(Q35202377)

7 August 2017

title

Role of the 26-hydroxylase in the biosynthesis of bile acids in the normal state and in cerebrotendinous xanthomatosis. An in vivo study (English)

1 reference

7 August 2017

1

Björkhem I

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7 August 2017

Fausa O

2

1 reference

7 August 2017

Hopen G

3

1 reference

7 August 2017

Oftebro H

4

1 reference

7 August 2017

Pedersen JI

5

1 reference

7 August 2017

Skrede S

6

1 reference

7 August 2017

language of work or name

English

0 references

publication date

1 January 1983

1 reference

Journal of Clinical Investigation

7 August 2017

published in

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7 August 2017

volume

71

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7 August 2017

issue

1

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7 August 2017

page(s)

142-148

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An in vivo evaluation of the quantitative significance of several potential pathways to cholic and chenodeoxycholic acids from cholesterol in man.

7 August 2017

cites work

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=436846

The formation and metabolism of 3α,7α-dihydroxy-5β-cholestan-26-oic acid in man

28 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=436846

A biochemical abnormality in cerebrotendinous xanthomatosis. Impairment of bile acid biosynthesis associated with incomplete degradation of the cholesterol side chain

28 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=436846

Bile acid formation in man: metabolism of 7 -hydroxy-4-cholesten-3-one in bile fistula patients

28 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=436846

Bile alcohol metabolism in man. Conversion of 5beta-cholestane-3alpha, 7alpha,12alpha, 25-tetrol to cholic acid

28 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=436846

Biosynthesis of bile acids in man. Hydroxylation of the C27-steroid side chain

28 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=436846

28 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=436846

Cholic acid biosynthesis: the enzymatic defect in cerebrotendinous xanthomatosis

28 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=436846

Metabolism of potential precursors of chenodeoxycholic acid in cerebrotendinous xanthomatosis (CTX)

28 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=436846

A 25-hydroxylation pathway of cholic acid biosynthesis in man and rat

28 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=436846

Cerebrotendinous xanthomatosis: a defect in mitochondrial 26-hydroxylation required for normal biosynthesis of cholic acid

28 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=436846

Assay of intermediates in bile acid biosynthesis using isotope dilution--mass spectrometry: hepatic levels in the normal state and in cerebrotendinous xanthomatosis

26 September 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=436846

Quantitative analysis of fecal bile acids by gas-liquid chromatography

26 September 2018

1 reference

12 December 2020

Side chain hydroxylation of C27-steroids and vitamin D3 by a cytochrome P-450 enzyme system isolated from human liver mitochondria

1 reference

12 December 2020

Stereochemistry of the Enzymatic Conversion of a Delta4-3-Oxosteroid into a 3-Oxo-5beta-Steroid. Bile Acids and Steroids 208

1 reference

12 December 2020

On the mechanism of the enzymatic conversn of cholest-5-ene-3-beta, 7-alpha-diol into 7-alpha-hydroxycholest-4-en-3-one

1 reference

12 December 2020

Reductive titrations of iron-sulfur proteins containing two to four iron atoms

1 reference

12 December 2020

Omega-hydroxylation of steriod side-chain in biosynthesis of bile acids

1 reference

12 December 2020

Enzymatic characteristics of CO-sensitive 26-hydroxylase system for 5beta-cholestane-3 alpha, 7 alpha, 12 alpha-triol in rat-liver mitochondria and its intramitochondrial localization

1 reference

12 December 2020

Purification of NADPH-ferredoxin reductase from rat liver mitochondria

1 reference

12 December 2020

Biosynthesis of bile acids in man. Multiple pathways to cholic acid and chenodeoxycholic acid

1 reference

12 December 2020

Cerebrotendinous xanthomatosis: defective liver mitochondrial hydroxylation of chenodeoxycholic acid precursors

1 reference

12 December 2020

On the Conversion of Cholesterol to 5beta-Cholestane-3alpha, 7alpha-Diol in Guinea Pig Liver Homogenates

1 reference

12 December 2020

Identifiers

DOI

10.1172/JCI110742

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7 August 2017

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7 August 2017

1 reference