(Q33381242)

26 July 2017

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title

Molecular basis of ADAMTS13 dysfunction in thrombotic thrombocytopenic purpura (English)

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thrombotic thrombocytopenic purpura

26 July 2017

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2

Diana Karpman

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26 July 2017

Minola Manea

1

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26 July 2017

publication date

20 September 2008

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26 July 2017

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26 July 2017

volume

24

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26 July 2017

issue

3

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26 July 2017

page(s)

447-458

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Unusually large plasma factor VIII:von Willebrand factor multimers in chronic relapsing thrombotic thrombocytopenic purpura

26 July 2017

cites work

1 reference

https://api.crossref.org/works/10.1007%2FS00467-008-0986-8

Antibody inhibitors to von Willebrand factor metalloproteinase and increased binding of von Willebrand factor to platelets in ticlopidine-associated thrombotic thrombocytopenic purpura

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS00467-008-0986-8

A classification of hemolytic uremic syndrome and thrombotic thrombocytopenic purpura and related disorders

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS00467-008-0986-8

Comparison of plasma exchange with plasma infusion in the treatment of thrombotic thrombocytopenic purpura. Canadian Apheresis Study Group

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS00467-008-0986-8

VWF-cleaving protease (ADAMTS13) in premature infants

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS00467-008-0986-8

Cellular source of serum lactate dehydrogenase elevation in patients with thrombotic thrombocytopenic purpura

21 January 2018

1 reference

12 December 2020

Treatment of Thrombotic Thrombocytopenic Purpura with Plasma

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12 December 2020

Thrombotic thrombocytopenic purpura--then and now.

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12 December 2020

ADAMTS13 activity to antigen ratio in physiological and pathological conditions associated with an increased risk of thrombosis

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12 December 2020

Immunohistochemistry of vascular lesion in thrombotic thrombocytopenic purpura, with special reference to factor VIII related antigen

1 reference

12 December 2020

Ultralarge multimers of von Willebrand factor form spontaneous high-strength bonds with the platelet glycoprotein Ib-IX complex: studies using optical tweezers

1 reference

12 December 2020

Von Willebrand factor-cleaving protease (ADAMTS13) in thrombocytopenic disorders: a severely deficient activity is specific for thrombotic thrombocytopenic purpura

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12 December 2020

Renin-angiotensin axis blockade reduces proteinuria in presymptomatic patients with familial FSGS

1 reference

12 December 2020

ADAMTS13 autoantibodies in patients with thrombotic microangiopathies and other immunomediated diseases

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12 December 2020

Increased platelet retention in familial recurrent thrombotic thrombocytopenic purpura

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12 December 2020

ADAMTS-13 plasma level determination uncovers antigen absence in acquired thrombotic thrombocytopenic purpura and ethnic differences

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12 December 2020

Characterization of a core binding site for ADAMTS-13 in the A2 domain of von Willebrand factor.

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12 December 2020

ADAMTS-13 activity in plasma is rapidly measured by a new ELISA method that uses recombinant VWF-A2 domain as substrate

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12 December 2020

Mutations in a member of the ADAMTS gene family cause thrombotic thrombocytopenic purpura

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12 December 2020

ADAMTS13 is expressed in hepatic stellate cells

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12 December 2020

Mutations and common polymorphisms in ADAMTS13 gene responsible for von Willebrand factor-cleaving protease activity

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12 December 2020

Aetiology and pathogenesis of thrombotic thrombocytopenic purpura and haemolytic uraemic syndrome: the role of von Willebrand factor-cleaving protease

1 reference

12 December 2020

Multiple B-cell clones producing antibodies directed to the spacer and disintegrin/thrombospondin type-1 repeat 1 (TSP1) of ADAMTS13 in a patient with acquired thrombotic thrombocytopenic purpura.

1 reference

12 December 2020

Assay of von Willebrand factor (vWF)-cleaving protease based on decreased collagen binding affinity of degraded vWF: a tool for the diagnosis of thrombotic thrombocytopenic purpura (TTP)

1 reference

12 December 2020

Nonneutralizing IgM and IgG antibodies to von Willebrand factor-cleaving protease (ADAMTS-13) in a patient with thrombotic thrombocytopenic purpura

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12 December 2020

Hemolytic uremic syndrome-associated Shiga toxins promote endothelial-cell secretion and impair ADAMTS13 cleavage of unusually large von Willebrand factor multimers

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12 December 2020

Shear-induced unfolding triggers adhesion of von Willebrand factor fibers

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12 December 2020

Thrombotic thrombocytopenic purpura associated with clopidogrel

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12 December 2020

The activity of the von Willebrand factor cleaving protease ADAMTS-13 in newborn infants

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12 December 2020

Splenectomy for thrombotic thrombocytopenic purpura

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12 December 2020

ADAMTS-13 metalloprotease interacts with the endothelial cell-derived ultra-large von Willebrand factor

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12 December 2020

Factor VIII accelerates proteolytic cleavage of von Willebrand factor by ADAMTS13.

