(Q34650435)

3 August 2017

title

Glutathione: a redox signature in monitoring EPI-743 therapy in children with mitochondrial encephalomyopathies (English)

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3 August 2017

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12

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Gianna Di Giovamberardino

3 August 2017

Sara Petrillo

2

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Gianna Di Giovamberardino

7

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Giulia Tozzi

Giulia Tozzi

3

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Anna Pastore

Anna Pastore

1

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Fiorella Piemonte

Fiorella Piemonte

13

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Rosalba Carrozzo

Rosalba Carrozzo

4

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Carlo Dionisi-Vici

Carlo Dionisi-Vici

6

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Diego Martinelli

5

Diego Martinelli

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3 August 2017

10

Guy Miller

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3 August 2017

Ferdinando Ceravolo

8

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3 August 2017

Matthew B Klein

9

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3 August 2017

Gregory M Enns

11

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3 August 2017

publication date

24 March 2013

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Molecular Genetics and Metabolism

3 August 2017

published in

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3 August 2017

volume

109

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3 August 2017

issue

2

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3 August 2017

page(s)

208-214

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Mitochondrial energetics and therapeutics

3 August 2017

cites work

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X-linked Leigh's syndrome

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Inherited disorders affecting mitochondrial function are associated with glutathione deficiency and hypocitrullinemia

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7 January 2021

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7 January 2021

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Biological markers of oxidative stress in mitochondrial myopathies with progressive external ophthalmoplegia

7 January 2021

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Increased expression of manganese-superoxide dismutase in fibroblasts of patients with CPEO syndrome

7 January 2021

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7 January 2021

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7 January 2021

Identifiers

DOI

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3 August 2017

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