(Q34518069)

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Correlation of Utrophin Levels with the Dystrophin Protein Complex and Muscle Fibre Regeneration in Duchenne and Becker Muscular Dystrophy Muscle Biopsies

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scholarly article

1 reference

Europe PubMed Central

PubMed publication ID

2 August 2017

Correlation of Utrophin Levels with the Dystrophin Protein Complex and Muscle Fibre Regeneration in Duchenne and Becker Muscular Dystrophy Muscle Biopsies (English)

1 reference

Europe PubMed Central

PubMed publication ID

2 August 2017

0 references

Becker muscular dystrophy

1 reference

based on heuristic

inferred from title

5

object named as

Kay E Davies

1 reference

Europe PubMed Central

PubMed publication ID

2 August 2017

Jonathon Tinsley

7

object named as

Jonathon Tinsley

1 reference

Europe PubMed Central

PubMed publication ID

2 August 2017

author name string

Narinder Janghra

1

1 reference

Europe PubMed Central

PubMed publication ID

2 August 2017

Jennifer E Morgan

2

1 reference

Europe PubMed Central

PubMed publication ID

2 August 2017

Caroline A Sewry

3

1 reference

Europe PubMed Central

PubMed publication ID

2 August 2017

Francis X Wilson

4

1 reference

Europe PubMed Central

PubMed publication ID

2 August 2017

Francesco Muntoni

6

1 reference

Europe PubMed Central

PubMed publication ID

2 August 2017

language of work or name

0 references

publication date

14 March 2016

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Europe PubMed Central

PubMed publication ID

2 August 2017

1 reference

Europe PubMed Central

PubMed publication ID

2 August 2017

11

1 reference

Europe PubMed Central

PubMed publication ID

2 August 2017

3

1 reference

Europe PubMed Central

PubMed publication ID

2 August 2017

e0150818

1 reference

Europe PubMed Central

PubMed publication ID

2 August 2017

copyright license

Creative Commons Attribution 4.0 International

14 March 2016

1 reference

April 2022 Public Data File from Crossref

copyright status

0 references

Concordant utrophin upregulation in phenotypically discordant DMD/BMD brothers

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4790853

7 July 2018

Developmental myosins: expression patterns and functional significance

1 reference

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7 July 2018

Second-generation compound for the modulation of utrophin in the therapy of DMD.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4790853

7 July 2018

The NorthStar Ambulatory Assessment in Duchenne muscular dystrophy: considerations for the design of clinical trials

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4790853

7 July 2018

Safety, tolerability, and pharmacokinetics of SMT C1100, a 2-arylbenzoxazole utrophin modulator, following single- and multiple-dose administration to healthy male adult volunteers

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4790853

7 July 2018

A sensitive, reproducible and objective immunofluorescence analysis method of dystrophin in individual fibers in samples from patients with duchenne muscular dystrophy

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4790853

7 July 2018

Microtubule binding distinguishes dystrophin from utrophin

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4790853

7 July 2018

Muscular dystrophy: new challenges and review of the current clinical trials.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4790853

7 July 2018

Clinical trials using antisense oligonucleotides in duchenne muscular dystrophy.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4790853

7 July 2018

Proteomic analysis reveals new cardiac-specific dystrophin-associated proteins

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4790853

7 July 2018

Dystrophin quantification and clinical correlations in Becker muscular dystrophy: implications for clinical trials

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4790853

7 July 2018

Restoration of the dystrophin-associated glycoprotein complex after exon skipping therapy in Duchenne muscular dystrophy

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4790853

7 July 2018

Level of muscle regeneration in limb-girdle muscular dystrophy type 2I relates to genotype and clinical severity

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4790853

7 July 2018

Exon skipping and dystrophin restoration in patients with Duchenne muscular dystrophy after systemic phosphorodiamidate morpholino oligomer treatment: an open-label, phase 2, dose-escalation study

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4790853

7 July 2018

Daily treatment with SMTC1100, a novel small molecule utrophin upregulator, dramatically reduces the dystrophic symptoms in the mdx mouse

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4790853

7 July 2018

Sarcolemmal nNOS anchoring reveals a qualitative difference between dystrophin and utrophin.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4790853

7 July 2018

Dystrophin, its interactions with other proteins, and implications for muscular dystrophy

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4790853

7 July 2018

Dystrophin and mutations: one gene, several proteins, multiple phenotypes

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4790853

7 July 2018

A- and B-utrophin have different expression patterns and are differentially up-regulated in mdx muscle

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4790853

7 July 2018

Expression of full-length utrophin prevents muscular dystrophy in mdx mice

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4790853

7 July 2018

Deficiency of dystrophin-associated proteins in Duchenne muscular dystrophy patients lacking COOH-terminal domains of dystrophin

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4790853

7 July 2018

Preservation of the C-terminus of dystrophin molecule in the skeletal muscle from Becker muscular dystrophy

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4790853

7 July 2018

Effect of dystrophin gene deletions on mRNA levels and processing in Duchenne and Becker muscular dystrophies

