(Q33936940)

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Differential expression of PGC-1α and metabolic sensors suggest age-dependent induction of mitochondrial biogenesis in Friedreich ataxia fibroblasts

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scholarly article

1 reference

Europe PubMed Central

PubMed publication ID

30 July 2017

Differential expression of PGC-1α and metabolic sensors suggest age-dependent induction of mitochondrial biogenesis in Friedreich ataxia fibroblasts (English)

1 reference

Europe PubMed Central

PubMed publication ID

30 July 2017

Friedreich ataxia

1 reference

based on heuristic

inferred from title

José Luis García-Giménez

object named as

José Luis García-Giménez

1

0 references

Francisco Dasí

object named as

Francisco Dasí

4

0 references

object named as

Francesc Palau

7

0 references

author name string

Amparo Gimeno

2

1 reference

Europe PubMed Central

PubMed publication ID

30 July 2017

Pilar Gonzalez-Cabo

3

1 reference

Europe PubMed Central

PubMed publication ID

30 July 2017

Arantxa Bolinches-Amorós

5

1 reference

Europe PubMed Central

PubMed publication ID

30 July 2017

Belén Mollá

6

1 reference

Europe PubMed Central

PubMed publication ID

30 July 2017

Federico V Pallardó

8

1 reference

Europe PubMed Central

PubMed publication ID

30 July 2017

language of work or name

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publication date

7 June 2011

1 reference

Europe PubMed Central

PubMed publication ID

30 July 2017

1 reference

Europe PubMed Central

PubMed publication ID

30 July 2017

6

1 reference

Europe PubMed Central

PubMed publication ID

30 July 2017

6

1 reference

Europe PubMed Central

PubMed publication ID

30 July 2017

e20666

1 reference

Europe PubMed Central

PubMed publication ID

30 July 2017

copyright license

Creative Commons Attribution 4.0 International

7 June 2011

1 reference

April 2022 Public Data File from Crossref

copyright status

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describes a project that uses

1 reference

Europe PubMed Central

11 June 2022

https://www.ebi.ac.uk/europepmc/webservices/rest/PMC3110204/fullTextXML

based on heuristic

inferred from PubMed Central ID database lookup

PGC-1alpha down-regulation affects the antioxidant response in Friedreich's ataxia

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3110204

5 July 2018

Functional genomic analysis of frataxin deficiency reveals tissue-specific alterations and identifies the PPARgamma pathway as a therapeutic target in Friedreich's ataxia

1 reference

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5 July 2018

Bacterial frataxin CyaY is the gatekeeper of iron-sulfur cluster formation catalyzed by IscS

1 reference

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5 July 2018

Oral administration of vitamin C decreases muscle mitochondrial biogenesis and hampers training-induced adaptations in endurance performance.

1 reference

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Suppression of reactive oxygen species and neurodegeneration by the PGC-1 transcriptional coactivators

1 reference

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Reactive oxygen species act through p38 MAPK to limit the lifespan of hematopoietic stem cells

1 reference

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1 reference

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Metabolic control through the PGC-1 family of transcription coactivators

1 reference

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5 July 2018

Oxidative stress, mitochondrial dysfunction and cellular stress response in Friedreich's ataxia

1 reference

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Mitochondrial biogenesis and mitochondrial DNA maintenance of mammalian cells under oxidative stress.

1 reference

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5 July 2018

Transcriptional regulatory circuits controlling mitochondrial biogenesis and function

1 reference

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5 July 2018

Suppression of mitochondrial respiration through recruitment of p160 myb binding protein to PGC-1alpha: modulation by p38 MAPK

1 reference

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5 July 2018

AMP-activated protein kinase: a key system mediating metabolic responses to exercise

1 reference

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5 July 2018

Friedreich's Ataxia: disease mechanisms, antioxidant and Coenzyme Q10 therapy

1 reference

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5 July 2018

P53 physically interacts with mitochondrial transcription factor A and differentially regulates binding to damaged DNA

1 reference

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Human mitochondrial DNA is packaged with TFAM.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3110204

5 July 2018

A cellular model for Friedreich Ataxia reveals small-molecule glutathione peroxidase mimetics as novel treatment strategy

1 reference

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5 July 2018

Idebenone and reduced cardiac hypertrophy in Friedreich's ataxia

1 reference

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Analysis of Relative Gene Expression Data Using Real-Time Quantitative PCR and the 2−ΔΔCT Method

1 reference

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Cytokine stimulation of energy expenditure through p38 MAP kinase activation of PPARgamma coactivator-1.

