(Q27658869)

2

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Alexander B Taylor

3

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P John Hart

4

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Rodney L Levine

Structural and Biophysical Properties of the Pathogenic SOD1 Variant H46R/H48Q †

5

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language of work or name

English

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publication date

16 February 2010

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published in

Biochemistry

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volume

49

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issue

6

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page(s)

1191-8

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cites work

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Oxidative stress in neurodegeneration: cause or consequence?

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Loss of metal ions, disulfide reduction and mutations related to familial ALS promote formation of amyloid-like aggregates from superoxide dismutase

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Wild-type SOD1 overexpression accelerates disease onset of a G85R SOD1 mouse.

29 September 2017

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Heterodimer formation of wild-type and amyotrophic lateral sclerosis-causing mutant Cu/Zn-superoxide dismutase induces toxicity independent of protein aggregation

29 September 2017

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Disulfide bond mediates aggregation, toxicity, and ubiquitylation of familial amyotrophic lateral sclerosis-linked mutant SOD1.

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Disease-associated mutations at copper ligand histidine residues of superoxide dismutase 1 diminish the binding of copper and compromise dimer stability

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Free radical biology and medicine: it's a gas, man!

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29 September 2017

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Enzymatic formation of polysulfides from mercaptopyruvate.

29 September 2017

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Familial amyotrophic lateral sclerosis mutants of copper/zinc superoxide dismutase are susceptible to disulfide reduction

29 September 2017

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Oxidation of either methionine 351 or methionine 358 in alpha 1-antitrypsin causes loss of anti-neutrophil elastase activity

29 September 2017

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A gain-of-function of an amyotrophic lateral sclerosis-associated Cu,Zn-superoxide dismutase mutant: An enhancement of free radical formation due to a decrease in Km for hydrogen peroxide

29 September 2017

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Altered reactivity of superoxide dismutase in familial amyotrophic lateral sclerosis

29 September 2017

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29 September 2017

The sulfurtransferases

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Sulphane sulphur in biological systems: a possible regulatory role

29 September 2017

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Copper, zinc superoxide dismutase catalyzes hydroxyl radical production from hydrogen peroxide

29 September 2017

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A source of hydrogen sulfide and a mechanism of its release in the brain

29 September 2017

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Modification of cysteine 111 in human Cu,Zn-superoxide dismutase

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2 June 2018

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Modification of cysteine 111 in Cu/Zn superoxide dismutase results in altered spectroscopic and biophysical properties.

2 June 2018

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Copper(2+) binding to the surface residue cysteine 111 of His46Arg human copper-zinc superoxide dismutase, a familial amyotrophic lateral sclerosis mutant

2 June 2018

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2 June 2018

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A familial amyotrophic lateral sclerosis-associated A4V Cu, Zn-superoxide dismutase mutant has a lower Km for hydrogen peroxide. Correlation between clinical severity and the Km value.

2 June 2018

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Contribution of conformational stability and reversibility of unfolding to the increased thermostability of human and bovine superoxide dismutase mutated at free cysteines.

2 June 2018

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Labile Sulfur in Human Superoxide Dismutase

2 June 2018

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The occurrence of bis-(2-amino-2-carboxyethyl) trisulphide in hydrolysates of wool and other proteins

2 June 2018

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Proteasomal degradation of mutant superoxide dismutases linked to amyotrophic lateral sclerosis

27 November 2018

1 reference

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Generation of reactive oxygen species by a persulfide (BnSSH).

27 November 2018

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Dissociation of human copper-zinc superoxide dismutase dimers using chaotrope and reductant. Insights into the molecular basis for dimer stability

27 November 2018

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Comparative effects of mono-, di-, tri-, and tetrasulfides derived from plants of the Allium family: redox cycling in vitro and hemolytic activity and Phase 2 enzyme induction in vivo

27 November 2018

1 reference

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Fibrillar inclusions and motor neuron degeneration in transgenic mice expressing superoxide dismutase 1 with a disrupted copper-binding site

27 November 2018

1 reference

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Human Cu/Zn superoxide dismutase (SOD1) overexpression in mice causes mitochondrial vacuolization, axonal degeneration, and premature motoneuron death and accelerates motoneuron disease in mice expressing a familial amyotrophic lateral sclerosis mut

27 November 2018

1 reference

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Amino acid sequence of chicken Cu, Zn-containing superoxide dismutase and identification of glutathionyl adducts at exposed cysteine residues

27 November 2018

1 reference

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Characterisation of a trisulphide derivative of biosynthetic human growth hormone produced in Escherichia coli.

27 November 2018

1 reference

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Mechanism of rhodanese action: isotopic tracer studies

27 November 2018

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12 December 2020

The unusually stable quaternary structure of human Cu,Zn-superoxide dismutase 1 is controlled by both metal occupancy and disulfide status

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12 December 2020

Disulphide-reduced superoxide dismutase-1 in CNS of transgenic amyotrophic lateral sclerosis models

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12 December 2020

Method for the determination of inorganic polysulfide distribution in aquatic systems

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12 December 2020

Fixation of nitrogen in an electrospray mass spectrometer

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12 December 2020

Motor neuron disease in mice expressing the wild type-like D90A mutant superoxide dismutase-1

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12 December 2020

Processing of X-ray diffraction data collected in oscillation mode

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12 December 2020

Evidence for an active site persulfide residue in rabbit liver aldehyde oxidase

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12 December 2020

Interaction of Proteins with Sulfide

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12 December 2020

On the mechanism of inactivation of xanthine oxidase by cyanide

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12 December 2020

The oxygen sensitivity of spinach ferredoxin and other iron-sulfur proteins. The formation of protein-bound sulfur-zero

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12 December 2020

The presence of S degrees-containing impurities in commercial samples of oxidized glutathione and their catalytic effect on the reduction of cytochrome c

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12 December 2020

Some sulfhydryl properties and primary structure of human erythrocyte superoxide dismutase

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12 December 2020

Sulfhydryl reactivity of human erythrocyte superoxide dismutase. On the origin of the unusual spectral properties of the protein when prepared by a procedure utilizing chloroform and ethanol for the precipitation of hemoglobin

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Interaction of Cu,Zn superoxide dismutase with hydrogen sulfide

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12 December 2020

Tissue and subcellular distribution of bound and acid-labile sulfur, and the enzymic capacity for sulfide production in the rat

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Enzyme function of copper, zinc superoxide dismutase as a free radical generator

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Enhanced sensitivity for peptide mapping with electrospray liquid chromatography-mass spectrometry in the presence of signal suppression due to trifluoroacetic acid-containing mobile phases

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DNA cleavage by 7-methylbenzopentathiepin: a simple analog of the antitumor antibiotic varacin

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