(Q37462429)

20 August 2017

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title

The human G93A-superoxide dismutase-1 mutation, mitochondrial glutathione and apoptotic cell death (English)

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20 August 2017

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H Muyderman

1

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20 August 2017

P G Hutson

2

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20 August 2017

D Matusica

3

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20 August 2017

M-L Rogers

4

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20 August 2017

R A Rush

5

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20 August 2017

language of work or name

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28 April 2009

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20 August 2017

published in

Neurochemical Research

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20 August 2017

volume

34

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20 August 2017

issue

10

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20 August 2017

page(s)

1847-1856

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Transgenic mouse models of amyotrophic lateral sclerosis

20 August 2017

cites work

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https://api.crossref.org/works/10.1007%2FS11064-009-9974-Z

Neuroblastoma x spinal cord (NSC) hybrid cell lines resemble developing motor neurons

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS11064-009-9974-Z

Oxidative stress in ALS: a mechanism of neurodegeneration and a therapeutic target

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS11064-009-9974-Z

Mitochondrial changes associated with glutathione deficiency

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS11064-009-9974-Z

Clinical limits of amyotrophic lateral sclerosis

21 January 2018

1 reference

12 December 2020

Induction of nitric oxide-dependent apoptosis in motor neurons by zinc-deficient superoxide dismutase

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12 December 2020

Aggregation and Motor Neuron Toxicity of an ALS-Linked SOD1 Mutant Independent from Wild-Type SOD1

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12 December 2020

Metabolism and functions of glutathione in brain.

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12 December 2020

Current status of SOD1 mutations in familial amyotrophic lateral sclerosis

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12 December 2020

The ubiquitin-proteasome pathway and pathogenesis of human diseases

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12 December 2020

Mitochondrial alterations in the spinal cord of patients with sporadic amyotrophic lateral sclerosis

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12 December 2020

Clinical epidemiology of amyotrophic lateral sclerosis

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12 December 2020

Gene therapy for central nervous system repair.

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12 December 2020

Intrathecal cyclosporin prolongs survival of late-stage ALS mice

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12 December 2020

Expression of mutant SOD1 in astrocytes induces functional deficits in motoneuron mitochondria

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12 December 2020

Molecular and cellular pathways of neurodegeneration in motor neurone disease

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12 December 2020

Astrocytes expressing ALS-linked mutated SOD1 release factors selectively toxic to motor neurons

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12 December 2020

Mitochondrial Glutathione: Importance and Transport

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12 December 2020

Toxicity of familial ALS-linked SOD1 mutants from selective recruitment to spinal mitochondria.

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12 December 2020

Molecular biology of amyotrophic lateral sclerosis: insights from genetics

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12 December 2020

Effect of chronic ethanol feeding on glutathione and functional integrity of mitochondria in periportal and perivenous rat hepatocytes

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12 December 2020

Mitochondrial dysfunction in a cell culture model of familial amyotrophic lateral sclerosis

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12 December 2020

Ultrastructural changes of mitochondria in the skeletal muscle of patients with amyotrophic lateral sclerosis

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12 December 2020

Oxidative stress in neurodegeneration and available means of protection.

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12 December 2020

Decreased zinc affinity of amyotrophic lateral sclerosis-associated superoxide dismutase mutants leads to enhanced catalysis of tyrosine nitration by peroxynitrite

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12 December 2020

Amyotrophic lateral sclerosis--are microglia killing motor neurons?

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12 December 2020

Mutations associated with amyotrophic lateral sclerosis convert superoxide dismutase from an antiapoptotic gene to a proapoptotic gene: studies in yeast and neural cells

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12 December 2020

Mitochondrial localization of mutant superoxide dismutase 1 triggers caspase-dependent cell death in a cellular model of familial amyotrophic lateral sclerosis

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12 December 2020

Origin and turnover of mitochondrial glutathione

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12 December 2020

Age-dependent penetrance of disease in a transgenic mouse model of familial amyotrophic lateral sclerosis

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12 December 2020

Highly selective and prolonged depletion of mitochondrial glutathione in astrocytes markedly increases sensitivity to peroxynitrite.

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12 December 2020

Glutaredoxin: role in reversible protein s-glutathionylation and regulation of redox signal transduction and protein translocation

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12 December 2020

Mutations in Cu/Zn superoxide dismutase gene are associated with familial amyotrophic lateral sclerosis

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12 December 2020

Mutated human SOD1 causes dysfunction of oxidative phosphorylation in mitochondria of transgenic mice.

