(Q34554753)

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:25312000%20AND%20SRC:MED&resulttype=core&format=json

21 February 2020

title

Neuronal and astrocyte dysfunction diverges from embryonic fibroblasts in the Ndufs4fky/fky mouse (English)

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:25312000%20AND%20SRC:MED&resulttype=core&format=json

21 February 2020

0 references

1

0 references

Michael T Ryan

series ordinal

5

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:25312000%20AND%20SRC:MED&resulttype=core&format=json

21 February 2020

David Thorburn

series ordinal

6

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:25312000%20AND%20SRC:MED&resulttype=core&format=json

21 February 2020

7

Ann E Frazier

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:25312000%20AND%20SRC:MED&resulttype=core&format=json

21 February 2020

4

Adrienne Laskowski

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:25312000%20AND%20SRC:MED&resulttype=core&format=json

21 February 2020

3

Jasper C Komen

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:25312000%20AND%20SRC:MED&resulttype=core&format=json

21 February 2020

author name string

Xiaonan W Wijeyeratne

series ordinal

2

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:25312000%20AND%20SRC:MED&resulttype=core&format=json

21 February 2020

publication date

21 November 2014

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:25312000%20AND%20SRC:MED&resulttype=core&format=json

21 February 2020

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:25312000%20AND%20SRC:MED&resulttype=core&format=json

21 February 2020

volume

34

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:25312000%20AND%20SRC:MED&resulttype=core&format=json

21 February 2020

issue

6

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:25312000%20AND%20SRC:MED&resulttype=core&format=json

21 February 2020

page(s)

e00151

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:25312000%20AND%20SRC:MED&resulttype=core&format=json

Creative Commons Attribution 3.0 Unported

21 February 2020

copyright license

start time

25 July 2019

1 reference

April 2022 Public Data File from Crossref

copyright status

copyrighted

0 references

cites work

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7 July 2018

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Astrocytic energetics during excitatory neurotransmission: What are contributions of glutamate oxidation and glycolysis?

7 July 2018

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7 July 2018

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7 July 2018

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7 July 2018

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Molecular mechanisms of superoxide production by the mitochondrial respiratory chain.

7 July 2018

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Fatal breathing dysfunction in a mouse model of Leigh syndrome

7 July 2018

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Proteomic and metabolomic analyses of mitochondrial complex I-deficient mouse model generated by spontaneous B2 short interspersed nuclear element (SINE) insertion into NADH dehydrogenase (ubiquinone) Fe-S protein 4 (Ndufs4) gene

7 July 2018

1 reference

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Metabolic consequences of NDUFS4 gene deletion in immortalized mouse embryonic fibroblasts.

7 July 2018

1 reference

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Biochemical analyses of the electron transport chain complexes by spectrophotometry.

7 July 2018

1 reference

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Diagnosis and treatment of mitochondrial myopathies

7 July 2018

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Astrocytes and microglia: responses to neuropathological conditions

7 July 2018

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Loss of mitochondrial complex I activity potentiates dopamine neuron death induced by microtubule dysfunction in a Parkinson's disease model

7 July 2018

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Specification and morphogenesis of astrocytes

7 July 2018

1 reference

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Complex I deficiency due to loss of Ndufs4 in the brain results in progressive encephalopathy resembling Leigh syndrome

7 July 2018

1 reference

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Mechanism of neurodegeneration of neurons with mitochondrial DNA mutations

7 July 2018

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Glycolysis: a bioenergetic or a survival pathway?

7 July 2018

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Mitochondria as ATP consumers in cellular pathology

7 July 2018

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The pathophysiology of mitochondrial disease as modeled in the mouse

7 July 2018

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Mitochondrial complex I deficiency: from organelle dysfunction to clinical disease.

7 July 2018

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Glucose metabolism inhibits apoptosis in neurons and cancer cells by redox inactivation of cytochrome c.

7 July 2018

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The mystery and magic of glia: a perspective on their roles in health and disease

7 July 2018

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Mitochondrial complex I inhibition is not required for dopaminergic neuron death induced by rotenone, MPP+, or paraquat.

