(Q33388274)

26 July 2017

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title

DEAP-HUS: deficiency of CFHR plasma proteins and autoantibody-positive form of hemolytic uremic syndrome (English)

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26 July 2017

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1

Peter F Zipfel

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26 July 2017

6

Christine Skerka

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26 July 2017

4

Christoph Licht

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26 July 2017

Christoph Mache

2

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26 July 2017

Dominik Müller

series ordinal

3

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26 July 2017

Marianne Wigger

series ordinal

5

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26 July 2017

European DEAP-HUS Study Group

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7

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26 July 2017

publication date

16 February 2010

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26 July 2017

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26 July 2017

volume

25

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26 July 2017

issue

10

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26 July 2017

page(s)

2009-2019

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The C-terminus of factor H: monoclonal antibodies inhibit heparin binding and identify epitopes common to factor H and factor H-related proteins

26 July 2017

cites work

1 reference

Crossref

https://api.crossref.org/works/10.1007%2FS00467-010-1446-9

Mutations in factor H reduce binding affinity to C3b and heparin and surface attachment to endothelial cells in hemolytic uremic syndrome

21 January 2018

1 reference

Crossref

https://api.crossref.org/works/10.1007%2FS00467-010-1446-9

Human factor H-related protein 5 has cofactor activity, inhibits C3 convertase activity, binds heparin and C-reactive protein, and associates with lipoprotein.

21 January 2018

1 reference

Crossref

https://api.crossref.org/works/10.1007%2FS00467-010-1446-9

21 January 2018

1 reference

12 December 2020

Functional analyses indicate a pathogenic role of factor H autoantibodies in atypical haemolytic uraemic syndrome

1 reference

12 December 2020

An integrated map of the human regulator of complement activation (RCA) gene cluster on 1q32

1 reference

12 December 2020

Varicella as a trigger of atypical haemolytic uraemic syndrome associated with complement dysfunction: two cases

1 reference

12 December 2020

Autoimmune forms of thrombotic microangiopathy and membranoproliferative glomerulonephritis: Indications for a disease spectrum and common pathogenic principles

1 reference

12 December 2020

Eculizumab for Atypical Hemolytic–Uremic Syndrome

1 reference

12 December 2020

The human factor H-related protein 4 (FHR-4). A novel short consensus repeat-containing protein is associated with human triglyceride-rich lipoproteins

1 reference

12 December 2020

Deletion of complement factor H-related genes CFHR1 and CFHR3 is associated with atypical hemolytic uremic syndrome

1 reference

12 December 2020

ADAMTS13 autoantibodies in patients with thrombotic microangiopathies and other immunomediated diseases

1 reference

12 December 2020

Molecular cloning of a human serum protein structurally related to complement factor H

1 reference

12 December 2020

Atypical haemolytic uraemic syndrome associated with a hybrid complement gene

1 reference

12 December 2020

The high frequency of complement factor H related CFHR1 gene deletion is restricted to specific subgroups of patients with atypical haemolytic uraemic syndrome.

1 reference

12 December 2020

Rituximab as pre-emptive treatment in patients with thrombotic thrombocytopenic purpura and evidence of anti-ADAMTS13 autoantibodies

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12 December 2020

Complement regulators and inhibitory proteins

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12 December 2020

Anti-Factor H autoantibodies in a fifth renal transplant recipient with atypical hemolytic and uremic syndrome.

1 reference

12 December 2020

Characterization of complement factor H-related (CFHR) proteins in plasma reveals novel genetic variations of CFHR1 associated with atypical hemolytic uremic syndrome

1 reference

12 December 2020

Complement inhibitor eculizumab in atypical hemolytic uremic syndrome

1 reference

12 December 2020

Association of factor H autoantibodies with deletions of CFHR1, CFHR3, CFHR4, and with mutations in CFH, CFI, CD46, and C3 in patients with atypical hemolytic uremic syndrome

1 reference

12 December 2020

Factor H autoantibodies in atypical hemolytic uremic syndrome correlate with CFHR1/CFHR3 deficiency

1 reference

12 December 2020

Binding of human factor H-related protein 1 to serum-resistant Borrelia burgdorferi is mediated by borrelial complement regulator-acquiring surface proteins

1 reference

12 December 2020

Factor H family proteins and human diseases

1 reference

12 December 2020

FHL-1/reconectin: a human complement and immune regulator with cell-adhesive function

1 reference

12 December 2020

Autoantibodies in haemolytic uraemic syndrome (HUS).

