(Q34180706)

31 July 2017

title

Stability and Cu(II) binding of prion protein variants related to inherited human prion diseases (English)

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31 July 2017

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4

Sabine Van Doorslaer

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author name string

Grazia M Cereghetti

series ordinal

1

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31 July 2017

Arthur Schweiger

series ordinal

2

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31 July 2017

Rudi Glockshuber

series ordinal

3

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31 July 2017

language of work or name

English

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publication date

1 March 2003

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31 July 2017

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31 July 2017

volume

84

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31 July 2017

issue

3

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31 July 2017

page(s)

1985-1997

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Molecular features of the copper binding sites in the octarepeat domain of the prion protein

31 July 2017

cites work

1 reference

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Mapping Cu(II) binding sites in prion proteins by diethyl pyrocarbonate modification and matrix-assisted laser desorption ionization-time of flight (MALDI-TOF) mass spectrometric footprinting

5 July 2018

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Location and properties of metal-binding sites on the human prion protein.

5 July 2018

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Electron paramagnetic resonance evidence for binding of Cu(2+) to the C-terminal domain of the murine prion protein

5 July 2018

1 reference

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Prion diseases of humans and animals: their causes and molecular basis

5 July 2018

1 reference

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Identification of the Cu2+ binding sites in the N-terminal domain of the prion protein by EPR and CD spectroscopy

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1302768

NMR structure of the bovine prion protein

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1302768

Copper binding to octarepeat peptides of the prion protein monitored by mass spectrometry

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1302768

NMR solution structure of the human prion protein

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1302768

Molecular dynamics simulations of human prion protein: importance of correct treatment of electrostatic interactions

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1302768

Influence of amino acid substitutions related to inherited human prion diseases on the thermodynamic stability of the cellular prion protein

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1302768

Copper binding to the prion protein: structural implications of four identical cooperative binding sites

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1302768

Copper stimulates endocytosis of the prion protein

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1302768

Prion protein NMR structure and familial human spongiform encephalopathies

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1302768

A scrapie-like unfolding intermediate of the prion protein domain PrP(121-231) induced by acidic pH.

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1302768

The cellular prion protein binds copper in vivo

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1302768

Structure of the recombinant full-length hamster prion protein PrP(29-231): the N terminus is highly flexible

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1302768

Prion diseases and the BSE crisis

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1302768

The role of PrP in pathogenesis of experimental scrapie

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1302768

Neuropsychological function in patients with Gerstmann-Sträussler-Scheinker disease from the Indiana kindred (F198S).

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1302768

Autonomous and reversible folding of a soluble amino-terminally truncated segment of the mouse prion protein.

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1302768

Measurement of endosome pH following folate receptor-mediated endocytosis.

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1302768

NMR structure of the mouse prion protein domain PrP(121-231)

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1302768

Complete penetrance of Creutzfeldt-Jakob disease in Libyan Jews carrying the E200K mutation in the prion protein gene

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1302768

Seeding "one-dimensional crystallization" of amyloid: a pathogenic mechanism in Alzheimer's disease and scrapie?

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1302768

Neuropathology of spongiform encephalopathies in humans

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1302768

Proposed three-dimensional structure for the cellular prion protein

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1302768

Structural clues to prion replication

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1302768

Conversion of alpha-helices into beta-sheets features in the formation of the scrapie prion proteins

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1302768

Gerstmann-Sträussler-Scheinker disease and the Indiana kindred

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1302768

Fatal familial insomnia and familial Creutzfeldt-Jakob disease: clinical, pathological and molecular features.

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1302768

Novel proteinaceous infectious particles cause scrapie

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1302768

Self-replication and scrapie

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1302768

Rapid and efficient site-specific mutagenesis without phenotypic selection

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1302768

Scrapie prion proteins are synthesized in neurons

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1302768

Calculation of protein extinction coefficients from amino acid sequence data

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1302768

Scrapie prion protein contains a phosphatidylinositol glycolipid

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1302768

Identification of glycoinositol phospholipid linked and truncated forms of the scrapie prion protein

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1302768

Molecular mass, biochemical composition, and physicochemical behavior of the infectious form of the scrapie precursor protein monomer

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1302768

Efficient site-directed mutagenesis using uracil-containing DNA.

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1302768

Molecular biology of prion diseases

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1302768

Fatal familial insomnia and familial Creutzfeldt-Jakob disease: disease phenotype determined by a DNA polymorphism

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1302768

Aberrant metal binding by prion protein in human prion disease.

5 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1302768

XAFS study of the high-affinity copper-binding site of human PrP(91-231) and its low-resolution structure in solution

28 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1302768

Copper refolding of prion protein.

28 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1302768

Amyloidogenicity and neurotoxicity of peptides corresponding to the helical regions of PrP(C).

28 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1302768

Novel PRNP sequence variant associated with familial encephalopathy

28 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1302768

Raman spectroscopic study on the copper(II) binding mode of prion octapeptide and its pH dependence

28 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1302768

Influence of mutations associated with familial prion-related encephalopathies on biological activity of prion protein peptides

28 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1302768

Familial mutations and the thermodynamic stability of the recombinant human prion protein

28 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1302768

Prion protein selectively binds copper(II) ions

28 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1302768

The cellular prion protein binds copper in vivo

28 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1302768

NMR characterization of the full-length recombinant murine prion protein, mPrP(23-231).

28 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1302768

Copper binding to the N-terminal tandem repeat regions of mammalian and avian prion protein.

28 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1302768

Structural implications derived from the analysis of electron paramagnetic resonance spectra of natural and artificial copper proteins.

28 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1302768

Strain-specific prion-protein conformation determined by metal ions

28 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1302768

B lymphocytes and neuroinvasion

28 October 2018

1 reference

https://api.crossref.org/works/10.1016%2FS0006-3495%2803%2975007-3

Inherited prion encephalopathy associated with the novel PRNP H187R mutation: a clinical study

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0006-3495%2803%2975007-3

Diversity of oligosaccharide structures linked to asparagines of the scrapie prion protein

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0006-3495%2803%2975007-3

Copper binding to the N-terminal tandem repeat region of mammalian and avian prion protein: structural studies using synthetic peptides

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0006-3495%2803%2975007-3

Prion protein binds copper within the physiological concentration range

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0006-3495%2803%2975007-3

Unraveling the Cu2+Binding Sites in the C-Terminal Domain of the Murine Prion Protein: A Pulse EPR and ENDOR Study†

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0006-3495%2803%2975007-3

Brain copper content and cuproenzyme activity do not vary with prion protein expression level

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0006-3495%2803%2975007-3

Copper has differential effect on prion protein with polymorphism of position 129

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0006-3495%2803%2975007-3

10.1016/S0006-3495(03)75007-3

7 January 2021

Identifiers

DOI

1 reference

31 July 2017

1 reference

31 July 2017

1 reference