1 reference

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Chronic activation of AMP kinase results in NRF-1 activation and mitochondrial biogenesis

2 references

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5 July 2018

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29 October 2018

Animal mitochondrial biogenesis and function: a regulatory cross-talk between two genomes

1 reference

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5 July 2018

Mouse models for Friedreich ataxia exhibit cardiomyopathy, sensory nerve defect and Fe-S enzyme deficiency followed by intramitochondrial iron deposits

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3110204

5 July 2018

Oxidative stress in patients with Friedreich ataxia.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3110204

5 July 2018

Frataxin activates mitochondrial energy conversion and oxidative phosphorylation

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3110204

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Mitochondrial free radical generation, oxidative stress, and aging

1 reference

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5 July 2018

Human frataxin maintains mitochondrial iron homeostasis in Saccharomyces cerevisiae.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3110204

5 July 2018

Peroxisome proliferator-activated receptor gamma coactivator-1 promotes cardiac mitochondrial biogenesis

1 reference

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Increase of mitochondria and mitochondrial DNA in response to oxidative stress in human cells

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3110204

5 July 2018

Deficit of in vivo mitochondrial ATP production in patients with Friedreich ataxia

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3110204

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Oxidative stress and upregulation of mitochondrial biogenesis genes in mitochondrial DNA-depleted HeLa cells

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3110204

5 July 2018

Increase in intracellular hydrogen peroxide and upregulation of a nuclear respiratory gene evoked by impairment of mitochondrial electron transfer in human cells.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3110204

5 July 2018

Mitochondrial transcription factor A is necessary for mtDNA maintenance and embryogenesis in mice

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3110204

5 July 2018

Frataxin is reduced in Friedreich ataxia patients and is associated with mitochondrial membranes

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3110204

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Phenotype correlation and intergenerational dynamics of the Friedreich ataxia GAA trinucleotide repeat

1 reference

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Clinical and genetic abnormalities in patients with Friedreich's ataxia

1 reference

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5 July 2018

Friedreich's ataxia: autosomal recessive disease caused by an intronic GAA triplet repeat expansion

1 reference

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A rapid, efficient method for purifying DNA-binding proteins. Denaturation-renaturation chromatography of human and yeast mitochondrial extracts

1 reference

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A simplification of the protein assay method of Lowry et al. which is more generally applicable

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3110204

5 July 2018

Frataxin promotes antioxidant defense in a thiol-dependent manner resulting in diminished malignant transformation in vitro

1 reference

https://api.crossref.org/works/10.1371%2FJOURNAL.PONE.0020666

21 January 2018

Glutathione in blood of patients with Friedreich's ataxia.

1 reference

https://api.crossref.org/works/10.1371%2FJOURNAL.PONE.0020666

21 January 2018

Idebenone delays the onset of cardiac functional alteration without correction of Fe-S enzymes deficit in a mouse model for Friedreich ataxia

1 reference

https://api.crossref.org/works/10.1371%2FJOURNAL.PONE.0020666

21 January 2018

Induction of mitochondrial biogenesis is a maladaptive mechanism in mitochondrial cardiomyopathies

1 reference

https://api.crossref.org/works/10.1371%2FJOURNAL.PONE.0020666

21 January 2018

Clinical, biochemical and molecular genetic correlations in Friedreich's ataxia

1 reference

https://pubmed.ncbi.nlm.nih.gov/21687738

12 December 2020

based on heuristic

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Disabled early recruitment of antioxidant defenses in Friedreich's ataxia

1 reference

https://pubmed.ncbi.nlm.nih.gov/21687738

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Manganese superoxide dismutase induction by iron is impaired in Friedreich ataxia cells

1 reference

https://pubmed.ncbi.nlm.nih.gov/21687738

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

The cardiomyopathy of Friedreich's ataxia morphological observations in 3 cases

1 reference

https://pubmed.ncbi.nlm.nih.gov/21687738

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Friedreich's ataxia: a clinical and genetic study of 90 families with an analysis of early diagnostic criteria and intrafamilial clustering of clinical features

1 reference

https://pubmed.ncbi.nlm.nih.gov/21687738

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Free radicals and tissue damage produced by exercise

1 reference

https://pubmed.ncbi.nlm.nih.gov/21687738

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Identifiers

10.1371/JOURNAL.PONE.0020666

1 reference

Europe PubMed Central

PubMed publication ID

30 July 2017

2011PLoSO...620666G

0 references

PMC publication ID

1 reference

Europe PubMed Central

PubMed publication ID

30 July 2017

PubMed publication ID

1 reference

Europe PubMed Central

PubMed publication ID

30 July 2017

ResearchGate publication ID

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