(Q36589169)

15 August 2017

1 reference

title

Polyglutamine disease: recent advances in the neuropathology of dentatorubral-pallidoluysian atrophy (English)

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15 August 2017

Mitsunori Yamada

1

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15 August 2017

Mitsuteru Shimohata

2

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15 August 2017

Toshiya Sato

3

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15 August 2017

Shoji Tsuji

4

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15 August 2017

Hitoshi Takahashi

5

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15 August 2017

publication date

1 August 2006

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15 August 2017

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15 August 2017

volume

26

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15 August 2017

issue

4

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15 August 2017

page(s)

346-351

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When more is less: pathogenesis of glutamine repeat neurodegenerative diseases

15 August 2017

cites work

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Formation of neuronal intranuclear inclusions underlies the neurological dysfunction in mice transgenic for the HD mutation

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Aggregation of huntingtin in neuronal intranuclear inclusions and dystrophic neurites in brain

21 January 2018

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Ataxin-1 with an expanded glutamine tract alters nuclear matrix-associated structures

21 January 2018

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21 January 2018

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21 January 2018

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Hereditary dentatorubral-pallidoluysian atrophy: detection of widespread ubiquitinated neuronal and glial intranuclear inclusions in the brain

21 January 2018

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Suppression of aggregate formation and apoptosis by transglutaminase inhibitors in cells expressing truncated DRPLA protein with an expanded polyglutamine stretch.

21 January 2018

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Neuronal intranuclear inclusions in spinocerebellar ataxia type 2: triple-labeling immunofluorescent study

21 January 2018

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Exon 1 of the HD gene with an expanded CAG repeat is sufficient to cause a progressive neurological phenotype in transgenic mice

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Expanded polyglutamine protein forms nuclear inclusions and causes neural degeneration in Drosophila

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Polyglutamine pathogenesis.

21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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Familial myoclonus epilepsy and choreoathetosis: hereditary dentatorubral-pallidoluysian atrophy

21 January 2018

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Widespread occurrence of intranuclear atrophin-1 accumulation in the central nervous system neurons of patients with dentatorubral-pallidoluysian atrophy

21 January 2018

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Atrophy of the cerebellum and brainstem in dentatorubral pallidoluysian atrophy. Influence of CAG repeat size on MRI findings

21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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Altered neurotransmitter receptor expression in transgenic mouse models of Huntington's disease

21 January 2018

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Expanded polyglutamine stretches interact with TAFII130, interfering with CREB-dependent transcription

21 January 2018

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Insoluble detergent-resistant aggregates form between pathological and nonpathological lengths of polyglutamine in mammalian cells

21 January 2018

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Interaction of Huntington disease protein with transcriptional activator Sp1

21 January 2018

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Huntingtin inclusions do not deplete polyglutamine-containing transcription factors in HD mice

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1440-1789.2006.00670.X

10.1111/J.1440-1789.2006.00670.X

21 January 2018

Identifiers

DOI

1 reference

15 August 2017

1 reference