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12 December 2020

Evaluation and clinical application of a new method for measuring activity of von Willebrand factor-cleaving metalloprotease (ADAMTS13).

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12 December 2020

An IAP retrotransposon in the mouse ADAMTS13 gene creates ADAMTS13 variant proteins that are less effective in cleaving von Willebrand factor multimers

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12 December 2020

Systemic antithrombotic effects of ADAMTS13.

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12 December 2020

Epitope mapping of ADAMTS13 autoantibodies in acquired thrombotic thrombocytopenic purpura

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12 December 2020

Shear stress enhances the proteolysis of von Willebrand factor in normal plasma

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12 December 2020

Paroxysmal nocturnal haemoglobinuria (PNH) is caused by somatic mutations in the PIG-A gene

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12 December 2020

Acquired deficiency of von Willebrand factor-cleaving protease in a patient with thrombotic thrombocytopenic purpura

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12 December 2020

von Willebrand factor and von Willebrand factor-cleaving metalloprotease activity in Escherichia coli O157:H7-associated hemolytic uremic syndrome

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12 December 2020

Guideline for the investigation and initial therapy of diarrhea-negative hemolytic uremic syndrome.

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12 December 2020

Podocytes express ADAMTS13 in normal renal cortex and in patients with thrombotic thrombocytopenic purpura

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12 December 2020

von Willebrand factor mediates increased platelet retention in recurrent thrombotic thrombocytopenic purpura

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12 December 2020

Modulation of ADAMTS13 secretion and specific activity by a combination of common amino acid polymorphisms and a missense mutation

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12 December 2020

Thrombotic thrombocytopenic purpura associated with von Willebrand factor-cleaving protease (ADAMTS13) deficiency in children

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12 December 2020

An acute febrile pleiochromic anemia with hyaline thrombosis of the terminal arterioles and capillaries: an undescribed disease. 1925.

1 reference

12 December 2020

Antibodies to von Willebrand factor-cleaving protease in acute thrombotic thrombocytopenic purpura

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12 December 2020

Prognostic value of anti-ADAMTS 13 antibody features (Ig isotype, titer, and inhibitory effect) in a cohort of 35 adult French patients undergoing a first episode of thrombotic microangiopathy with undetectable ADAMTS 13 activity

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12 December 2020

Structure of von Willebrand factor-cleaving protease (ADAMTS13), a metalloprotease involved in thrombotic thrombocytopenic purpura

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12 December 2020

Localization of ADAMTS13 to the stellate cells of human liver

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12 December 2020

Apical sorting of ADAMTS13 in vascular endothelial cells and Madin-Darby canine kidney cells depends on the CUB domains and their association with lipid rafts

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12 December 2020

Is severe deficiency of ADAMTS-13 specific for thrombotic thrombocytopenic purpura? Yes

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12 December 2020

Activation-independent platelet adhesion and aggregation under elevated shear stress

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12 December 2020

Changes in von Willebrand factor-cleaving protease (ADAMTS13) activity after infusion of desmopressin

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12 December 2020

Changes in health and disease of the metalloprotease that cleaves von Willebrand factor.

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12 December 2020

Physiologic cleavage of von Willebrand factor by a plasma protease is dependent on its conformation and requires calcium ion.

1 reference

12 December 2020

ADAMTS-13, von Willebrand factor and related parameters in severe sepsis and septic shock

1 reference

12 December 2020

Advances in the pathogenesis, diagnosis, and treatment of thrombotic thrombocytopenic purpura

1 reference

12 December 2020

FRETS-VWF73, a first fluorogenic substrate for ADAMTS13 assay

1 reference

12 December 2020

Effects of inflammatory cytokines on the release and cleavage of the endothelial cell-derived ultralarge von Willebrand factor multimers under flow

1 reference

12 December 2020

Human von Willebrand factor: a multivalent protein composed of identical subunits

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12 December 2020

Multimeric composition of factor VIII/von Willebrand factor following administration of DDAVP: implications for pathophysiology and therapy of von Willebrand's disease subtypes

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12 December 2020

Thrombotic thrombocytopenic purpura in humans and mice

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12 December 2020

Severe secondary deficiency of von Willebrand factor-cleaving protease (ADAMTS13) in patients with sepsis-induced disseminated intravascular coagulation: its correlation with development of renal failure.

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12 December 2020

Decreased von Willebrand factor protease activity associated with thrombocytopenic disorders

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12 December 2020

Mild to moderate reduction of a von Willebrand factor cleaving protease (ADAMTS-13) in pregnant women with HELLP microangiopathic syndrome.

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12 December 2020

Anti-Factor H autoantibodies associated with atypical hemolytic uremic syndrome

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12 December 2020

An enzyme immunoassay of ADAMTS13 distinguishes patients with thrombotic thrombocytopenic purpura from normal individuals and carriers of ADAMTS13 mutations

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12 December 2020

Inflammation-associated ADAMTS13 deficiency promotes formation of ultra-large von Willebrand factor

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12 December 2020

Shigatoxin triggers thrombotic thrombocytopenic purpura in genetically susceptible ADAMTS13-deficient mice

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12 December 2020

Purification of human von Willebrand factor-cleaving protease and its identification as a new member of the metalloproteinase family

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12 December 2020

Coagulation studies in thrombotic thrombocytopenic purpura, with special reference to von Willebrand factor and protein S.

