(Q33382672)

26 July 2017

1 reference

title

Inherited bleeding disorders (English)

1 reference

26 July 2017

1

Blanchette VS

1 reference

26 July 2017

Sparling C

2

1 reference

26 July 2017

Turner C

series ordinal

3

1 reference

26 July 2017

publication date

1 April 1991

1 reference

Best Practice and Research: Clinical Haematology

26 July 2017

published in

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26 July 2017

volume

4

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26 July 2017

issue

2

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26 July 2017

page(s)

291-332

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von Willebrand's disease and hemorrhagic telangiectasia: association of two complex disorders of hemostasis resulting in life-threatening hemorrhage

26 July 2017

cites work

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Congenital SPCA deficiency: a hitherto unrecognized coagulation defect with hemorrhage rectified by serum and serum fractions

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Congenital Deficiency of α2-Plasmin Inhibitor Associated with Severe Hemorrhagic Tendency *

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

A relatively high frequency of severe (type III) von Willebrand's disease in Israel

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Use of a high-purity factor VIII concentrate (Hemate P) in von Willebrand's disease

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Prothrombin Madrid : a new familial abnormality of prothrombin

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Prothrombin Salakta: an abnormal prothrombin characterized by a defect in the active site of thrombin.

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Christmas disease: a condition previously mistaken for haemophilia

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Determination of the amino acid substitution in human prothrombin type 3 (157 Glu leads to Lys) and the localization of a third thrombin cleavage site

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Genetic heterogeneity of prothrombin (FII)

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Inheritance and bleeding in factor XI deficiency

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Recent advances in the preparation of plasma-derived and recombinant coagulation factor VIII.

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Congenital deficiency of factor 13 (fibrin-stabilizing factor): Report of a case and review of the literature

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Characterization of the platelet membrane glycoprotein abnormalities in Bernard-Soulier syndrome and comparison with normal by surface-labeling techniques and high-resolution two-dimensional gel electrophoresis

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Sex-Linked Hereditary Thrombocytopenia with Immunological Defects

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Immunologic and biochemical characterization of homozygous and heterozygous Glanzmann thrombasthenia in the Iraqi-Jewish and Arab populations of Israel: comparison of techniques for carrier detection

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Williams trait. Human kininogen deficiency with diminished levels of plasminogen proactivator and prekallikrein associated with abnormalities of the Hageman factor-dependent pathways

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Telangiectasia and von Willebrand's Disease in Two Families

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Clinical and laboratory evaluation of National Health Service factor VIII concentrate (8Y) for the treatment of von Willebrand's disease

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Familial Bleeding Tendency with Partial Platelet Thromboxane Synthetase Deficiency: Reorientation of Cyclic Endoperoxide Metabolism

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Response of patients with mild and moderate hemophilia A and von Willebrand's disease to treatment with desmopressin

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

The Factor-X Defect: Recognition of Abnormal Forms of Factor X

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Genetic variants of factor VII

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Type IIB von Willebrand's disease with probable autosomal recessive inheritance and presenting as thrombocytopenia in infancy

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Recurrent thrombosis in a patient with factor XII deficiency

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Inherited factor X deficiency: Presentation of a case with etiologic and treatment considerations

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Hereditary macrothrombocytopathia, nephritis and deafness

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Familial Bleeding Disorder with a Moderate Thrombocytopenia and Giant Blood Platelets

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Combined Functional and Immunochemical Analysis of Normal and Abnormal Human Factor X

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Tranexamic Acid in Control of Haemorrhage after Dental Extraction in Haemophilia and Christmas Disease

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Congenital afibrinogenemia in 10 offspring of uncle-niece marriages

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Hemostatic effect of a heat-treated factor VIII concentrate (Haemate P) in von Willebrand's disease

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

The clinical importance of acquired abnormalities of platelet function

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Bernard-Soulier disease: a study of four patients and their parents

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Biochemical studies of two patients with the gray platelet syndrome. Selective deficiency of platelet alpha granules

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Deep vein thrombosis and pulmonary embolism in congenital factor VII deficiency

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Severe congenital hypoprothrombinemia

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Divalent cation regulation of the surface orientation of platelet membrane glycoprotein IIb. Correlation with fibrinogen binding function and definition of a novel variant of Glanzmann's thrombasthenia

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

A ‘New’ Congenital Haemorrhagic Condition due to the Presence of an Abnormal Factor X (Factor X Friuli): Study of a Large Kindred

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Congenital thrombocytopathy (platelet factor 3 defect) with prolonged bleeding time but normal platelet adhesiveness and aggregation

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

A new family with classical factor X deficiency as demonstrated by electroimmunoassay

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Stuart clotting defect. II. Genetic aspects of a new hemorrhagic state

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

A variant of type II von Willebrand disease with an abnormal triplet structure and discordant effects of protease inhibitors on plasma and platelet von Willebrand factor structure

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Platelet function, ultrastructure, and survival in the May-Hegglin anomaly

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

THROMBASTHENIA. STUDIES ON THREE CASES

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

A new congenital defect of platelet secretion: impaired responsiveness of the platelets to cytoplasmic free calcium

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Comparison of continuous and intermittent Factor VIII concentrate therapy in hemophilia A.

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Arterial and venous thrombosis and normal response to streptokinase treatment in a young patient with severe Hageman factor deficiency

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Investigation of a kindred with a new autosomal dominantly inherited variant type von Willebrand's disease (possible type IID).

