(Q28589500)

31 January 2017

title

C-terminal deletion of the atrophin-1 protein results in growth retardation but not neurodegeneration in mice (English)

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31 January 2017

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GOA release 2020-03-11

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Juehua Yu

1

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31 January 2017

Mingyao Ying

2

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31 January 2017

Yuan Zhuang

3

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31 January 2017

Tian Xu

4

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31 January 2017

Min Han

5

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31 January 2017

Xiaohui Wu

6

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31 January 2017

Rener Xu

7

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31 January 2017

publication date

1 October 2009

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31 January 2017

published in

Developmental Dynamics

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31 January 2017

volume

238

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31 January 2017

issue

10

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31 January 2017

page(s)

2471–2478

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Familial myoclonus epilepsy and choreoathetosis: hereditary dentatorubral-pallidoluysian atrophy

31 January 2017

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Contribution of nuclear and extranuclear polyQ to neurological phenotypes in mouse models of Huntington's disease

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7 January 2021

Loss of normal huntingtin function: new developments in Huntington's disease research

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7 January 2021

YAC transgenic mice carrying pathological alleles of the MJD1 locus exhibit a mild and slowly progressive cerebellar deficit

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7 January 2021

Purkinje cell expression of a mutant allele of SCA1 in transgenic mice leads to disparate effects on motor behaviors, followed by a progressive cerebellar dysfunction and histological alterations.

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7 January 2021

Formation of neuronal intranuclear inclusions underlies the neurological dysfunction in mice transgenic for the HD mutation

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7 January 2021

Inactivation of Hdh in the brain and testis results in progressive neurodegeneration and sterility in mice

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7 January 2021

Flanking sequences profoundly alter polyglutamine toxicity in yeast

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7 January 2021

Suppression of aggregate formation and apoptosis by transglutaminase inhibitors in cells expressing truncated DRPLA protein with an expanded polyglutamine stretch.

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7 January 2021

Generation and characterization of Sca2 (ataxin-2) knockout mice

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7 January 2021

Unstable expansion of CAG repeat in hereditary dentatorubral-pallidoluysian atrophy (DRPLA)

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7 January 2021

Exon 1 of the HD gene with an expanded CAG repeat is sufficient to cause a progressive neurological phenotype in transgenic mice

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7 January 2021

Structure and expression of the gene responsible for the triplet repeat disorder, dentatorubral and pallidoluysian atrophy (DRPLA)

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7 January 2021

SCA17, a novel autosomal dominant cerebellar ataxia caused by an expanded polyglutamine in TATA-binding protein

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7 January 2021

Nuclear localization of a non-caspase truncation product of atrophin-1, with an expanded polyglutamine repeat, increases cellular toxicity

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7 January 2021

Dentatorubral-pallidoluysian atrophy protein interacts through a proline-rich region near polyglutamine with the SH3 domain of an insulin receptor tyrosine kinase substrate

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7 January 2021

When more is less: pathogenesis of glutamine repeat neurodegenerative diseases

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7 January 2021

Pathogenesis of neurodegenerative diseases associated with expanded glutamine repeats: new answers, new questions.

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7 January 2021

Transgenic mice harboring a full-length human mutant DRPLA gene exhibit age-dependent intergenerational and somatic instabilities of CAG repeats comparable with those in DRPLA patients.

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7 January 2021

Nuclear accumulation of truncated atrophin-1 fragments in a transgenic mouse model of DRPLA.

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7 January 2021

Distinct behavioral and neuropathological abnormalities in transgenic mouse models of HD and DRPLA.

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7 January 2021

Inactivation of the mouse Atxn3 (ataxin-3) gene increases protein ubiquitination

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7 January 2021

Functional architecture of atrophins

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7 January 2021

Histone deacetylase-associating Atrophin proteins are nuclear receptor corepressors

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https://api.crossref.org/works/10.1002%2FDVDY.22063

7 January 2021

Atrophin-1, the dentato-rubral and pallido-luysian atrophy gene product, interacts with ETO/MTG8 in the nuclear matrix and represses transcription

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https://api.crossref.org/works/10.1002%2FDVDY.22063

7 January 2021

Widespread occurrence of intranuclear atrophin-1 accumulation in the central nervous system neurons of patients with dentatorubral-pallidoluysian atrophy

1 reference

https://api.crossref.org/works/10.1002%2FDVDY.22063

7 January 2021

Protein binding of a DRPLA family through arginine-glutamic acid dipeptide repeats is enhanced by extended polyglutamine

1 reference

https://api.crossref.org/works/10.1002%2FDVDY.22063

7 January 2021

Abnormal gene product identified in hereditary dentatorubral–pallidoluysian atrophy (DRPLA) brain

1 reference

https://api.crossref.org/works/10.1002%2FDVDY.22063

7 January 2021

Expression of dentatorubral-pallidoluysian atrophy (DRPLA) proteins in patients

1 reference

https://api.crossref.org/works/10.1002%2FDVDY.22063

7 January 2021

Sodium butyrate ameliorates histone hypoacetylation and neurodegenerative phenotypes in a mouse model for DRPLA.

1 reference

https://api.crossref.org/works/10.1002%2FDVDY.22063

7 January 2021

SCA7 knockin mice model human SCA7 and reveal gradual accumulation of mutant ataxin-7 in neurons and abnormalities in short-term plasticity.

1 reference

https://api.crossref.org/works/10.1002%2FDVDY.22063

7 January 2021

Expanded polyglutamines induce neurodegeneration and trans-neuronal alterations in cerebellum and retina of SCA7 transgenic mice

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https://api.crossref.org/works/10.1002%2FDVDY.22063

7 January 2021

Drosophila atrophin homolog functions as a transcriptional corepressor in multiple developmental processes

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https://api.crossref.org/works/10.1002%2FDVDY.22063

7 January 2021

Atrophin 2 recruits histone deacetylase and is required for the function of multiple signaling centers during mouse embryogenesis

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https://api.crossref.org/works/10.1002%2FDVDY.22063

7 January 2021

Identifiers

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31 January 2017

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