(Q35490408)

8 August 2017

title

Evaluation of orally administered PEGylated phenylalanine ammonia lyase in mice for the treatment of Phenylketonuria (English)

1 reference

8 August 2017

1 reference

4

Charles R Scriver

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author name string

Christineh N Sarkissian

1

1 reference

8 August 2017

Tse Siang Kang

2

1 reference

8 August 2017

Alejandra Gámez

3

1 reference

8 August 2017

Raymond C Stevens

5

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8 August 2017

publication date

29 June 2011

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Molecular Genetics and Metabolism

8 August 2017

published in

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8 August 2017

volume

104

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8 August 2017

issue

3

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8 August 2017

page(s)

249-254

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Converting an injectable protein therapeutic into an oral form: phenylalanine ammonia lyase for phenylketonuria

8 August 2017

cites work

1 reference

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12 July 2018

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Structural and Biochemical Characterization of the Therapeutic Anabaena variabilis Phenylalanine Ammonia Lyase

12 July 2018

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The response of patients with phenylketonuria and elevated serum phenylalanine to treatment with oral sapropterin dihydrochloride (6R-tetrahydrobiopterin): a phase II, multicentre, open-label, screening study

12 July 2018

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12 July 2018

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Correction of kinetic and stability defects by tetrahydrobiopterin in phenylketonuria patients with certain phenylalanine hydroxylase mutations

12 July 2018

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Toward PKU enzyme replacement therapy: PEGylation with activity retention for three forms of recombinant phenylalanine hydroxylase

12 July 2018

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A SIMPLE PHENYLALANINE METHOD FOR DETECTING PHENYLKETONURIA IN LARGE POPULATIONS OF NEWBORN INFANTS

12 July 2018

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12 July 2018

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12 July 2018

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12 July 2018

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12 July 2018

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12 July 2018

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The metabolism of cinnamic acid by healthy and phenylketonuric adults: a kinetic study

12 July 2018

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12 July 2018

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Autonomous functional domains of chemically synthesized human immunodeficiency virus tat trans-activator protein

12 July 2018

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Phenylalanine ammonia-lyase. Induction and purification from yeast and clearance in mammals

12 July 2018

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Phenylalanine Depletion for the Management of Phenylketonuria: Use of Enzyme Reactors with Immobilized Enzymes

12 July 2018

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Efficacy of sapropterin dihydrochloride (tetrahydrobiopterin, 6R-BH4) for reduction of phenylalanine concentration in patients with phenylketonuria: a phase III randomised placebo-controlled study.

12 July 2018

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Structure-based epitope and PEGylation sites mapping of phenylalanine ammonia-lyase for enzyme substitution treatment of phenylketonuria.

26 September 2018

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26 September 2018

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Structure-based chemical modification strategy for enzyme replacement treatment of phenylketonuria

26 September 2018

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Development of pegylated forms of recombinant Rhodosporidium toruloides phenylalanine ammonia-lyase for the treatment of classical phenylketonuria

26 September 2018

1 reference

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The influence of phenylalanine intake on the chemistry and behaviour of a phenyl-ketonuric child.

26 September 2018

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Formation of alginate microspheres produced using emulsification technique

26 September 2018

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Tetrahydrobiopterin as an alternative treatment for mild phenylketonuria

26 September 2018

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How practical are recommendations for dietary control in phenylketonuria?

26 September 2018

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Phenylalanine ammonia lyase in the management of phenylketonuria: the relationship between ingested cinnamate and urinary hippurate in humans.

26 September 2018

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Oral Bioavailability of Insulin Contained in Polysaccharide Nanoparticles

26 September 2018

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Recommendations for protein and amino acid intake in phenylketonuric patients

15 November 2018

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Comments on diet and compliance in phenylketonuria

7 January 2021

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https://api.crossref.org/works/10.1016%2FJ.YMGME.2011.06.016

Artificial cell-microencapsulated phenylalanine ammonia-lyase

7 January 2021

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https://api.crossref.org/works/10.1016%2FJ.YMGME.2011.06.016

Effect of Ca2+, Ba2+, and Sr2+ on alginate microbeads

7 January 2021

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Characterization of mutations at the mouse phenylalanine hydroxylase locus

7 January 2021

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A new theory of enterorecirculation of amino acids and its use for depleting unwanted amino acids using oral enzyme-artificial cells, as in removing phenylalanine in phenylketonuria

7 January 2021

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https://api.crossref.org/works/10.1016%2FJ.YMGME.2011.06.016

10.1016/J.YMGME.2011.06.016

7 January 2021

Identifiers

DOI

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8 August 2017

1 reference

8 August 2017

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