(Q35016854)

English

Progressive retinal degeneration and glial activation in the CLN6 (nclf) mouse model of neuronal ceroid lipofuscinosis: a beneficial effect of DHA and curcumin supplementation

scientific article

In more languages

Statements

scholarly article

1 reference

Europe PubMed Central

5 August 2017

Progressive retinal degeneration and glial activation in the CLN6 (nclf) mouse model of neuronal ceroid lipofuscinosis: a beneficial effect of DHA and curcumin supplementation (English)

1 reference

Europe PubMed Central

5 August 2017

0 references

retinal degeneration

1 reference

based on heuristic

inferred from title

neuronal ceroid lipofuscinosis

1 reference

based on heuristic

inferred from title

object named as

Ernst R Tamm

7

0 references

author name string

Myriam Mirza

1

1 reference

Europe PubMed Central

5 August 2017

Cornelia Volz

2

1 reference

Europe PubMed Central

5 August 2017

Marcus Karlstetter

3

1 reference

Europe PubMed Central

5 August 2017

Monica Langiu

4

1 reference

Europe PubMed Central

5 August 2017

Aleksandra Somogyi

5

1 reference

Europe PubMed Central

5 August 2017

Mika O Ruonala

6

1 reference

Europe PubMed Central

5 August 2017

Herbert Jägle

8

1 reference

Europe PubMed Central

5 August 2017

Thomas Langmann

9

1 reference

Europe PubMed Central

5 August 2017

language of work or name

0 references

publication date

4 October 2013

1 reference

Europe PubMed Central

5 August 2017

1 reference

Europe PubMed Central

5 August 2017

8

1 reference

Europe PubMed Central

5 August 2017

10

1 reference

Europe PubMed Central

5 August 2017

e75963

1 reference

Europe PubMed Central

5 August 2017

copyright license

Creative Commons Attribution 4.0 International

4 October 2013

1 reference

April 2022 Public Data File from Crossref

copyright status

0 references

Altered biometal homeostasis is associated with CLN6 mRNA loss in mouse neuronal ceroid lipofuscinosis

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3790850

8 July 2018

Sterile alpha motif containing 7 (samd7) is a novel crx-regulated transcriptional repressor in the retina

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3790850

8 July 2018

The role of nonsense-mediated decay in neuronal ceroid lipofuscinosis

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3790850

8 July 2018

Large-scale phenotyping of an accurate genetic mouse model of JNCL identifies novel early pathology outside the central nervous system

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3790850

8 July 2018

Disruption of the autophagy-lysosome pathway is involved in neuropathology of the nclf mouse model of neuronal ceroid lipofuscinosis

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3790850

8 July 2018

The Rd8 mutation of the Crb1 gene is present in vendor lines of C57BL/6N mice and embryonic stem cells, and confounds ocular induced mutant phenotypes

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3790850

8 July 2018

Update of the mutation spectrum and clinical correlations of over 360 mutations in eight genes that underlie the neuronal ceroid lipofuscinoses

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3790850

8 July 2018

Role of microglia in CNS inflammation

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3790850

8 July 2018

Kufs disease, the major adult form of neuronal ceroid lipofuscinosis, caused by mutations in CLN6

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3790850

8 July 2018

Distinct early molecular responses to mutations causing vLINCL and JNCL presage ATP synthase subunit C accumulation in cerebellar cells

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3790850

8 July 2018

Can consuming flavonoids restore old microglia to their youthful state?

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3790850

8 July 2018

Immunosuppression alters disease severity in juvenile Batten disease mice

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3790850

8 July 2018

Pathogenic mutations cause rapid degradation of lysosomal storage disease-related membrane protein CLN6.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3790850

8 July 2018

Curcumin protects retinal cells from light-and oxidant stress-induced cell death

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3790850

8 July 2018

Curcumin attenuates the release of pro-inflammatory cytokines in lipopolysaccharide-stimulated BV2 microglia

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3790850

8 July 2018

Neurotrophins enhance retinal pigment epithelial cell survival through neuroprotectin D1 signaling

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3790850

8 July 2018

The neuronal ceroid-lipofuscinoses: from past to present

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3790850

8 July 2018

Ocular phenotype in a mouse gene knockout model for infantile neuronal ceroid lipofuscinosis

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3790850

8 July 2018

Molecular genetics of the NCLs -- status and perspectives

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3790850

8 July 2018

Independent visual threshold measurements in the two eyes of freely moving rats and mice using a virtual-reality optokinetic system.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3790850

8 July 2018

The genomic response to retinal disease and injury: evidence for endothelin signaling from photoreceptors to glia.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3790850

