(Q26699142)

Europe PubMed Central

https://scigraph.springernature.com/pub.10.1007/s10545-010-9061-2

5 July 2021

exact match

0 references

cites work

Mitochondrial 2,4-dienoyl-CoA reductase deficiency in mice results in severe hypoglycemia with stress intolerance and unimpaired ketogenesis

1 reference

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Mammalian long-chain acyl-CoA synthetases

7 April 2017

1 reference

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A new genetic disorder in mitochondrial fatty acid beta-oxidation: ACAD9 deficiency

7 April 2017

1 reference

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Medium-chain acyl-CoA dehydrogenase deficiency in gene-targeted mice

7 April 2017

1 reference

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Bench-to-bedside review: Rhabdomyolysis -- an overview for clinicians

7 April 2017

1 reference

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Molecular recognition of fatty acids by peroxisome proliferator-activated receptors

7 April 2017

1 reference

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Identification of a common mutation in patients with medium-chain acyl-CoA dehydrogenase deficiency

7 April 2017

1 reference

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Cardiac hypertrophy in mice with long-chain acyl-CoA dehydrogenase or very long-chain acyl-CoA dehydrogenase deficiency

7 April 2017

1 reference

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Mitochondrial long chain fatty acid beta-oxidation in man and mouse

7 April 2017

1 reference

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Skeletal muscle lipid metabolism in exercise and insulin resistance

7 April 2017

1 reference

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Carnitine palmitoyltransferases 1 and 2: biochemical, molecular and medical aspects

7 April 2017

1 reference

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Peroxisome proliferator-activated receptor alpha target genes

7 April 2017

1 reference

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A novel brain-expressed protein related to carnitine palmitoyltransferase I

7 April 2017

1 reference

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Lack of mitochondrial trifunctional protein in mice causes neonatal hypoglycemia and sudden death

7 April 2017

1 reference

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Genomics of the human carnitine acyltransferase genes

7 April 2017

1 reference

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Disorders of mitochondrial fatty acyl-CoA beta-oxidation

7 April 2017

1 reference

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Evidence for direct binding of fatty acids and eicosanoids to human peroxisome proliferators-activated receptor alpha

7 April 2017

1 reference

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Hypolipidemic drugs, polyunsaturated fatty acids, and eicosanoids are ligands for peroxisome proliferator-activated receptors alpha and delta

7 April 2017

1 reference

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Muscle Carnitine Palmityltransferase Deficiency and Myoglobinuria

7 April 2017

1 reference

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Suberylglycine excretion in the urine from a patient with dicarboxylic aciduria

7 April 2017

1 reference

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Targeted deletion of FATP5 reveals multiple functions in liver metabolism: alterations in hepatic lipid homeostasis

7 April 2017

1 reference

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Disruption of mitochondrial beta -oxidation of unsaturated fatty acids in the 3,2-trans-enoyl-CoA isomerase-deficient mouse

7 April 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2950079

Targeted disruption of mouse long-chain acyl-CoA dehydrogenase gene reveals crucial roles for fatty acid oxidation

7 April 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2950079

Animal model of systemic carnitine deficiency: analysis in C3H-H-2 degrees strain of mouse associated with juvenile visceral steatosis

7 April 2017

1 reference

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Carnitine and type 2 diabetes

7 April 2017

1 reference

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Carnitine insufficiency caused by aging and overnutrition compromises mitochondrial performance and metabolic control

28 September 2017

1 reference

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The Randle cycle revisited: a new head for an old hat.

28 September 2017

1 reference

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Plasma acylcarnitine profiles suggest incomplete long-chain fatty acid beta-oxidation and altered tricarboxylic acid cycle activity in type 2 diabetic African-American women.

28 September 2017

1 reference

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Mitochondrial overload and incomplete fatty acid oxidation contribute to skeletal muscle insulin resistance

28 September 2017

1 reference

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Homozygous carnitine palmitoyltransferase 1b (muscle isoform) deficiency is lethal in the mouse

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2950079

Regulation of sarcolemmal transport of substrates in the healthy and diseased heart.

28 September 2017

1 reference

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Protein-mediated fatty acid uptake: novel insights from in vivo models

28 September 2017

1 reference

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Human acyl-CoA dehydrogenase-9 plays a novel role in the mitochondrial beta-oxidation of unsaturated fatty acids

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2950079

Mitochondrial energy metabolism in heart failure: a question of balance

28 September 2017

1 reference

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Mitochondrial beta-oxidation

28 September 2017

1 reference

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Characterization of a heart-specific fatty acid transport protein

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2950079

Cloning and functional characterization of ACAD-9, a novel member of human acyl-CoA dehydrogenase family

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2950079

28 September 2017

Rhabdomyolysis: a review

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2950079

Fatty acid oxidation disorders

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2950079

Molecular enzymology of carnitine transfer and transport

28 September 2017

1 reference

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Recognition and management of fatty acid oxidation defects: a series of 107 patients.