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Familial and constitutional bleeding disorder due to platelet cyclo-oxygenase deficiency

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Role of factor VIII-von Willebrand factor and fibronectin in the interaction of platelets in flowing blood with monomeric and fibrillar human collagen types I and III.

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Stuart clotting defect. I. Segregation of an hereditary hemorrhagic state from the heterogeneous group heretofore called stable factor (SPCA, proconvertin, factor VII) deficiency

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Hereditary Giant Platelet Syndrome: A Disorder of a New Aspect of Platelet Function

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Platelet storage pool deficiency: diagnosis in patients with prolonged bleeding times and normal platelet aggregation

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Prothrombin Brussels, a new congenital defective protein

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

1 reference

7 January 2021

Shortening of bleeding time by 1-deamino-8-D-arginine vasopressin in various bleeding disorders

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Alpha2-plasmin-inhibitor deficiency (Miyasato disease).

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Recurrent subarachnoid haemorrhages in patient with Hageman factor deficiency

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Impairment of Platelet Thromboxane A2Generation and of the Platelet Release Reaction in Two Patients with Congenital Deficiency of Platelet Cyclo-oxygenase

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Heterogeneous defects of platelet secretion and responses to weak agonists in patients with bleeding disorders

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Factor X deficiency in the neonatal period

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

CLINICAL ASPECTS OF CONGENITAL FACTOR VII DEFICIENCY

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Intracranial hemorrhage in congenital factor VII deficiency

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

A CRM-Positive variant of factor-VII deficiency and the detection of heterozygotes with the assay of factor-like antigen

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

SEVERE BLEEDING ASSOCIATED WITH DEFECTIVE THROMBOXANE SYNTHETASE

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Large-scale production and properties of a solvent-detergent-treated factor IX concentrate from human plasma

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Genetic thrombocytopenia with autosomal dominant transmission: a review of 54 cases

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

1-Desamino-8-D-arginine vasopressin (desmopressin) shortens the bleeding time in storage pool deficiency

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Specific roles for platelet surface glycoproteins in platelet function

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

A variant of Glanzmann's thrombasthenia with abnormal glycoprotein IIb-IIIa complexes in the platelet membrane

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Variability in the Aggregation of Human Platelets by adrenaline

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Abnormalities in the contact activation through factor XII in Fujiwara trait: a deficiency in both high and low molecular weight kininogens with low level of prekallikrein

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

1 reference

7 January 2021

Congenital deficiency of thromboxane and prostacyclin

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Clinical and laboratory evaluation of the treatment of von Willebrand's disease patients with heat-treated factor VIII concentrate (BPL 8Y)

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

The Marfan Syndrome: Diagnosis and Management

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Gray platelet syndrome. A variety of qualitative platelet disorder

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Factor VII deficiency

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Haemostatic balance in congenital deficiency of platelet cyclo-oxygenase

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Persistent gastrointestinal bleeding due to angiodysplasia of the gut in von Willebrand's disease

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

A familial hemorrhagic trait associated with a deficiency of a clot-promoting fraction of plasma

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Prothrombin Habana: a new dysfunctional molecule of human prothrombin associated with a true prothrombin deficiency

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Variant von Willebrand's disease: characterization of two subtypes by analysis of multimeric composition of factor VIII/von Willebrand factor in plasma and platelets

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Heightened interaction between platelets and factor VIII/von Willebrand factor in a new subtype of von Willebrand's disease

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Aberrant multimeric structure of von Willebrand factor in a new variant of von Willebrand's disease (type IIC)

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Identification of a 160,000 dalton platelet membrane protein that mediates the initial divalent cation-dependent adhesion of platelets to collagen

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Human recombinant DNA-derived antihemophilic factor (factor VIII) in the treatment of hemophilia A. recombinant Factor VIII Study Group

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Parahemophilia: Factor V Deficiency

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Congenital dysprothrombinemia: an inherited structural disorder of human prothrombin

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Thromboembolism in congenital factor VII deficiency

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Dissociation of the aggregating effect and the inhibitory effect upon cyclic adenosine monophosphate accumulation by adrenaline and adenosine diphosphate in human platelets

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Letter: Isolated platelet factor 3 deficiency

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

A new coagulation defect

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Fitzgerald factor: a hitherto unrecognised coagulation factor

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Epsilon-Aminocaproic Acid Therapy for Dental Extractions in Haemophilia and Christmas Disease: A Double Blind Controlled Trial

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

DDAVP: a useful alternative to blood components in moderate hemophilia A and von Willebrand disease

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

A familialdefect in platelet function associated with imapired release of adenosine diphosphate

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Studies of platelet 5-hydroxytryptamine (serotonin) in storage pool disease and albinism

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Isolated deficiency of platelet procoagulant activity

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Abnormal platelet response to thromboxane A2.

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Prekallikrein deficiency in man

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Congenital factor VII deficiency. A report of four new cases

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

The Factor VIII Abnormality in Severe von Willebrand's Disease

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

Subunit composition of plasma von Willebrand factor. Cleavage is present in normal individuals, increased in IIA and IIB von Willebrand disease, but minimal in variants with aberrant structure of individual oligomers (types IIC, IID, and IIE).

1 reference

https://api.crossref.org/works/10.1016%2FS0950-3536%2805%2980162-3

7 January 2021

10.1016/S0950-3536(05)80162-3

Identifiers

DOI

1 reference

26 July 2017

1 reference