(Q34007930)

30 July 2017

title

A metabolomic comparison of mouse models of the Neuronal Ceroid Lipofuscinoses (English)

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30 July 2017

1

Reza M Salek

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Jonathan D. Cooper

object named as

Jonathan D Cooper

3

0 references

Julian L Griffin

7

object named as

Julian L Griffin

1 reference

Russell J Mortishire-Smith

30 July 2017

6

object named as

Russell J Mortishire-Smith

1 reference

30 July 2017

Michael R Pears

2

1 reference

30 July 2017

Hannah M Mitchison

4

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30 July 2017

David A Pearce

5

1 reference

30 July 2017

language of work or name

1 reference

3 April 2011

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Journal of Biomolecular NMR

30 July 2017

published in

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30 July 2017

volume

49

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30 July 2017

issue

3-4

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30 July 2017

page(s)

175-184

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A metabolomic study of the CRND8 transgenic mouse model of Alzheimer's disease

30 July 2017

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High resolution 1H NMR-based metabolomics indicates a neurotransmitter cycling deficit in cerebral tissue from a mouse model of Batten disease

5 July 2018

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5 July 2018

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Selectivity and types of cell death in the neuronal ceroid lipofuscinoses

5 July 2018

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Two motifs target Batten disease protein CLN3 to lysosomes in transfected nonneuronal and neuronal cells

5 July 2018

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A role in vacuolar arginine transport for yeast Btn1p and for human CLN3, the protein defective in Batten disease

5 July 2018

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Progress towards understanding the neurobiology of Batten disease or neuronal ceroid lipofuscinosis

5 July 2018

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A comparison of cell and tissue extraction techniques using high-resolution 1H-NMR spectroscopy

5 July 2018

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The gene mutated in variant late-infantile neuronal ceroid lipofuscinosis (CLN6) and in nclf mutant mice encodes a novel predicted transmembrane protein

5 July 2018

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CLN3 protein is targeted to neuronal synapses but excluded from synaptic vesicles: new clues to Batten disease

5 July 2018

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Changes in GABAergic neuron distribution in situ and in neuron cultures in ovine (OCL6) Batten disease

5 July 2018

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Intraneuronal N-acetylaspartate supplies acetyl groups for myelin lipid synthesis: evidence for myelin-associated aspartoacylase

5 July 2018

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Proton NMR chemical shifts and coupling constants for brain metabolites

5 July 2018

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5 July 2018

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The neuronal ceroid lipofuscinoses in human EPMR and mnd mutant mice are associated with mutations in CLN8

5 July 2018

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5 July 2018

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Action of BTN1, the yeast orthologue of the gene mutated in Batten disease

5 July 2018

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Apparent loss and hypertrophy of interneurons in a mouse model of neuronal ceroid lipofuscinosis: evidence for partial response to insulin-like growth factor-1 treatment

5 July 2018

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5 July 2018

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5 July 2018

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5 July 2018

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5 July 2018

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Accumulation of the adenosine triphosphate synthase subunit C in the mnd mutant mouse. A model for neuronal ceroid lipofuscinosis

5 July 2018

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Retinal degeneration in motor neuron degeneration: a mouse model of ceroid lipofuscinosis

5 July 2018

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The relationship between lipofuscin pigment and ageing in the human nervous system

5 July 2018

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Impaired glutamate transport and glutamate-glutamine cycling: downstream effects of the Huntington mutation

5 July 2018

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Regional and cellular neuropathology in the palmitoyl protein thioesterase-1 null mutant mouse model of infantile neuronal ceroid lipofuscinosis

21 January 2018

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21 January 2018

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Altered arginine metabolism in the central nervous system (CNS) of the Cln3-/- mouse model of juvenile Batten disease

21 January 2018

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An autoantibody inhibitory to glutamic acid decarboxylase in the neurodegenerative disorder Batten disease

21 January 2018

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btn1, the Schizosaccharomyces pombe homologue of the human Batten disease gene CLN3, regulates vacuole homeostasis.

21 January 2018

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Vitamin E deficiency and metabolic deficits in neuronal ceroid lipofuscinosis described by bioinformatics.

21 January 2018

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Analysis of phospholipid molecular species in brains from patients with infantile and juvenile neuronal-ceroid lipofuscinosis using liquid chromatography-electrospray ionization mass spectrometry

21 January 2018

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Glutamate-glutamine cycling in the epileptic human hippocampus

21 January 2018

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Late onset neurodegeneration in the Cln3-/- mouse model of juvenile neuronal ceroid lipofuscinosis is preceded by low level glial activation.

21 January 2018

1 reference

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A metabolomic study of brain tissues from aged mice with low expression of the vesicular monoamine transporter 2 (VMAT2) gene

21 January 2018

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Orthogonal projections to latent structures (O-PLS)

21 January 2018

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Ultrastructural changes in neurons of the spinal anterior horn of ageing mice with particular reference to the accumulation of lipofuscin pigment

21 January 2018

1 reference

PubMed

https://pubmed.ncbi.nlm.nih.gov/21461951

inferred from PubMed ID database lookup

12 December 2020

based on heuristic

Identifiers

DOI

10.1007/S10858-011-9491-7

1 reference

30 July 2017

1 reference

30 July 2017

1 reference