7 July 2018

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Mice with mitochondrial complex I deficiency develop a fatal encephalomyopathy

7 July 2018

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Mitochondrial disorders in the nervous system

7 July 2018

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Mitochondrial ND5 gene variation associated with encephalomyopathy and mitochondrial ATP consumption

7 July 2018

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Human CIA30 is involved in the early assembly of mitochondrial complex I and mutations in its gene cause disease

7 July 2018

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Analysis of the assembly profiles for mitochondrial- and nuclear-DNA-encoded subunits into complex I

7 July 2018

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Mitochondrial respiratory chain supercomplexes are destabilized in Barth Syndrome patients

7 July 2018

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Reactive astrocytes in neural repair and protection

7 July 2018

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Mitochondria, oxidants, and aging

7 July 2018

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Glutathione pathways in the brain.

7 July 2018

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Clinical spectrum and diagnosis of mitochondrial disorders

7 July 2018

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Cloning of neuronal mtDNA variants in cultured cells by synaptosome fusion with mtDNA-less cells

7 July 2018

1 reference

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Role of astrocytes in the clearance of excess extracellular potassium

7 July 2018

1 reference

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Functional F1-ATPase essential in maintaining growth and membrane potential of human mitochondrial DNA-depleted rho degrees cells

7 July 2018

1 reference

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The ATP synthase--a splendid molecular machine

7 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4240023

Pathogenic factors underlying the lesions in Leigh's disease. Tissue responses to cellular energy deprivation and their clinico-pathological consequences

7 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4240023

Minimum birth prevalence of mitochondrial respiratory chain disorders in children

7 July 2018

1 reference

https://api.crossref.org/works/10.1042%2FBSR20140151

Leigh syndrome: clinical features and biochemical and DNA abnormalities.

21 January 2018

1 reference

https://api.crossref.org/works/10.1042%2FBSR20140151

A constant and similar assembly defect of mitochondrial respiratory chain complex I allows rapid identification of NDUFS4 mutations in patients with Leigh syndrome.

21 January 2018

1 reference

https://api.crossref.org/works/10.1042%2FBSR20140151

Primary fibroblasts of NDUFS4(-/-) mice display increased ROS levels and aberrant mitochondrial morphology

21 January 2018

1 reference

https://api.crossref.org/works/10.1042%2FBSR20140151

Superoxide production is inversely related to complex I activity in inherited complex I deficiency.

21 January 2018

1 reference

https://api.crossref.org/works/10.1042%2FBSR20140151

Mitochondrial and cytosolic thiol redox state are not detectably altered in isolated human NADH:ubiquinone oxidoreductase deficiency.

21 January 2018

1 reference

https://api.crossref.org/works/10.1042%2FBSR20140151

Culturing hippocampal and cortical neurons

21 January 2018

1 reference

https://api.crossref.org/works/10.1042%2FBSR20140151

Analysis of mitochondrial subunit assembly into respiratory chain complexes using Blue Native polyacrylamide gel electrophoresis.

21 January 2018

1 reference

https://api.crossref.org/works/10.1042%2FBSR20140151

Mitochondrial reactive oxygen species in mice lacking superoxide dismutase 2: attenuation via antioxidant treatment

21 January 2018

1 reference

https://api.crossref.org/works/10.1042%2FBSR20140151

Quantitation and origin of the mitochondrial membrane potential in human cells lacking mitochondrial DNA.

21 January 2018

1 reference

https://api.crossref.org/works/10.1042%2FBSR20140151

Regulation of mitochondrial structure and function by the F1Fo-ATPase inhibitor protein, IF1.

21 January 2018

1 reference

https://api.crossref.org/works/10.1042%2FBSR20140151

Superoxide is produced by the reduced flavin in mitochondrial complex I: a single, unified mechanism that applies during both forward and reverse electron transfer

21 January 2018

1 reference

https://api.crossref.org/works/10.1042%2FBSR20140151

Mitochondrial metabolism of reactive oxygen species

21 January 2018

1 reference

12 December 2020

Titrating the effects of mitochondrial complex I impairment in the cell physiology

1 reference

12 December 2020

Purity, cell viability, expression of GFAP and bystin in astrocytes cultured by different procedures

1 reference

12 December 2020

Mitochondrial complex III stabilizes complex I in the absence of NDUFS4 to provide partial activity

1 reference

12 December 2020

Studies on mitochondrial oxidative phosphorylation in permeabilized human skin fibroblasts: application to mitochondrial encephalomyopathies

1 reference

12 December 2020

Identifiers

DOI

10.1042/BSR20140151

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:25312000%20AND%20SRC:MED&resulttype=core&format=json

21 February 2020

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:25312000%20AND%20SRC:MED&resulttype=core&format=json

21 February 2020

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:25312000%20AND%20SRC:MED&resulttype=core&format=json