(Q35157608)

6 August 2017

1 reference

title

The chemical biology of branched-chain lipid metabolism (English)

1 reference

6 August 2017

Christopher J. Schofield

series ordinal

2

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6 August 2017

3

Anthony S Wierzbicki

1 reference

6 August 2017

5

Ronald J A Wanders

1 reference

6 August 2017

Matthew D Lloyd

6

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ORCID Public Data File 2021

author name string

Mridul Mukherji

series ordinal

1

1 reference

PubMed ID

12814641

6 August 2017

Gerbert A Jansen

series ordinal

4

1 reference

PubMed ID

12814641

6 August 2017

language of work or name

1 reference

1 September 2003

1 reference

Progress in Lipid Research

6 August 2017

1 reference

6 August 2017

42

1 reference

6 August 2017

359-376

1 reference

6 August 2017

5

1 reference

A conserved tripeptide sorts proteins to peroxisomes

6 August 2017

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Peroxisome targeting signal of rat liver acyl-coenzyme A oxidase resides at the carboxy terminus

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Human metabolism of phytanic acid and pristanic acid

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Pathways of straight and branched chain fatty acid catabolism in higher plants

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Biochemistry of peroxisomes in health and disease

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Isolation and characterization of rat liver microsomal R-ibuprofenoyl-CoA synthetase.

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Chiral inversion of 2-arylpropionic acid non-steroidal anti-inflammatory drugs—II Racemization and hydrolysis of (R)- and (S)-ibuprofen-CoA thioesters

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

The metabolism of phytanic acid and pristanic acid in man: a review

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Lignoceroyl-CoASH ligase: enzyme defect in fatty acid beta-oxidation system in X-linked childhood adrenoleukodystrophy

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Mammalian mitochondrial beta-oxidation

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Fatty acid beta-oxidation in peroxisomes and mitochondria: the first, unequivocal evidence for the involvement of carnitine in shuttling propionyl-CoA from peroxisomes to mitochondria

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Molecular characterization of carnitine-dependent transport of acetyl-CoA from peroxisomes to mitochondria in Saccharomyces cerevisiae and identification of a plasma membrane carnitine transporter, Agp2p

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Peroxisomal beta-oxidation enzymes

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Identification of pristanoyl-CoA oxidase as a distinct, clofibrate non-inducible enzyme in rat liver peroxisomes

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Mutations in the gene encoding peroxisomal alpha-methylacyl-CoA racemase cause adult-onset sensory motor neuropathy

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

In mouse alpha -methylacyl-CoA racemase, the same gene product is simultaneously located in mitochondria and peroxisomes

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Reinvestigation of peroxisomal 3-ketoacyl-CoA thiolase deficiency: identification of the true defect at the level of d-bifunctional protein

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Induction and peroxisomal appearance of gulonolactone oxidase upon clofibrate treatment in mouse liver

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Tocopherols are metabolized in HepG2 cells by side chain omega-oxidation and consecutive beta-oxidation

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Refsum's disease: a peroxisomal disorder affecting phytanic acid alpha-oxidation

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Phytanic acid alpha-oxidation in rat liver peroxisomes. Production of alpha-hydroxyphytanoyl-CoA and formate is enhanced by dioxygenase cofactors

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Identification of pristanal dehydrogenase activity in peroxisomes: conclusive evidence that the complete phytanic acid alpha-oxidation pathway is localized in peroxisomes

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Phytanic acid alpha-oxidation: identification of 2-hydroxyphytanoyl-CoA lyase in rat liver and its localisation in peroxisomes

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Purification, molecular cloning, and expression of 2-hydroxyphytanoyl-CoA lyase, a peroxisomal thiamine pyrophosphate-dependent enzyme that catalyzes the carbon-carbon bond cleavage during alpha-oxidation of 3-methyl-branched fatty acids

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Resolution of the phytanic acid alpha-oxidation pathway: identification of pristanal as product of the decarboxylation of 2-hydroxyphytanoyl-CoA

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Alpha-decarboxylation, an important pathway for degradation of phytanic acid in animals

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

A pathway for oxidative degradation of phytanic acid in mammals

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

The existence of an alternative pathway for the degradation of branch-chained fatty acids, and its failure in heredopathia atactica polyneuritiformis (Refsum's disease).

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Refsum's disease: characterization of the enzyme defect in cell culture

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Refsum's disease: nature of the enzyme defect

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Localization of the oxidative defect in phytanic acid degradation in patients with Refsum's disease

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Human phytanoyl-CoA hydroxylase: resolution of the gene structure and the molecular basis of Refsum's disease.