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12 December 2020

Measurement of von Willebrand factor cleaving protease (ADAMTS-13): results of an international collaborative study involving 11 methods testing the same set of coded plasmas

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12 December 2020

Decreased ADAMTS-13 (A disintegrin-like and metalloprotease with thrombospondin type 1 repeats) is associated with a poor prognosis in sepsis-induced organ failure*

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12 December 2020

Biosynthesis of von Willebrand protein by human megakaryocytes

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12 December 2020

The combined roles of ADAMTS13 and VWF in murine models of TTP, endotoxemia, and thrombosis

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12 December 2020

Successful treatment of severe thrombotic thrombocytopenic purpura with the monoclonal antibody rituximab

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12 December 2020

von Willebrand factor-cleaving protease in childhood diarrhoea-associated haemolytic uraemic syndrome

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12 December 2020

Proteolytic inactivation of ADAMTS13 by thrombin and plasmin.

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12 December 2020

Evaluation of ADAMTS-13 activity in plasma using recombinant von Willebrand Factor A2 domain polypeptide as substrate

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12 December 2020

Measurement of ADAMTS-13 activity in plasma by the FRETS-VWF73 assay: comparison with other assay methods

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12 December 2020

ADAMTS13 and anti-ADAMTS13 antibodies as markers for recurrence of acquired thrombotic thrombocytopenic purpura during remission

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12 December 2020

von Willebrand factor-cleaving protease in thrombotic thrombocytopenic purpura and the hemolytic-uremic syndrome

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12 December 2020

Ultralarge von Willebrand factor multimers and normal ADAMTS13 activity in the umbilical cord blood

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12 December 2020

von Willebrand factor-cleaving protease (ADAMTS13) activity in normal non-pregnant women, pregnant and post-delivery women

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12 December 2020

Prevalence of the ADAMTS-13 missense mutation R1060W in late onset adult thrombotic thrombocytopenic purpura

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12 December 2020

ADAMTS13-binding IgG are present in patients with thrombotic thrombocytopenic purpura

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12 December 2020

Binding of platelet glycoprotein Ibalpha to von Willebrand factor domain A1 stimulates the cleavage of the adjacent domain A2 by ADAMTS13.

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12 December 2020

Estimation of the von Willebrand factor-cleaving protease in plasma using monoclonal antibodies to vWF.

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12 December 2020

Quantitative Western blot analysis of plasma ADAMTS13 antigen in patients with Upshaw-Schulman syndrome

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12 December 2020

Hepatic stellate cell damage may lead to decreased plasma ADAMTS13 activity in rats

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12 December 2020

Triplet structure of von Willebrand factor reflects proteolytic degradation of high molecular weight multimers

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12 December 2020

Fatal congenital thrombotic thrombocytopenic purpura with apparent ADAMTS13 inhibitor: in vitro inhibition of ADAMTS13 activity by hemoglobin

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12 December 2020

Von Willebrand factor: molecular size and functional activity

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12 December 2020

Acquired ADAMTS-13 deficiency in pediatric patients with severe sepsis

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12 December 2020

Human endothelial cells synthesize and release ADAMTS-13.

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12 December 2020

Pathogenesis of thrombotic microangiopathies

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12 December 2020

ADAMTS13 phenotype in plasma from normal individuals and patients with thrombotic thrombocytopenic purpura

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12 December 2020

Partial purification and characterization of a protease from human plasma cleaving von Willebrand factor to fragments produced by in vivo proteolysis.

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12 December 2020

VWF73, a region from D1596 to R1668 of von Willebrand factor, provides a minimal substrate for ADAMTS-13

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12 December 2020

Synthesis of von Willebrand factor by cultured human endothelial cells

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12 December 2020

Amino acid regions 572-579 and 657-666 of the spacer domain of ADAMTS13 provide a common antigenic core required for binding of antibodies in patients with acquired TTP.

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12 December 2020

Mechanisms of the interaction between two ADAMTS13 gene mutations leading to severe deficiency of enzymatic activity.

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12 December 2020

ADAMTS-13 rapidly cleaves newly secreted ultralarge von Willebrand factor multimers on the endothelial surface under flowing conditions

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12 December 2020

Partial amino acid sequence of purified von Willebrand factor-cleaving protease

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12 December 2020

Detection of von Willebrand factor-cleaving protease (ADAMTS-13) in human platelets.

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12 December 2020

[Improved methods of preventing tuberculosis and nonspecific lung diseases]

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12 December 2020

10.1007/S00467-008-0986-8

Identifiers

DOI

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Dimensions Publication ID

26 July 2017

1047487823

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