type of peroxisomal disorder in a patient with an impairment in peroxisomal beta-oxidation of unknown aetiology by means of complementation analysis

1 reference

12 December 2020

Novel subtype of peroxisomal acyl-CoA oxidase deficiency and bifunctional enzyme deficiency with detectable enzyme protein: identification by means of complementation analysis

1 reference

12 December 2020

Studies on the substrate specificity of the inducible and non-inducible acyl-CoA oxidases from rat kidney peroxisomes

1 reference

12 December 2020

X-linked adrenoleukodystrophy: biochemical diagnosis and enzyme defect

1 reference

12 December 2020

Metabolic pathways in mammalian peroxisomes

1 reference

12 December 2020

Presence of three acyl-CoA oxidases in rat liver peroxisomes. An inducible fatty acyl-CoA oxidase, a noninducible fatty acyl-CoA oxidase, and a noninducible trihydroxycoprostanoyl-CoA oxidase

1 reference

12 December 2020

Peroxisomal bifunctional protein from rat liver is a trifunctional enzyme possessing 2-enoyl-CoA hydratase, 3-hydroxyacyl-CoA dehydrogenase, and delta 3, delta 2-enoyl-CoA isomerase activities

1 reference

12 December 2020

A fatty acyl-CoA oxidizing system in rat liver peroxisomes; enhancement by clofibrate, a hypolipidemic drug

1 reference

12 December 2020

Human peroxisomal 3-oxoacyl-coenzyme A thiolase deficiency

1 reference

12 December 2020

Peroxisomal lignoceroyl-CoA ligase deficiency in childhood adrenoleukodystrophy and adrenomyeloneuropathy

1 reference

12 December 2020

Identification and purification of a peroxisomal branched chain fatty acyl-CoA oxidase

1 reference

12 December 2020

Peroxisomal beta-oxidation defect with detectable peroxisomes: a case with neonatal onset and progressive course

1 reference

12 December 2020

Peroxisomal localization of the immunoreactive beta-oxidation enzymes in a neonate with a beta-oxidation defect. Pathological observations in liver, adrenal cortex and kidney.

1 reference

12 December 2020

Identifiers

DOI

10.1007/BF00711434

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:9053546%20AND%20SRC:MED&resulttype=core&format=json

Dimensions Publication ID

1 November 2019

0 references

1 reference