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2950079

Demonstration of a critical role for free fatty acids in mediating counterregulatory stimulation of gluconeogenesis and suppression of glucose utilization in humans

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2950079

Regulation of fatty acid oxidation in heart

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2950079

Mechanism for the stimulation of gluconeogenesis by fatty acids in perfused rat liver

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2950079

Prophylaxis of early ventricular fibrillation by inhibition of acylcarnitine accumulation

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2950079

Molecular basis of medium chain acyl-coenzyme A dehydrogenase deficiency. An A to G transition at position 985 that causes a lysine-304 to glutamate substitution in the mature protein is the single prevalent mutation

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2950079

Molecular characterization of inherited medium-chain acyl-CoA dehydrogenase deficiency

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2950079

Long-chain fatty acids activate calcium channels in ventricular myocytes

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2950079

The syndrome of systemic carnitine deficiency: Clinical, morphologic, biochemical, and pathophysiologic features

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2950079

Fatty acids, eicosanoids, and hypolipidemic agents identified as ligands of peroxisome proliferator-activated receptors by coactivator-dependent receptor ligand assay

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2950079

Flux control exerted by mitochondrial outer membrane carnitine palmitoyltransferase over beta-oxidation, ketogenesis and tricarboxylic acid cycle activity in hepatocytes isolated from rats in different metabolic states

31 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2950079

Inhibition of fatty acid stimulation of gluconeogenesis by (+)-decanoylcarnitine in perfused rat liver.

31 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2950079

Short-chain acyl-coenzyme A dehydrogenase deficiency in mice.

31 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2950079

Pyruvate dehydrogenase kinase 4 expression is synergistically induced by AMP-activated protein kinase and fatty acids.

31 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2950079

Muscle metabolism during graded quadriceps exercise in man

28 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2950079

Polymorphic ventricular tachycardia and abnormal Ca2+ handling in very-long-chain acyl-CoA dehydrogenase null mice

28 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2950079

Abnormal mitochondrial bioenergetics and heart rate dysfunction in mice lacking very-long-chain acyl-CoA dehydrogenase.

28 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2950079

Homozygous carnitine palmitoyltransferase 1a (liver isoform) deficiency is lethal in the mouse

28 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2950079

Fuel utilization in subjects with carnitine palmitoyltransferase 2 gene mutations.

28 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2950079

Fuel utilization in patients with very long-chain acyl-coa dehydrogenase deficiency.

28 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2950079

Liver fatty acid binding protein is required for high rates of hepatic fatty acid oxidation but not for the action of PPARalpha in fasting mice

28 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2950079

PYRUVATE CARBOXYLASE. I. NATURE OF THE REACTION

28 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2950079

A null mutation in H-FABP only partially inhibits skeletal muscle fatty acid metabolism

28 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2950079

Very-long-chain acyl-coenzyme a dehydrogenase deficiency in mice

28 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2950079

Comparative studies of the mode of oxidation of phenyl derivatives of fatty acids by the animal organism and by hydrogen peroxide (Dakin, H. D. (1908) J. Biol. Chem. 4, 419-435).

28 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2950079

Regulation of pyruvate dehydrogenase kinase expression by peroxisome proliferator-activated receptor-alpha ligands, glucocorticoids, and insulin

28 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2950079

Gestational, pathologic and biochemical differences between very long-chain acyl-CoA dehydrogenase deficiency and long-chain acyl-CoA dehydrogenase deficiency in the mouse

28 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2950079

Adaptive increase in pyruvate dehydrogenase kinase 4 during starvation is mediated by peroxisome proliferator-activated receptor alpha.

28 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2950079

Arrhythmias and conduction defects as presenting symptoms of fatty acid oxidation disorders in children

28 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2950079

Impaired long-chain fatty acid utilization by cardiac myocytes isolated from mice lacking the heart-type fatty acid binding protein gene.

28 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2950079

Pyruvate carboxylase. IX. Some properties of the activation by certain acyl derivatives of coenzyme A

28 November 2018

1 reference

12 December 2020

The effect of muscle extracts on the oxidation of palmitic acid by liver slices and homogenates

1 reference

12 December 2020

Purification and properties of rat liver acyl-CoA dehydrogenases and electron transfer flavoprotein

1 reference

12 December 2020

Long-chain acyl-CoA dehydrogenase is a key enzyme in the mitochondrial beta-oxidation of unsaturated fatty acids

1 reference

12 December 2020

2,6-Dimethylheptanoyl-CoA is a specific substrate for long-chain acyl-CoA dehydrogenase (LCAD): evidence for a major role of LCAD in branched-chain fatty acid oxidation

1 reference

12 December 2020

Effects of carnitine on fatty-acid oxidation by muscle

1 reference

12 December 2020

Organic aciduria and butyryl CoA dehydrogenase deficiency in BALB/cByJ mice

1 reference

12 December 2020

Infantile disease with microvesicular fatty infiltration of viscera spontaneously occurring in the C3H-H-2° strain of mouse with similarities to Reye's syndrome

1 reference

12 December 2020

10.1007/S10545-010-9061-2

Identifiers

DOI

1 reference

Dimensions Publication ID

1602603

1016736818

0 references

1602603

1 reference

1 reference

1 reference