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12 December 2020

ALS: a disease of motor neurons and their nonneuronal neighbors

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12 December 2020

Development and characterisation of a glutamate-sensitive motor neurone cell line

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12 December 2020

Motoneuron differentiation of immortalized human spinal cord cell lines

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12 December 2020

Histological evidence of redox system breakdown caused by superoxide dismutase 1 (SOD1) aggregation is common to SOD1-mutated motor neurons in humans and animal models

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12 December 2020

ALS-linked mutant SOD1 induces ER stress- and ASK1-dependent motor neuron death by targeting Derlin-1.

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12 December 2020

From Charcot to Lou Gehrig: deciphering selective motor neuron death in ALS

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12 December 2020

Superoxide dismutase activity, oxidative damage, and mitochondrial energy metabolism in familial and sporadic amyotrophic lateral sclerosis

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12 December 2020

Apoptosis in amyotrophic lateral sclerosis--what is the evidence?

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12 December 2020

SOD1 mutations disrupt redox-sensitive Rac regulation of NADPH oxidase in a familial ALS model

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12 December 2020

Embryonic mouse spinal cord motor neuron hybrid cells

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12 December 2020

Mitochondrial glutathione: a modulator of brain cell death

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12 December 2020

Complex I and energy thresholds in the brain

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12 December 2020

Antisense peptide nucleic acid targeting GluR3 delays disease onset and progression in the SOD1 G93A mouse model of familial ALS.

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12 December 2020

Toxicity of ALS-linked SOD1 mutants

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12 December 2020

Massive mitochondrial degeneration in motor neurons triggers the onset of amyotrophic lateral sclerosis in mice expressing a mutant SOD1

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12 December 2020

Isolation and culture of motor neurons from the newborn mouse spinal cord

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12 December 2020

Astrocytes as determinants of disease progression in inherited amyotrophic lateral sclerosis

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12 December 2020

Cytochrome c association with the inner mitochondrial membrane is impaired in the CNS of G93A-SOD1 mice.

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12 December 2020

Neuron-specific expression of mutant superoxide dismutase is sufficient to induce amyotrophic lateral sclerosis in transgenic mice

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12 December 2020

Mitochondrial dysfunction in SOD1G93A-bearing astrocytes promotes motor neuron degeneration: prevention by mitochondrial-targeted antioxidants

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12 December 2020

Retrograde axonal transport and motor neuron disease

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12 December 2020

Purification of embryonic rat motoneurons by panning on a monoclonal antibody to the low-affinity NGF receptor

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12 December 2020

Gene therapy for central nervous system injury: the use of cationic liposomes: an invited review

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12 December 2020

Transcriptional profile of primary astrocytes expressing ALS-linked mutant SOD1.

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12 December 2020

GM2 ganglioside regulates the function of ciliary neurotrophic factor receptor in murine immortalized motor neuron-like cells (NSC-34).

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12 December 2020

Effect of p75 neurotrophin receptor antagonist on disease progression in transgenic amyotrophic lateral sclerosis mice

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12 December 2020

Early vacuolization and mitochondrial damage in motor neurons of FALS mice are not associated with apoptosis or with changes in cytochrome oxidase histochemical reactivity.

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12 December 2020

S-glutathionylation: from redox regulation of protein functions to human diseases.

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12 December 2020

A gain-of-function of an amyotrophic lateral sclerosis-associated Cu,Zn-superoxide dismutase mutant: An enhancement of free radical formation due to a decrease in Km for hydrogen peroxide

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12 December 2020

Mitochondrial glutathione protects against cell death induced by oxidative and nitrative stress in astrocytes

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12 December 2020

Fine structural observations of neurofilamentous changes in amyotrophic lateral sclerosis

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12 December 2020

Mitochondrial DNA and respiratory chain function in spinal cords of ALS patients

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12 December 2020

Bcl-2: prolonging life in a transgenic mouse model of familial amyotrophic lateral sclerosis

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12 December 2020

Depletion in vitro of mitochondrial glutathione in rat hepatocytes and enhancement of lipid peroxidation by adriamycin and 1,3-bis(2-chloroethyl)-1-nitrosourea (BCNU)

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12 December 2020

Mitochondrial respiratory chain function in skeletal muscle of ALS patients.

