(Q36966865)

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:23722904%20AND%20SRC:MED&resulttype=core&format=json

2 March 2020

title

Dominant protein interactions that influence the pathogenesis of conformational diseases (English)

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:23722904%20AND%20SRC:MED&resulttype=core&format=json

2 March 2020

5

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:23722904%20AND%20SRC:MED&resulttype=core&format=json

2 March 2020

author name string

Jordan Wright

1

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:23722904%20AND%20SRC:MED&resulttype=core&format=json

2 March 2020

Xiaofan Wang

2

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:23722904%20AND%20SRC:MED&resulttype=core&format=json

2 March 2020

Leena Haataja

3

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:23722904%20AND%20SRC:MED&resulttype=core&format=json

2 March 2020

Aaron P Kellogg

4

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:23722904%20AND%20SRC:MED&resulttype=core&format=json

2 March 2020

Ming Liu

6

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:23722904%20AND%20SRC:MED&resulttype=core&format=json

2 March 2020

Peter Arvan

7

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:23722904%20AND%20SRC:MED&resulttype=core&format=json

2 March 2020

language of work or name

English

0 references

publication date

3 June 2013

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:23722904%20AND%20SRC:MED&resulttype=core&format=json

2 March 2020

number of pages

11

1 reference

Journal of Clinical Investigation

inferred from page(s)

published in

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:23722904%20AND%20SRC:MED&resulttype=core&format=json

2 March 2020

volume

123

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:23722904%20AND%20SRC:MED&resulttype=core&format=json

2 March 2020

issue

7

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:23722904%20AND%20SRC:MED&resulttype=core&format=json

2 March 2020

page(s)

3124-3134

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:23722904%20AND%20SRC:MED&resulttype=core&format=json

describes a project that uses

2 March 2020

ImageQuant

1 reference

11 June 2022

https://www.ebi.ac.uk/europepmc/webservices/rest/PMC3696544/fullTextXML

inferred from PubMed Central ID database lookup

ImageJ

1 reference

11 June 2022

https://www.ebi.ac.uk/europepmc/webservices/rest/PMC3696544/fullTextXML

inferred from PubMed Central ID database lookup

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29 September 2017

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29 September 2017

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29 September 2017

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A model of threshold behavior reveals rescue mechanisms of bystander proteins in conformational diseases

29 September 2017

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Mutant INS-gene induced diabetes of youth: proinsulin cysteine residues impose dominant-negative inhibition on wild-type proinsulin transport

29 September 2017

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29 September 2017

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PERK (EIF2AK3) regulates proinsulin trafficking and quality control in the secretory pathway

29 September 2017

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Cis and trans actions of the cholinesterase-like domain within the thyroglobulin dimer

29 September 2017

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Genetics and phenomics of hypothyroidism and goiter due to thyroglobulin mutations

29 September 2017

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In vitro processing and secretion of mutant insulin proteins that cause permanent neonatal diabetes

29 September 2017

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Misfolded proinsulin affects bystander proinsulin in neonatal diabetes

29 September 2017

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Drug development and the cellular quality control system

29 September 2017

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Pharmacological manipulation of gain-of-function and dominant-negative mechanisms in rhodopsin retinitis pigmentosa.

29 September 2017

1 reference

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The cholinesterase-like domain of thyroglobulin functions as an intramolecular chaperone.

29 September 2017

1 reference

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The unfolded protein response: a pathway that links insulin demand with beta-cell failure and diabetes

29 September 2017

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Adapting proteostasis for disease intervention

29 September 2017

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Endoplasmic reticulum stress contributes to beta cell apoptosis in type 2 diabetes

29 September 2017

1 reference

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Oxidoreductase interactions include a role for ERp72 engagement with mutant thyroglobulin from the rdw/rdw rat dwarf

29 September 2017

1 reference

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A mutation linked with autism reveals a common mechanism of endoplasmic reticulum retention for the alpha,beta-hydrolase fold protein family

29 September 2017

1 reference

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Dominant and recessive distal renal tubular acidosis mutations of kidney anion exchanger 1 induce distinct trafficking defects in MDCK cells

