(Q36308010)

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:23055718%20AND%20SRC:MED&resulttype=core&format=json

10 March 2020

title

The effects of weekly augmentation therapy in patients with PiZZ α1-antitrypsin deficiency (English)

1 reference

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10 March 2020

1

1 reference

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10 March 2020

Elena Miranda

8

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:23055718%20AND%20SRC:MED&resulttype=core&format=json

10 March 2020

author name string

J Koepke

2

1 reference

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10 March 2020

M Dresel

3

1 reference

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10 March 2020

A Hattesohl

4

1 reference

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10 March 2020

E Frenzel

5

1 reference

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10 March 2020

J Perez

6

1 reference

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10 March 2020

D A Lomas

7

1 reference

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10 March 2020

T Greulich

9

1 reference

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10 March 2020

S Noeske

10

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10 March 2020

M Wencker

11

1 reference

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10 March 2020

H Teschler

12

1 reference

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10 March 2020

C Vogelmeier

13

1 reference

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10 March 2020

S Janciauskiene

14

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10 March 2020

A R Koczulla

15

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10 March 2020

language of work or name

English

0 references

publication date

28 September 2012

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:23055718%20AND%20SRC:MED&resulttype=core&format=json

International Journal of Chronic Obstructive Pulmonary Disease

10 March 2020

published in

1 reference

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10 March 2020

volume

7

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10 March 2020

page(s)

687-696

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Creative Commons Attribution-NonCommercial 3.0 Unported

10 March 2020

copyright license

start time

1 September 2012

1 reference

April 2022 Public Data File from Crossref

copyright status

copyrighted

0 references

cites work

Why has it been so difficult to prove the efficacy of alpha-1-antitrypsin replacement therapy? Insights from the study of disease pathogenesis

1 reference

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The discovery of α1-antitrypsin and its role in health and disease

30 September 2017

1 reference

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The role of augmentation therapy in alpha-1 antitrypsin deficiency

30 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3468059

α-1 Antitrypsin regulates human neutrophil chemotaxis induced by soluble immune complexes and IL-8

30 September 2017

1 reference

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A novel monoclonal antibody to characterize pathogenic polymers in liver disease associated with alpha1-antitrypsin deficiency.

30 September 2017

1 reference

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Clinical practice. Alpha1-antitrypsin deficiency

30 September 2017

1 reference

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Alpha-1-antitrypsin is an endogenous inhibitor of proinflammatory cytokine production in whole blood

30 September 2017

1 reference

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Recruitment of the inflammatory subset of monocytes to sites of ischemia induces angiogenesis in a monocyte chemoattractant protein-1-dependent fashion

30 September 2017

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30 September 2017

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Exhaled breath condensate: methodological recommendations and unresolved questions.

30 September 2017

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Prolastin, a pharmaceutical preparation of purified human alpha1-antitrypsin, blocks endotoxin-mediated cytokine release

30 September 2017

1 reference

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Polymers of Z alpha1-antitrypsin co-localize with neutrophils in emphysematous alveoli and are chemotactic in vivo

30 September 2017

1 reference

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Differential detection of PAS-positive inclusions formed by the Z, Siiyama, and Mmalton variants of alpha1-antitrypsin.

30 September 2017

1 reference

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Inhibition of VEGF receptors causes lung cell apoptosis and emphysema

30 September 2017

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Augmentation therapy reduces frequency of lung infections in antitrypsin deficiency: a new hypothesis with supporting data

30 September 2017

1 reference

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A randomized clinical trial of alpha(1)-antitrypsin augmentation therapy

30 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3468059

Clinical features and prognosis of life time non-smokers with severe alpha 1-antitrypsin deficiency

30 September 2017

1 reference

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Impaired monocyte migration and reduced type 1 (Th1) cytokine responses in C-C chemokine receptor 2 knockout mice

30 September 2017

1 reference

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Replacement therapy of alpha 1-antitrypsin deficiency. Reversal of protease-antiprotease imbalance within the alveolar structures of PiZ subjects

30 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3468059

Interleukin-8, a chemotactic and inflammatory cytokine

30 September 2017

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Polymers of alpha(1)-antitrypsin are chemotactic for human neutrophils: a new paradigm for the pathogenesis of emphysema

30 September 2017

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Does alpha1-antitrypsin augmentation therapy slow the annual decline in FEV1 in patients with severe hereditary alpha1-antitrypsin deficiency? Wissenschaftliche Arbeitsgemeinschaft zur Therapie von Lungenerkrankungen (WATL) alpha1-AT study group.

29 June 2018

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29 June 2018

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29 June 2018

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Exploring the role of CT densitometry: a randomised study of augmentation therapy in alpha1-antitrypsin deficiency.

22 September 2018

1 reference

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MCP-1 induces cardioprotection against ischaemia/reperfusion injury: role of reactive oxygen species

22 September 2018

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22 September 2018

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Inhibition of lipopolysaccharide-mediated human monocyte activation, in vitro, by alpha1-antitrypsin

22 September 2018

1 reference

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Divergent effects of alpha1-antitrypsin on neutrophil activation, in vitro

22 September 2018

1 reference

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22 September 2018

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Compartmentalized IL-8 and elastase release within the human lung in unilateral pneumonia

22 September 2018

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12 December 2020

The effect of augmentation therapy on bronchial inflammation in alpha1-antitrypsin deficiency

1 reference

12 December 2020

Biochemical efficacy and safety of monthly augmentation therapy for alpha 1-antitrypsin deficiency

1 reference

12 December 2020

Longitudinal follow-up of patients with alpha(1)-protease inhibitor deficiency before and during therapy with IV alpha(1)-protease inhibitor

1 reference

12 December 2020

Lung neutrophil burden correlates with increased pro-inflammatory cytokines and decreased lung function in individuals with alpha(1)-antitrypsin deficiency

1 reference

12 December 2020

Ambient temperature impacts on pH of exhaled breath condensate

1 reference

12 December 2020

Multiplex analysis of cytokines in exhaled breath condensate

1 reference

12 December 2020

Identifiers

DOI

10.2147/COPD.S34560

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:23055718%20AND%20SRC:MED&resulttype=core&format=json

10 March 2020

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:23055718%20AND%20SRC:MED&resulttype=core&format=json

10 March 2020

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:23055718%20AND%20SRC:MED&resulttype=core&format=json