(Q27641284)

10

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Jennifer Stine Elam

1

object named as

Jennifer Stine Elam

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author name string

Alexander B Taylor

2

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Richard Strange

3

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Peter A Doucette

5

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Jorge A Rodriguez

6

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S Samar Hasnain

7

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Lawrence J Hayward

8

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Joan Selverstone Valentine

9

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P John Hart

Nature structural biology

11

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publication date

June 2003

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published in

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volume

10

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page(s)

461-7

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issue

6

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cites work

Natural history of amyotrophic lateral sclerosis in a database population. Validation of a scoring system and a model for survival prediction.

1 reference

Amyotrophic lateral sclerosis and structural defects in Cu,Zn superoxide dismutase

31 March 2020

1 reference

Mutations in Cu/Zn superoxide dismutase gene are associated with familial amyotrophic lateral sclerosis

31 March 2020

1 reference

Superoxide dismutase activity, oxidative damage, and mitochondrial energy metabolism in familial and sporadic amyotrophic lateral sclerosis

31 March 2020

1 reference

Motor neurons in Cu/Zn superoxide dismutase-deficient mice develop normally but exhibit enhanced cell death after axonal injury

31 March 2020

1 reference

Transgenic mice expressing an altered murine superoxide dismutase gene provide an animal model of amyotrophic lateral sclerosis

31 March 2020

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ALS-linked SOD1 mutant G85R mediates damage to astrocytes and promotes rapidly progressive disease with SOD1-containing inclusions.

31 March 2020

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Motor neuron degeneration in mice that express a human Cu,Zn superoxide dismutase mutation

31 March 2020

1 reference

An adverse property of a familial ALS-linked SOD1 mutation causes motor neuron disease characterized by vacuolar degeneration of mitochondria

31 March 2020

1 reference

Altered reactivity of superoxide dismutase in familial amyotrophic lateral sclerosis

31 March 2020

1 reference

A gain-of-function of an amyotrophic lateral sclerosis-associated Cu,Zn-superoxide dismutase mutant: An enhancement of free radical formation due to a decrease in Km for hydrogen peroxide

31 March 2020

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Induction of nitric oxide-dependent apoptosis in motor neurons by zinc-deficient superoxide dismutase

31 March 2020

1 reference

Aggregation and Motor Neuron Toxicity of an ALS-Linked SOD1 Mutant Independent from Wild-Type SOD1

31 March 2020

1 reference

Fibrillar inclusions and motor neuron degeneration in transgenic mice expressing superoxide dismutase 1 with a disrupted copper-binding site

31 March 2020

1 reference

Up-regulation of protein chaperones preserves viability of cells expressing toxic Cu/Zn-superoxide dismutase mutants associated with amyotrophic lateral sclerosis

31 March 2020

1 reference

Amyotrophic lateral sclerosis: a proposed mechanism

31 March 2020

1 reference

Axonal transport of mutant superoxide dismutase 1 and focal axonal abnormalities in the proximal axons of transgenic mice.

31 March 2020

1 reference

Slowing of axonal transport is a very early event in the toxicity of ALS-linked SOD1 mutants to motor neurons

31 March 2020

1 reference

Formation of high molecular weight complexes of mutant Cu, Zn-superoxide dismutase in a mouse model for familial amyotrophic lateral sclerosis.

31 March 2020

1 reference

Decreased metallation and activity in subsets of mutant superoxide dismutases associated with familial amyotrophic lateral sclerosis.

31 March 2020

1 reference

Copper(2+) binding to the surface residue cysteine 111 of His46Arg human copper-zinc superoxide dismutase, a familial amyotrophic lateral sclerosis mutant

31 March 2020

1 reference

Familial amyotrophic lateral sclerosis-associated mutations decrease the thermal stability of distinctly metallated species of human copper/zinc superoxide dismutase

31 March 2020

1 reference

Mutations in copper-zinc superoxide dismutase that cause amyotrophic lateral sclerosis alter the zinc binding site and the redox behavior of the protein

31 March 2020

1 reference

Decreased zinc affinity of amyotrophic lateral sclerosis-associated superoxide dismutase mutants leads to enhanced catalysis of tyrosine nitration by peroxynitrite

31 March 2020

1 reference

The metal binding properties of the zinc site of yeast copper-zinc superoxide dismutase: implications for amyotrophic lateral sclerosis

31 March 2020

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Mutant SOD1 causes motor neuron disease independent of copper chaperone-mediated copper loading

31 March 2020

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Arrangement of subunits and ordering of beta-strands in an amyloid sheet

31 March 2020

1 reference

Sequence Communication: Tabulation of transthyretin (TTR) variants as of 1/1/2000

31 March 2020

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Natural beta-sheet proteins use negative design to avoid edge-to-edge aggregation

31 March 2020

1 reference

Histological evidence of protein aggregation in mutant SOD1 transgenic mice and in amyotrophic lateral sclerosis neural tissues

31 March 2020

1 reference

The structure of holo and metal-deficient wild-type human Cu, Zn superoxide dismutase and its relevance to familial amyotrophic lateral sclerosis

31 March 2020

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Amyloid fibers are water-filled nanotubes

31 March 2020

1 reference

Neurodegenerative disease: amyloid pores from pathogenic mutations.

31 March 2020

1 reference

Cellular defenses against unfolded proteins: a cell biologist thinks about neurodegenerative diseases

31 March 2020

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Intense superoxide dismutase-1 immunoreactivity in intracytoplasmic hyaline inclusions of familial amyotrophic lateral sclerosis with posterior column involvement.

31 March 2020

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High molecular weight complexes of mutant superoxide dismutase 1: age-dependent and tissue-specific accumulation

31 March 2020

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Toxic proteins in neurodegenerative disease

31 March 2020

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Loss of in vitro metal ion binding specificity in mutant copper-zinc superoxide dismutases associated with familial amyotrophic lateral sclerosis

31 March 2020

1 reference

Subunit asymmetry in the three-dimensional structure of a human CuZnSOD mutant found in familial amyotrophic lateral sclerosis

31 March 2020

1 reference

[33] AMoRe: An automated molecular replacement program package

31 March 2020

1 reference

MOLREP: an Automated Program for Molecular Replacement

31 March 2020

1 reference

Efficient anisotropic refinement of macromolecular structures using FFT

31 March 2020

1 reference

Crystallography & NMR System: A New Software Suite for Macromolecular Structure Determination

31 March 2020

1 reference

Improved methods for building protein models in electron density maps and the location of errors in these models

31 March 2020

1 reference

Use of TLS parameters to model anisotropic displacements in macromolecular refinement

31 March 2020

1 reference

Errors in protein structures

31 March 2020

1 reference

PROCHECK: a program to check the stereochemical quality of protein structures

31 March 2020

1 reference

MOLSCRIPT: a program to produce both detailed and schematic plots of protein structures

31 March 2020

1 reference

Further additions to MolScript version 1.4, including reading and contouring of electron-density maps

31 March 2020

1 reference

Improved Fourier coefficients for maps using phases from partial structures with errors

31 March 2020

1 reference

Reactions of nitric oxide, superoxide and peroxynitrite with superoxide dismutase in neurodegeneration

31 March 2020

1 reference

inferred from DOI database lookup

7 January 2021

based on heuristic

Rapid automated molecular replacement by evolutionary search

1 reference