29 September 2017

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Proinsulin disulfide maturation and misfolding in the endoplasmic reticulum

29 September 2017

1 reference

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29 September 2017

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Cytoprotection by pre-emptive conditional phosphorylation of translation initiation factor 2

29 September 2017

1 reference

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29 September 2017

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A mutation in the human norepinephrine transporter gene (SLC6A2) associated with orthostatic intolerance disrupts surface expression of mutant and wild-type transporters

29 September 2017

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Traffic jam: a compendium of human diseases that affect intracellular transport processes

29 September 2017

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A single amino acid change in the acetylcholinesterase-like domain of thyroglobulin causes congenital goiter with hypothyroidism in the cog/cog mouse: a model of human endoplasmic reticulum storage diseases

29 September 2017

1 reference

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The role of assembly in insulin's biosynthesis

29 September 2017

1 reference

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Assembly of immunoglobulin light chains as a prerequisite for secretion. A model for oligomerization-dependent subunit folding

29 September 2017

1 reference

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Direct identification of prohormone conversion site in insulin-secreting cells

29 September 2017

1 reference

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Glucose stimulates proinsulin biosynthesis by a dose-dependent recruitment of pancreatic beta cells

29 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3696544

Protein oligomerization in the endoplasmic reticulum

29 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3696544

Tissue-specific expression and methylation of a thyroglobulin-chloramphenicol acetyltransferase fusion gene in transgenic mice

29 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3696544

Differences in glucose recognition by individual rat pancreatic B cells are associated with intercellular differences in glucose-induced biosynthetic activity

29 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3696544

Transient aggregation of nascent thyroglobulin in the endoplasmic reticulum: relationship to the molecular chaperone, BiP

29 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3696544

Misfolding and aggregation of newly synthesized proteins in the endoplasmic reticulum

29 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3696544

Endocrinopathies in the family of endoplasmic reticulum (ER) storage diseases: disorders of protein trafficking and the role of ER molecular chaperones

29 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3696544

Interrelations between assembly and secretion of recombinant human acetylcholinesterase

27 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3696544

Posttranslational association of immunoglobulin heavy chain binding protein with nascent heavy chains in nonsecreting and secreting hybridomas

27 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3696544

Oligomerization and protein transport

27 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3696544

A mutation in the ectodomain of herpes simplex virus 1 glycoprotein B causes defective processing and retention in the endoplasmic reticulum

27 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3696544

Calcium is required for folding of newly made subunits of the asialoglycoprotein receptor within the endoplasmic reticulum.

27 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3696544

Low-molecular-weight iodoproteins in the congenital goiters of cog/cog mice

27 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3696544

The cholinesterase-like domain, essential in thyroglobulin trafficking for thyroid hormone synthesis, is required for protein dimerization

27 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3696544

A novel missense mutation (G2320R) in thyroglobulin causes hypothyroidism in rdw rats

4 September 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3696544

Dynamics and retention of misfolded proteins in native ER membranes

4 September 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3696544

Evaluation and characterization of congenital hypothyroidism in rdw dwarf rats

4 December 2018

1 reference

12 December 2020

Folding and assembly of newly synthesized thyroglobulin occurs in a pre-Golgi compartment

1 reference

12 December 2020

Lacidipine remodels protein folding and Ca 2+ homeostasis in Gaucher's disease fibroblasts: a mechanism to rescue mutant glucocerebrosidase

1 reference

12 December 2020

The dominant negative LQT2 mutation A561V reduces wild-type HERG expression

1 reference

12 December 2020

A missense mutation G2320R in the thyroglobulin gene causes non-goitrous congenital primary hypothyroidism in the WIC-rdw rat

1 reference

12 December 2020

Assembly, sorting, and exit of oligomeric proteins from the endoplasmic reticulum

1 reference

12 December 2020

Identifiers

DOI

10.1172/JCI67260

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:23722904%20AND%20SRC:MED&resulttype=core&format=json

2 March 2020

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:23722904%20AND%20SRC:MED&resulttype=core&format=json

2 March 2020

PubMed publication ID

23722904

1 reference