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Refsum disease is caused by mutations in the phytanoyl-CoA hydroxylase gene

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Identification of PAHX, a Refsum disease gene

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Identification of PEX7 as the second gene involved in Refsum disease

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Involvement of microsomal fatty aldehyde dehydrogenase in the alpha-oxidation of phytanic acid.

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Clinical, biochemical and molecular genetic characteristics of 19 patients with the Sjögren-Larsson syndrome

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Inherited disorders of fatty alcohol metabolism

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

The molecular basis of Sjögren-Larsson syndrome: mutation analysis of the fatty aldehyde dehydrogenase gene

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

The formation of alpha-hydroxy phytanic acid from phytanic acid in mammalian tissues

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Characterization of phytanoyl-Coenzyme A hydroxylase in human liver and activity measurements in patients with peroxisomal disorders

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Formation of a 2-methyl-branched fatty aldehyde during peroxisomal α-oxidation

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Production of formyl-CoA during peroxisomal alpha-oxidation of 3-methyl-branched fatty acids

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Formic acid is a product of the alpha-oxidation of fatty acids by human skin fibroblasts: deficiency of formic acid production in peroxisome-deficient fibroblasts

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

alpha-Oxidation of 3-methyl-substituted fatty acids in rat liver. Production of formic acid instead of CO2, cofactor requirements, subcellular localization and formation of a 2-hydroxy-3-methylacyl-CoA intermediate

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Stable isotope studies of phytanic acid alpha-oxidation: in vivo production of formic acid

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Human very-long-chain acyl-CoA synthetase: cloning, topography, and relevance to branched-chain fatty acid metabolism

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Very long-chain acyl-CoA synthetases. Human "bubblegum" represents a new family of proteins capable of activating very long-chain fatty acids

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Purification and properties of an alpha-methylacyl-CoA racemase from rat liver

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Purification and characterization of an alpha-methylacyl-CoA racemase from human liver

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Characteristics and subcellular localization of pristanoyl-CoA synthetase in rat liver

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Utilization of sterol carrier protein-2 by phytanoyl-CoA 2-hydroxylase in the peroxisomal alpha oxidation of phytanic acid

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Defective peroxisomal catabolism of branched fatty acyl coenzyme A in mice lacking the sterol carrier protein-2/sterol carrier protein-x gene function

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

FRET microscopy demonstrates molecular association of non-specific lipid transfer protein (nsL-TP) with fatty acid oxidation enzymes in peroxisomes

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Biosynthetic systems for nonribosomal peptide antibiotic assembly.

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Structural basis for the activation of phenylalanine in the non-ribosomal biosynthesis of gramicidin S

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Crystal structure of firefly luciferase throws light on a superfamily of adenylate-forming enzymes

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Characterization of the propionyl-CoA synthetase (PrpE) enzyme of Salmonella enterica: residue Lys592 is required for propionyl-AMP synthesis

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Affinity labeling fatty acyl-CoA synthetase with 9-p-azidophenoxy nonanoic acid and the identification of the fatty acid-binding site.

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Mutational analysis of 4-coumarate:CoA ligase identifies functionally important amino acids and verifies its close relationship to other adenylate-forming enzymes

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Structure-function analysis of phytanoyl-CoA 2-hydroxylase mutations causing Refsum's disease

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

The iron(II) and 2-oxoacid-dependent dioxygenases and their role in metabolism

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

C. elegans EGL-9 and mammalian homologs define a family of dioxygenases that regulate HIF by prolyl hydroxylation

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Hypoxia-inducible factor (HIF) asparagine hydroxylase is identical to factor inhibiting HIF (FIH) and is related to the cupin structural family

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Studies on the active site of deacetoxycephalosporin C synthase

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Kinetic and crystallographic studies on deacetoxycephalosporin C synthase (DAOCS)

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Structure of a cephalosporin synthase

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Structural origins of the selectivity of the trifunctional oxygenase clavaminic acid synthase

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Structure and mechanism of anthocyanidin synthase from Arabidopsis thaliana

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Structure of proline 3-hydroxylase. Evolution of the family of 2-oxoglutarate dependent oxygenases

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

X-ray crystal structure of Escherichia coli taurine/alpha-ketoglutarate dioxygenase complexed to ferrous iron and substrates

