(Q24598867)

1

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Patricia O'Donnell

2

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Steven Fernandez

3

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Charles H Vite

Chronic cyclodextrin treatment of murine Niemann-Pick C disease ameliorates neuronal cholesterol and glycosphingolipid storage and disease progression

4

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language of work or name

English

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publication date

July 2010

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published in

Pediatric Research

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volume

68

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issue

1

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page(s)

52-6

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cites work

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2913583

Cholesterol reduction by methyl-beta-cyclodextrin attenuates the delta opioid receptor-mediated signaling in neuronal cells but enhances it in non-neuronal cells

24 March 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2913583

Cyclodextrin overcomes the transport defect in nearly every organ of NPC1 mice leading to excretion of sequestered cholesterol as bile acid

24 March 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2913583

Cyclodextrin overcomes deficient lysosome-to-endoplasmic reticulum transport of cholesterol in Niemann-Pick type C cells

27 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2913583

Reversal of defective lysosomal transport in NPC disease ameliorates liver dysfunction and neurodegeneration in the npc1-/- mouse

27 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2913583

Clinical, electrophysiological, and serum biochemical measures of progressive neurological and hepatic dysfunction in feline Niemann-Pick type C disease

27 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2913583

27 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2913583

Effects of the cholesterol-lowering compound methyl-beta-cyclodextrin in models of alpha-synucleinopathy

27 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2913583

2-Hydroxypropyl-beta-cyclodextrin (HP-beta-CD): a toxicology review

27 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2913583

Consequences of NPC1 and NPC2 loss of function in mammalian neurons

27 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2913583

Niemann-Pick disease type C.

27 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2913583

Neurons in Niemann-Pick disease type C accumulate gangliosides as well as unesterified cholesterol and undergo dendritic and axonal alterations

27 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2913583

Pharmaceutical applications of cyclodextrins. III. Toxicological issues and safety evaluation

27 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2913583

Feline Niemann-Pick disease type C

27 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2913583

Parenteral hydroxypropyl cyclodextrins: intravenous and intracerebral administration of lipophiles

27 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2913583

Hypocholesterolemic action of beta-cyclodextrin and its effects on cholesterol metabolism in pigs fed a cholesterol-enriched diet.

30 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2913583

Cyclodextrins in the treatment of a mouse model of Niemann-Pick C disease

30 May 2018

1 reference

https://api.crossref.org/works/10.1203%2FPDR.0B013E3181DF4623

Mutation analysis of feline Niemann-Pick C1 disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1203%2FPDR.0B013E3181DF4623

Effects of dietary cholesterol restriction in a feline model of Niemann-Pick type C disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1203%2FPDR.0B013E3181DF4623

Neurological manifestations of Niemann-Pick disease type C in cats.

21 January 2018

1 reference

https://api.crossref.org/works/10.1203%2FPDR.0B013E3181DF4623

GABAergic neuroaxonal dystrophy and other cytopathological alterations in feline Niemann-Pick disease type C.

21 January 2018

1 reference

https://api.crossref.org/works/10.1203%2FPDR.0B013E3181DF4623

Critical role for glycosphingolipids in Niemann-Pick disease type C.

21 January 2018

1 reference

https://api.crossref.org/works/10.1203%2FPDR.0B013E3181DF4623

Behavior of alpha-, beta-, and gamma-cyclodextrins and their derivatives on an in vitro model of blood-brain barrier.

21 January 2018

1 reference

https://api.crossref.org/works/10.1203%2FPDR.0B013E3181DF4623

Evaluation of brain-targeting for the nasal delivery of estradiol by the microdialysis method.

21 January 2018

1 reference

https://api.crossref.org/works/10.1203%2FPDR.0B013E3181DF4623

Delivery of galanin-like peptide to the brain: targeting with intranasal delivery and cyclodextrins

21 January 2018

1 reference

https://api.crossref.org/works/10.1203%2FPDR.0B013E3181DF4623

Drug solubilizers to aid pharmacologists: amorphous cyclodextrin derivatives

21 January 2018

1 reference

12 December 2020

Differential effects of alpha-, beta- and gamma-cyclodextrins on human erythrocytes

1 reference

12 December 2020

Feline sphingolipidosis resembling Niemann-Pick disease type C

1 reference

12 December 2020

Alteration of the myometrial plasma membrane cholesterol content with beta-cyclodextrin modulates the binding affinity of the oxytocin receptor

1 reference

12 December 2020

Intravenous and oral pharmacokinetic evaluation of a 2-hydroxypropyl-beta-cyclodextrin-based formulation of carbamazepine in the dog: comparison with commercially available tablets and suspensions

1 reference

12 December 2020

10.1203/PDR.0B013E3181DF4623

Identifiers

DOI

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10.1203/00006450-201011001-00099

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Dimensions Publication ID

1009367996

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1021212655

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Fatcat ID

release_dwhqb5necfbide2xyg3k5qkyvi

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release_n7w5hv7eibgcjluyeggziazkpu

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1 reference

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PubMed publication ID

20357695

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