8 July 2018

The neuronal ceroid-lipofuscinoses

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3790850

8 July 2018

Mutations in a novel CLN6-encoded transmembrane protein cause variant neuronal ceroid lipofuscinosis in man and mouse

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3790850

8 July 2018

The gene mutated in variant late-infantile neuronal ceroid lipofuscinosis (CLN6) and in nclf mutant mice encodes a novel predicted transmembrane protein

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3790850

8 July 2018

Progress in neuropathology of the neuronal ceroid lipofuscinoses

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3790850

8 July 2018

Neuronal ceroid lipofuscinosis (nclf), a new disorder of the mouse linked to chromosome 9

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3790850

8 July 2018

Human forms of neuronal ceroid-lipofuscinosis (Batten disease): consensus on diagnostic criteria, Hamburg 1992.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3790850

8 July 2018

Pharmacology of Curcuma longa

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3790850

8 July 2018

Ocular pathology in infantile type of neuronal ceroid-lipofuscinosis

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3790850

8 July 2018

Neuronal ceroid lipofuscinoses

1 reference

https://api.crossref.org/works/10.1371%2FJOURNAL.PONE.0075963

21 January 2018

Glial activation spreads from specific cerebral foci and precedes neurodegeneration in presymptomatic ovine neuronal ceroid lipofuscinosis (CLN6).

1 reference

https://api.crossref.org/works/10.1371%2FJOURNAL.PONE.0075963

21 January 2018

Immune cells perturb axons and impair neuronal survival in a mouse model of infantile neuronal ceroid lipofuscinosis.

1 reference

https://api.crossref.org/works/10.1371%2FJOURNAL.PONE.0075963

21 January 2018

Inhibitory effect of curcumin on nitric oxide production from lipopolysaccharide-activated primary microglia.

1 reference

https://api.crossref.org/works/10.1371%2FJOURNAL.PONE.0075963

21 January 2018

Docosahexaenoic acid attenuates microglial activation and delays early retinal degeneration.

1 reference

https://api.crossref.org/works/10.1371%2FJOURNAL.PONE.0075963

21 January 2018

Discordant anatomical, electrophysiological, and visual behavioral profiles of retinal degeneration in rat models of retinal degenerative disease

1 reference

https://api.crossref.org/works/10.1371%2FJOURNAL.PONE.0075963

21 January 2018

Regional and cellular neuropathology in the palmitoyl protein thioesterase-1 null mutant mouse model of infantile neuronal ceroid lipofuscinosis

1 reference

https://api.crossref.org/works/10.1371%2FJOURNAL.PONE.0075963

21 January 2018

High expression of disease-related Cln6 in the cerebral cortex, purkinje cells, dentate gyrus, and hippocampal ca1 neurons.

1 reference

https://api.crossref.org/works/10.1371%2FJOURNAL.PONE.0075963

21 January 2018

A missense mutation (c.184C>T) in ovine CLN6 causes neuronal ceroid lipofuscinosis in Merino sheep whereas affected South Hampshire sheep have reduced levels of CLN6 mRNA.

1 reference

https://api.crossref.org/works/10.1371%2FJOURNAL.PONE.0075963

21 January 2018

Curcumin protects pre-oligodendrocytes from activated microglia in vitro and in vivo

1 reference

https://api.crossref.org/works/10.1371%2FJOURNAL.PONE.0075963

21 January 2018

P23H and S334ter opsin mutations: Increasing photoreceptor outer segment n-3 fatty acid content does not affect the course of retinal degeneration

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3790850

25 October 2018

Rapid quantification of adult and developing mouse spatial vision using a virtual optomotor system

1 reference

https://pubmed.ncbi.nlm.nih.gov/24124525

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Docosahexaenoic acid modulates inflammatory and antineurogenic functions of activated microglial cells

1 reference

https://pubmed.ncbi.nlm.nih.gov/24124525

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Low erythrocyte plasmalogen and plasma docosahexaenoic acid (DHA) in juvenile neuronal ceroid-lipofuscinosis (JNCL)

1 reference

https://pubmed.ncbi.nlm.nih.gov/24124525

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Identifiers

10.1371/JOURNAL.PONE.0075963

1 reference

Europe PubMed Central

5 August 2017

2013PLoSO...875963M

0 references

1 reference

Europe PubMed Central

5 August 2017

1 reference

Europe PubMed Central

5 August 2017

ResearchGate publication ID

0 references

Sitelinks

Wikipedia(0 entries)

Wikibooks(0 entries)

Wikinews(0 entries)

Wikiquote(0 entries)

Wikisource(0 entries)

Wikiversity(0 entries)

Wikivoyage(0 entries)

Wiktionary(0 entries)

Multilingual sites(0 entries)

Retrieved from "https://www.wikidata.org/w/index.php?title=Q35016854&oldid=1863829574"