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

The 2-His-1-carboxylate facial triad--an emerging structural motif in mononuclear non-heme iron(II) enzymes

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Characterization of the iron- and 2-oxoglutarate-binding sites of human prolyl 4-hydroxylase

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Purification and initial characterization of proline 4-hydroxylase from Streptomyces griseoviridus P8648: a 2-oxoacid, ferrous-dependent dioxygenase involved in etamycin biosynthesis

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Role of the nonheme Fe(II) center in the biosynthesis of the plant hormone ethylene

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Crystal structure of a clavaminate synthase-Fe(II)-2-oxoglutarate-substrate-NO complex: evidence for metal centered rearrangements

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Spectroscopic studies of substrate interactions with clavaminate synthase 2, a multifunctional alpha-KG-dependent non-heme iron enzyme: correlation with mechanisms and reactivities

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

A stereochemical concept for the catalytic mechanism of prolylhydroxylase: applicability to classification and design of inhibitors.

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

A non-heme iron protein with heme tendencies: an investigation of the substrate specificity of thymine hydroxylase

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Molecular cloning, DNA sequence, and gene expression of the oxalyl-coenzyme A decarboxylase gene, oxc, from the bacterium Oxalobacter formigenes

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Interplay of organic and biological chemistry in understanding coenzyme mechanisms: example of thiamin diphosphate-dependent decarboxylations of 2-oxo acids

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Regulation of thiamin diphosphate-dependent 2-oxo acid decarboxylases by substrate and thiamin diphosphate.Mg(II) - evidence for tertiary and quaternary interactions.

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Structure and electron transfer mechanism of pyruvate:ferredoxin oxidoreductase.

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Properties and functions of the thiamin diphosphate dependent enzyme transketolase

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Structure-function relationships and flexible tetramer assembly in pyruvate decarboxylase revealed by analysis of crystal structures

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Sixty years of thiamin diphosphate biochemistry.

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

On the mechanism of action of thiamin enzymes in the presence of bivalent metal ions

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Purification and characterization of oxalyl-coenzyme A decarboxylase from Oxalobacter formigenes

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

2-Hydroxyphytanic acid oxidase activity in rat and human liver and its deficiency in the Zellweger syndrome

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Identification and characterization of HAOX1, HAOX2, and HAOX3, three human peroxisomal 2-hydroxy acid oxidases

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Fatty aldehyde dehydrogenase: genomic structure, expression and mutation analysis in Sjögren-Larsson syndrome

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Human liver fatty aldehyde dehydrogenase: microsomal localization, purification, and biochemical characterization

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

The first structure of an aldehyde dehydrogenase reveals novel interactions between NAD and the Rossmann fold

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Chemical mechanism and substrate binding sites of NADP-dependent aldehyde dehydrogenase from Streptococcus mutans.

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Differences in nucleotide specificity and catalytic mechanism between Vibrio harveyi aldehyde dehydrogenase and other members of the aldehyde dehydrogenase superfamily

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

A common deletion mutation in European patients with Sjögren-Larsson syndrome.

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Expression of alpha-Methylacyl-CoA racemase (P504S) in atypical adenomatous hyperplasia of the prostate

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Alpha-Methylacyl-CoA racemase: a novel tumor marker over-expressed in several human cancers and their precursor lesions

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Peroxisomal beta-oxidation of 2-methyl-branched acyl-CoA esters: stereospecific recognition of the 2S-methyl compounds by trihydroxycoprostanoyl-CoA oxidase and pristanoyl-CoA oxidase

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Substrate stereospecificity in oxidation of (25S)-3 alpha, 7 alpha, 12 alpha-trihydroxy-5 beta-cholestanoyl-CoA by peroxisomal trihydroxy-5 beta-cholestanoyl-CoA oxidase

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Role of hepatic fatty acid:coenzyme A ligases in the metabolism of xenobiotic carboxylic acids

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Molecular cloning and expression of a 2-arylpropionyl-coenzyme A epimerase: a key enzyme in the inversion metabolism of ibuprofen

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Metabolic stereoisomeric inversion of ibuprofen in mammals

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

Mutation analysis of PEX7 in 60 probands with rhizomelic chondrodysplasia punctata and functional correlations of genotype with phenotype

1 reference

https://api.crossref.org/works/10.1016%2FS0163-7827%2803%2900016-X

7 January 2021

10.1016/S0163-7827(03)00016-X

Identifiers

DOI

1 reference

6 August 2017

1 reference

PubMed ID

12814641