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12 December 2020

Dissociation between neurodegeneration and caspase-11-mediated activation of caspase-1 and caspase-3 in a mouse model of amyotrophic lateral sclerosis

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12 December 2020

Structure, function and evolution of glutathione transferases: implications for classification of non-mammalian members of an ancient enzyme superfamily

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12 December 2020

ALS-associated mutant SOD1G93A causes mitochondrial vacuolation by expansion of the intermembrane space and by involvement of SOD1 aggregation and peroxisomes

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12 December 2020

Neuron-specific expression of mutant superoxide dismutase 1 in transgenic mice does not lead to motor impairment.

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12 December 2020

Analysis of the cytosolic proteome in a cell culture model of familial amyotrophic lateral sclerosis reveals alterations to the proteasome, antioxidant defenses, and nitric oxide synthetic pathways

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12 December 2020

Delaying caspase activation by Bcl-2: A clue to disease retardation in a transgenic mouse model of amyotrophic lateral sclerosis

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12 December 2020

Ultrastructural study of mitochondria in the spinal cord of transgenic mice with a G93A mutant SOD1 gene

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12 December 2020

Superoxide dismutase and the death of motoneurons in ALS.

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12 December 2020

Metabolic dysfunction in familial, but not sporadic, amyotrophic lateral sclerosis

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12 December 2020

Plasma membrane glutathione transporters and their roles in cell physiology and pathophysiology

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12 December 2020

Aggregation of mutant Cu/Zn superoxide dismutase proteins in a culture model of ALS

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12 December 2020

Unraveling the mechanisms involved in motor neuron degeneration in ALS

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12 December 2020

Amyotrophic lateral sclerosis-associated SOD1 mutant proteins bind and aggregate with Bcl-2 in spinal cord mitochondria

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12 December 2020

Rats expressing human cytosolic copper-zinc superoxide dismutase transgenes with amyotrophic lateral sclerosis: associated mutations develop motor neuron disease

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12 December 2020

How do ALS-associated mutations in superoxide dismutase 1 promote aggregation of the protein?

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12 December 2020

Mitochondrial dysfunction and death in motor neurons exposed to the glutathione-depleting agent ethacrynic acid

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12 December 2020

Incidence of amyotrophic lateral sclerosis in three counties in western Washington state

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12 December 2020

48 Assay of glutathione, glutathione disulfide, and glutathione mixed disulfides in biological samples

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12 December 2020

Activated microglia (BV-2) facilitation of TNF-alpha-mediated motor neuron death in vitro.

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12 December 2020

Mitochondrial fragmentation in neurodegeneration

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12 December 2020

ALS: life and death in a bad neighborhood

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12 December 2020

Cytotoxicity of immunoglobulins from amyotrophic lateral sclerosis patients on a hybrid motoneuron cell line

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12 December 2020

Characterization and use of the NSC-34 cell line for study of neurotrophin receptor trafficking.

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12 December 2020

Motor neuron degeneration in mice that express a human Cu,Zn superoxide dismutase mutation

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12 December 2020

Formation of high molecular weight complexes of mutant Cu, Zn-superoxide dismutase in a mouse model for familial amyotrophic lateral sclerosis.

1 reference

12 December 2020

Motor neuron disease: The curious ways of ALS

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12 December 2020

Expression of a Cu,Zn superoxide dismutase typical of familial amyotrophic lateral sclerosis induces mitochondrial alteration and increase of cytosolic Ca2+ concentration in transfected neuroblastoma SH-SY5Y cells

1 reference

12 December 2020

Establishment of a cell model of ALS disease: Golgi apparatus disruption occurs independently from apoptosis

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12 December 2020

Selective changes in mitochondria respiratory properties in oxidative or glycolytic muscle fibers isolated from G93AhumanSOD1 transgenic mice

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12 December 2020

The effects of focal ischemia and reperfusion on the glutathione content of mitochondria from rat brain subregions

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12 December 2020

Selective glutathione depletion of mitochondria by ethanol sensitizes hepatocytes to tumor necrosis factor

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12 December 2020

Motor neurons in Cu/Zn superoxide dismutase-deficient mice develop normally but exhibit enhanced cell death after axonal injury

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12 December 2020

Interaction between familial amyotrophic lateral sclerosis (ALS)-linked SOD1 mutants and the dynein complex

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12 December 2020

Glutathione depletion and neuronal cell death: the role of reactive oxygen intermediates and mitochondrial function

1 reference

12 December 2020

10.1007/S11064-009-9974-Z

Identifiers

DOI

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20 August 2017

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