(Q73482721)

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:11196106%20AND%20SRC:MED&resulttype=core&format=json

4 November 2019

title

Branched-chain L-amino acid metabolism in classical maple syrup urine disease after orthotopic liver transplantation (English)

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:11196106%20AND%20SRC:MED&resulttype=core&format=json

4 November 2019

1 reference

ChEBI release 2020-05-28

ChEBI ID

43433

orthotopic liver transplantation

1 reference

maple syrup urine disease

inferred from title

1 reference

A Bodner-Leidecker

1

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:11196106%20AND%20SRC:MED&resulttype=core&format=json

4 November 2019

U Wendel

series ordinal

2

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:11196106%20AND%20SRC:MED&resulttype=core&format=json

4 November 2019

J M Saudubray

series ordinal

3

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:11196106%20AND%20SRC:MED&resulttype=core&format=json

4 November 2019

P Schadewaldt

series ordinal

4

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:11196106%20AND%20SRC:MED&resulttype=core&format=json

4 November 2019

publication date

1 December 2000

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:11196106%20AND%20SRC:MED&resulttype=core&format=json

Journal of Inherited Metabolic Disease

4 November 2019

published in

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:11196106%20AND%20SRC:MED&resulttype=core&format=json

4 November 2019

volume

23

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:11196106%20AND%20SRC:MED&resulttype=core&format=json

4 November 2019

issue

8

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:11196106%20AND%20SRC:MED&resulttype=core&format=json

4 November 2019

page(s)

805-818

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:11196106%20AND%20SRC:MED&resulttype=core&format=json

https://scigraph.springernature.com/pub.10.1023/a:1026708618507

4 November 2019

exact match

0 references

cites work

Oral L-Alloisoleucine Loading Studies in Healthy Subjects and in Patients with Maple Syrup Urine Disease

1 reference

12 December 2020

Exercise-induced activation of the branched-chain 2-oxo acid dehydrogenase in human muscle

1 reference

12 December 2020

Nutritional status affects branched-chain oxoacid dehydrogenase activity during exercise in humans

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12 December 2020

Tracers in metabolic research: radioisotope and stable isotope/mass spectrometry methods.

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12 December 2020

Modulation of whole body protein metabolism, during and after exercise, by variation of dietary protein

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12 December 2020

Regulation of branched-chain alpha-ketoacid dehydrogenase kinase

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12 December 2020

Geometric method for measuring body surface area: a height-weight formula validated in infants, children, and adults

1 reference

12 December 2020

[Mid-term outcome of 2 cases with maple syrup urine disease: role of liver transplantation in the treatment]

1 reference

12 December 2020

Distribution of branched-chain alpha-keto acid dehydrogenases in primate tissues

1 reference

12 December 2020

On the mechanism of L-alloisoleucine formation: studies on a healthy subject and in fibroblasts from normals and patients with maple syrup urine disease

1 reference

12 December 2020

Isozyme patterns of branched-chain amino acid transaminase in human tissues and tumors

1 reference

12 December 2020

The 2-oxo acid dehydrogenase complexes: recent advances

1 reference

12 December 2020

Dietary protein level regulates expression of the mitochondrial branched-chain aminotransferase in rats

1 reference

12 December 2020

Liver transplantation in maple syrup urine disease

1 reference

12 December 2020

Significance of L-alloisoleucine in plasma for diagnosis of maple syrup urine disease

1 reference

12 December 2020

Assessment of whole body L-leucine oxidation by noninvasive L-[1-13C]leucine breath tests: a reappraisal in patients with maple syrup urine disease, obligate heterozygotes, and healthy subjects

1 reference

12 December 2020

Thiamine increases the specific activity of human liver branched chain α-ketoacid dehydrogenase

1 reference

12 December 2020

A molecular model of human branched-chain amino acid metabolism

1 reference

12 December 2020

Metabolism of branched-chain amino acids in maple syrup urine disease

1 reference

12 December 2020

Deamination of amino acids as a source for ammonia production in human skeletal muscle during prolonged exercise

1 reference

12 December 2020

Alteration in gene expression of branched-chain keto acid dehydrogenase kinase but not in gene expression of its substrate in the liver of clofibrate-treated rats

1 reference

12 December 2020

Exercise causes branched-chain oxoacid dehydrogenase dephosphorylation but not AMP deaminase binding

1 reference

12 December 2020

Formation of L-alloisoleucine in vivo: an L-[13C]isoleucine study in man

1 reference

12 December 2020

Down-regulation of rat mitochondrial branched-chain 2-oxoacid dehydrogenase kinase gene expression by glucocorticoids

1 reference

12 December 2020

A convenient enzymatic method for the determination of 4-methyl-2-oxopentanoate in plasma: comparison with high performance liquid chromatographic analysis

1 reference

12 December 2020

Amino Acid Metabolism in Man

1 reference

12 December 2020

Metabolism of [2-14C] pyruvate in normal, acromegalic and hgh-treated human subjects

1 reference

12 December 2020

Kidney, splanchnic, and leg protein turnover in humans. Insight from leucine and phenylalanine kinetics.

1 reference

12 December 2020