(Q33929671)

30 July 2017

title

Cystic fibrosis pigs develop lung disease and exhibit defective bacterial eradication at birth (English)

1 reference

eradication of infectious diseases

30 July 2017

0 references

1 reference

Alejandro A Pezzulo

3

0 references

Lynda S Ostedgaard

Lynda S Ostedgaard

21

0 references

Joel Shilyansky

Joel Shilyansky

28

0 references

David Stoltz

David A Stoltz

1

0 references

David Meyerholz

David K Meyerholz

2

0 references

Paul B McCray

Paul B McCray

29

0 references

Randall S. Prather

Randall S Prather

26

0 references

Timothy D Starner

Timothy D Starner

23

0 references

Aliye Uc

Aliye Uc

22

0 references

Joseph Zabner

Joseph Zabner

30

0 references

Alexander R Horswill

24

Alexander R Horswill

1 reference

30 July 2017

Shyam Ramachandran

4

1 reference

30 July 2017

Mark P Rogan

5

1 reference

30 July 2017

Greg J Davis

6

1 reference

30 July 2017

Robert A Hanfland

7

1 reference

30 July 2017

Chris Wohlford-Lenane

8

1 reference

30 July 2017

Cassie L Dohrn

9

1 reference

30 July 2017

Jennifer A Bartlett

10

1 reference

30 July 2017

George A Nelson

11

1 reference

30 July 2017

Eugene H Chang

12

1 reference

30 July 2017

Peter J Taft

13

1 reference

30 July 2017

Paula S Ludwig

14

1 reference

30 July 2017

Mira Estin

15

1 reference

30 July 2017

Emma E Hornick

16

1 reference

30 July 2017

Janice L Launspach

17

1 reference

30 July 2017

Melissa Samuel

18

1 reference

30 July 2017

Tatiana Rokhlina

19

1 reference

30 July 2017

Philip H Karp

20

1 reference

30 July 2017

Kim A Brogden

25

1 reference

30 July 2017

Sandra S Richter

27

1 reference

30 July 2017

Michael J Welsh

31

1 reference

30 July 2017

language of work or name

English

0 references

publication date

1 April 2010

1 reference

Science Translational Medicine

30 July 2017

published in

1 reference

30 July 2017

volume

2

1 reference

30 July 2017

issue

29

1 reference

30 July 2017

page(s)

29ra31

1 reference

Pathology of gastrointestinal organs in a porcine model of cystic fibrosis

30 July 2017

cites work

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2889616

Respiratory microbiology of patients with cystic fibrosis in the United States, 1995 to 2005.

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2889616

Disruption of the CFTR gene produces a model of cystic fibrosis in newborn pigs

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2889616

Adeno-associated virus-targeted disruption of the CFTR gene in cloned ferrets.

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2889616

Production of CFTR-null and CFTR-DeltaF508 heterozygous pigs by adeno-associated virus-mediated gene targeting and somatic cell nuclear transfer

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2889616

Molecular identification of bacteria in bronchoalveolar lavage fluid from children with cystic fibrosis

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2889616

Inflammation in cystic fibrosis--when and why? Friend or foe?

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2889616

Microbial ecology of the cystic fibrosis lung

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2889616

CFTR inhibition mimics the cystic fibrosis inflammatory profile

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2889616

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2889616

Digitoxin mimics gene therapy with CFTR and suppresses hypersecretion of IL-8 from cystic fibrosis lung epithelial cells

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2889616

Standardized procedure for measurement of nasal potential difference: an outcome measure in multicenter cystic fibrosis clinical trials

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2889616

State of the Art: Why do the lungs of patients with cystic fibrosis become infected and why can't they clear the infection?

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2889616

Early pulmonary infection, inflammation, and clinical outcomes in infants with cystic fibrosis

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2889616

Activation of NF-kappaB in airway epithelial cells is dependent on CFTR trafficking and Cl- channel function

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2889616

Inflammation and infection in naive human cystic fibrosis airway grafts

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2889616

Cystic fibrosis and the salt controversy

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2889616

Pathophysiology of gene-targeted mouse models for cystic fibrosis

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2889616

Severe viral respiratory infections in infants with cystic fibrosis.

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2889616

Repeat administration of an adenovirus vector encoding cystic fibrosis transmembrane conductance regulator to the nasal epithelium of patients with cystic fibrosis

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2889616

Quantitative evaluation of the development of tracheal submucosal glands in infants with cystic fibrosis and control infants

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2889616

Identification of the cystic fibrosis gene: cloning and characterization of complementary DNA

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2889616

Genetic systems in staphylococci

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2889616

Management and survival of meconium ileus. A 30-year review

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2889616

The lung in cystic fibrosis. A quantitative study including prevalence of pathologic findings among different age groups

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2889616

Inflammatory response in airway epithelial cells isolated from patients with cystic fibrosis.

5 July 2018

1 reference

Crossref

https://api.crossref.org/works/10.1126%2FSCITRANSLMED.3000928

CYSTIC FIBROSIS OF THE PANCREAS AND ITS RELATION TO CELIAC DISEASE

21 January 2018

1 reference

Crossref

https://api.crossref.org/works/10.1126%2FSCITRANSLMED.3000928

Lower airway inflammation in infants with cystic fibrosis detected by newborn screening.

21 January 2018

1 reference

Crossref

https://api.crossref.org/works/10.1126%2FSCITRANSLMED.3000928

Physiological basis of cystic fibrosis: a historical perspective

21 January 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2889616

Hemorrhagic gastroesophageal ulceration by pulmonary infection in extrahepatic cholestatic pigs.

29 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2889616

The relationship between infection and inflammation in the early stages of lung disease from cystic fibrosis

29 October 2018

1 reference

12 December 2020

Early pulmonary inflammation in infants with cystic fibrosis

1 reference

12 December 2020

Prevalence and antimicrobial susceptibility of microorganisms isolated from sputa of patients with cystic fibrosis

1 reference

12 December 2020

Observations in cystic fibrosis of the pancreas. 3. Pulmonary lesions

1 reference

12 December 2020

1 reference

12 December 2020

10.1126/SCITRANSLMED.3000928

Identifiers

DOI

1 reference

30 July 2017

1 reference

30 July 2017

1 reference