1 reference

https://api.crossref.org/works/10.1371%2FJOURNAL.PONE.0150818

21 January 2018

Eteplirsen for the treatment of Duchenne muscular dystrophy

1 reference

https://api.crossref.org/works/10.1371%2FJOURNAL.PONE.0150818

21 January 2018

AAV vector-mediated microdystrophin expression in a relatively small percentage of mdx myofibers improved the mdx phenotype

1 reference

https://api.crossref.org/works/10.1371%2FJOURNAL.PONE.0150818

21 January 2018

Dystrophin-related protein, utrophin, in normal and dystrophic human fetal skeletal muscle

1 reference

https://api.crossref.org/works/10.1371%2FJOURNAL.PONE.0150818

21 January 2018

A and B utrophin in human muscle and sarcolemmal A-utrophin associated with tumours

1 reference

https://api.crossref.org/works/10.1371%2FJOURNAL.PONE.0150818

21 January 2018

Consequences of the combined deficiency in dystrophin and utrophin on the mechanical properties and myosin composition of some limb and respiratory muscles of the mouse.

1 reference

https://api.crossref.org/works/10.1371%2FJOURNAL.PONE.0150818

21 January 2018

Absence of neuronal nitric oxide synthase (nNOS) as a pathological marker for the diagnosis of Becker muscular dystrophy with rod domain deletions

1 reference

https://api.crossref.org/works/10.1371%2FJOURNAL.PONE.0150818

21 January 2018

Prevention of pathology in mdx mice by expression of utrophin: analysis using an inducible transgenic expression system.

1 reference

https://api.crossref.org/works/10.1371%2FJOURNAL.PONE.0150818

21 January 2018

ZZ domain is essentially required for the physiological binding of dystrophin and utrophin to beta-dystroglycan

1 reference

https://api.crossref.org/works/10.1371%2FJOURNAL.PONE.0150818

21 January 2018

Muscle precursor cells injected into irradiated mdx mouse muscle persist after serial injury.

1 reference

https://api.crossref.org/works/10.1371%2FJOURNAL.PONE.0150818

21 January 2018

Utrophin is a regeneration-associated protein transiently present at the sarcolemma of regenerating skeletal muscle fibers in dystrophin-deficient hypertrophic feline muscular dystrophy.

1 reference

https://api.crossref.org/works/10.1371%2FJOURNAL.PONE.0150818

21 January 2018

Immunohistological intensity measurements as a tool to assess sarcolemma-associated protein expression

1 reference

https://api.crossref.org/works/10.1371%2FJOURNAL.PONE.0150818

21 January 2018

Comparison of skeletal muscle pathology and motor function of dystrophin and utrophin deficient mouse strains

1 reference

https://api.crossref.org/works/10.1371%2FJOURNAL.PONE.0150818

21 January 2018

Amelioration of the dystrophic phenotype of mdx mice using a truncated utrophin transgene

1 reference

https://api.crossref.org/works/10.1371%2FJOURNAL.PONE.0150818

21 January 2018

The abnormal expression of utrophin in Duchenne and Becker muscular dystrophy is age related

1 reference

https://pubmed.ncbi.nlm.nih.gov/26974331

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Absence of correlation between utrophin localization and quantity and the clinical severity in Duchenne/Becker dystrophies

1 reference

https://pubmed.ncbi.nlm.nih.gov/26974331

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Duchenne muscular dystrophy: deficiency of dystrophin-associated proteins in the sarcolemma

1 reference

https://pubmed.ncbi.nlm.nih.gov/26974331

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Expression of utrophin (dystrophin-related protein) during regeneration and maturation of skeletal muscle in canine X-linked muscular dystrophy

1 reference

https://pubmed.ncbi.nlm.nih.gov/26974331

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Sustained AAV-mediated dystrophin expression in a canine model of Duchenne muscular dystrophy with a brief course of immunosuppression

1 reference

https://pubmed.ncbi.nlm.nih.gov/26974331

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Quantitation of muscle function in children: a prospective study in Duchenne muscular dystrophy

1 reference

https://pubmed.ncbi.nlm.nih.gov/26974331

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Asymptomatic Becker muscular dystrophy: histological changes in biopsied muscles

1 reference

https://pubmed.ncbi.nlm.nih.gov/26974331

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Expression of utrophin (dystrophin-related protein) and dystrophin-associated glycoproteins in muscles from patients with Duchenne muscular dystrophy

1 reference

https://pubmed.ncbi.nlm.nih.gov/26974331

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

The dystrophin-related protein, utrophin, is expressed on the sarcolemma of regenerating human skeletal muscle fibres in dystrophies and inflammatory myopathies

1 reference

https://pubmed.ncbi.nlm.nih.gov/26974331

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Naturally occurring utrophin correlates with disease severity in Duchenne muscular dystrophy

1 reference

https://pubmed.ncbi.nlm.nih.gov/26974331

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Identifiers

10.1371/JOURNAL.PONE.0150818

1 reference

Europe PubMed Central

PubMed publication ID

2 August 2017

2016PLoSO..1150818J

0 references

PMC publication ID

1 reference

Europe PubMed Central

PubMed publication ID

2 August 2017

PubMed publication ID

1 reference

Europe PubMed Central

PubMed publication ID

2 August 2017

ResearchGate publication ID

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