1 reference

12 December 2020

Coagulation factor XIII B subunit is encoded by a gene linked to the regulator of complement activation (RCA) gene cluster in man

1 reference

12 December 2020

Guideline for the investigation and initial therapy of diarrhea-negative hemolytic uremic syndrome.

1 reference

12 December 2020

The human complement factor H: functional roles, genetic variations and disease associations

1 reference

12 December 2020

Eculizumab for congenital atypical hemolytic-uremic syndrome.

1 reference

12 December 2020

The complement factor H R1210C mutation is associated with atypical hemolytic uremic syndrome

1 reference

12 December 2020

Successful pre-transplant management of a patient with anti-factor H autoantibodies-associated haemolytic uraemic syndrome

1 reference

12 December 2020

A novel short consensus repeat-containing molecule is related to human complement factor H

1 reference

12 December 2020

Factor H and atypical hemolytic uremic syndrome: mutations in the C-terminus cause structural changes and defective recognition functions

1 reference

12 December 2020

The molecular basis of familial hemolytic uremic syndrome: mutation analysis of factor H gene reveals a hot spot in short consensus repeat 20.

1 reference

12 December 2020

Functional properties of complement factor H-related proteins FHR-3 and FHR-4: binding to the C3d region of C3b and differential regulation by heparin

1 reference

12 December 2020

Anti-Factor H autoantibodies associated with atypical hemolytic uremic syndrome

1 reference

12 December 2020

A novel mutation in the complement regulator clusterin in recurrent hemolytic uremic syndrome.

1 reference

12 December 2020

Clinical practice guidelines for the management of atypical haemolytic uraemic syndrome in the United Kingdom

1 reference

12 December 2020

Mechanisms of killing by anti-CD20 monoclonal antibodies.

1 reference

12 December 2020

Hemolytic Uremic Syndrome

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12 December 2020

Anti factor H autoantibodies block C-terminal recognition function of factor H in hemolytic uremic syndrome

1 reference

12 December 2020

Two additional human serum proteins structurally related to complement factor H. Evidence for a family of factor H-related genes.

1 reference

12 December 2020

Atypical hemolytic uremic syndrome associated with complement factor H autoantibodies and CFHR1/CFHR3 deficiency

1 reference

12 December 2020

The C-terminus of complement regulator Factor H mediates target recognition: evidence for a compact conformation of the native protein

1 reference

12 December 2020

Complement and the atypical hemolytic uremic syndrome in children.

1 reference

12 December 2020

Thrombomodulin mutations in atypical hemolytic-uremic syndrome

1 reference

12 December 2020

Structural and functional characterization of factor H mutations associated with atypical hemolytic uremic syndrome

1 reference

12 December 2020

The interactive Factor H-atypical hemolytic uremic syndrome mutation database and website: update and integration of membrane cofactor protein and Factor I mutations with structural models

1 reference

12 December 2020

FHR-4A: a new factor H-related protein is encoded by the human FHR-4 gene.

1 reference

12 December 2020

Hemolytic uremic syndrome: a factor H mutation (E1172Stop) causes defective complement control at the surface of endothelial cells

1 reference

12 December 2020

The role of complement inhibition in PNH.

1 reference

12 December 2020

Factor H mutations in hemolytic uremic syndrome cluster in exons 18-20, a domain important for host cell recognition

1 reference

12 December 2020

10.1007/S00467-010-1446-9

Identifiers

DOI

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Dimensions Publication ID

26 July 2017

1003986446

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