(Q37905853)

25 August 2017

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title

Biochemical and strain properties of CJD prions: complexity versus simplicity (English)

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25 August 2017

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Stéphane Haïk

1

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25 August 2017

Jean-Philippe Brandel

series ordinal

2

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25 August 2017

language of work or name

English

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publication date

20 September 2011

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Journal of Neurochemistry

25 August 2017

published in

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25 August 2017

volume

119

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25 August 2017

issue

2

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25 August 2017

page(s)

251-261

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BSE prions propagate as either variant CJD-like or sporadic CJD-like prion strains in transgenic mice expressing human prion protein

25 August 2017

cites work

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Prominent and persistent extraneural infection in human PrP transgenic mice infected with variant CJD.

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Non-genetic propagation of strain-specific properties of scrapie prion protein.

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Predicting susceptibility and incubation time of human-to-human transmission of vCJD.

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Defining sporadic Creutzfeldt-Jakob disease strains and their transmission properties

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Variant Creutzfeldt-Jakob disease in France and the United Kingdom: Evidence for the same agent strain

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Variant or sporadic Creutzfeldt-Jakob disease?

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Normal host prion protein necessary for scrapie-induced neurotoxicity

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Iatrogenic Creutzfeldt-Jakob disease: the waning of an era.

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Transmissions to mice indicate that 'new variant' CJD is caused by the BSE agent

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Mice devoid of PrP are resistant to scrapie

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Co-existence of scrapie prion protein types 1 and 2 in sporadic Creutzfeldt-Jakob disease: its effect on the phenotype and prion-type characteristics

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Identification of a second bovine amyloidotic spongiform encephalopathy: molecular similarities with sporadic Creutzfeldt-Jakob disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

In vitro generation of infectious scrapie prions.

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Crossing the species barrier by PrP(Sc) replication in vitro generates unique infectious prions.

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Cell-free propagation of prion strains.

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Strain-dependent differences in beta-sheet conformations of abnormal prion protein

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Transmission and spreading of tauopathy in transgenic mouse brain

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Variant Creutzfeldt-Jakob disease.

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

A general model of prion strains and their pathogenicity

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Molecular analysis of prion strain variation and the aetiology of 'new variant' CJD.

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Kuru in the 21st century--an acquired human prion disease with very long incubation periods

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Atypical BSE (BASE) transmitted from asymptomatic aging cattle to a primate

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Prion strain- and species-dependent effects of antiprion molecules in primary neuronal cultures

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Prions: protein only or something more? Overview of potential prion cofactors

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Loss of cerebellar granule neurons is associated with punctate but not with large focal deposits of prion protein in Creutzfeldt-Jakob disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Conformational diversity of wild-type Tau fibrils specified by templated conformation change

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

A novel human disease with abnormal prion protein sensitive to protease

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Molecular biology and pathology of prion strains in sporadic human prion diseases.

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Resistance of bovine spongiform encephalopathy (BSE) prions to inactivation

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Human prion strain selection in transgenic mice

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

The sympathetic nervous system is involved in variant Creutzfeldt-Jakob disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Compassionate use of quinacrine in Creutzfeldt-Jakob disease fails to show significant effects

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Brain targeting through the autonomous nervous system: lessons from prion diseases

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Striking PrPsc heterogeneity in inherited prion diseases with the D178N mutation

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Neuropathologic variants of sporadic Creutzfeldt-Jakob disease and codon 129 of PrP gene.

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Prion protein heterogeneity in sporadic but not variant Creutzfeldt-Jakob disease: UK cases 1991-2002.

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

A case of protease sensitive prionopathy in a patient in the UK.

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Pathological investigation of the first blood donor and recipient pair linked by transfusion-associated variant Creutzfeldt-Jakob disease transmission

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Molecular classification of sporadic Creutzfeldt-Jakob disease.

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

The residue 129 polymorphism in human prion protein does not confer susceptibility to Creutzfeldt-Jakob disease by altering the structure or global stability of PrPC.

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Variant Creutzfeldt-Jakob disease: prion protein genotype analysis of positive appendix tissue samples from a retrospective prevalence study

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

The first case of protease-sensitive prionopathy (PSPr) in The Netherlands: a patient with an unusual GSS-like clinical phenotype

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

In vitro amplification and detection of variant Creutzfeldt-Jakob disease PrPSc.

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Effects of human PrPSc type and PRNP genotype in an in-vitro conversion assay

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Molecular model of prion transmission to humans

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Evidence for protein X binding to a discontinuous epitope on the cellular prion protein during scrapie prion propagation

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Autopsy case of Creutzfeldt-Jakob disease with Met/Val heterozygosity at codon 129 and type 1 protease-resistant prion protein presenting some florid-type plaques and many Kuru plaques in the cerebellum

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Plaque-type deposition of prion protein in the damaged white matter of sporadic Creutzfeldt-Jakob disease MM1 patients

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Experimental verification of a traceback phenomenon in prion infection

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Evaluation of the human transmission risk of an atypical bovine spongiform encephalopathy prion strain

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Abbreviated incubation times for human prions in mice expressing a chimeric mouse-human prion protein transgene

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Genetic prion disease: the EUROCJD experience

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

The N-terminal cleavage of cellular prion protein in the human brain

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Truncated PrP(c) in mammalian brain: interspecies variation and location in membrane rafts

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Risk of oral infection with bovine spongiform encephalopathy agent in primates

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Conformational diversity in prion protein variants influences intermolecular beta-sheet formation

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Regulating factors of PrP glycosylation in Creutzfeldt-Jakob disease--implications for the dissemination and the diagnosis of human prion strains

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Lewy bodies in grafted neurons in subjects with Parkinson's disease suggest host-to-graft disease propagation

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Possible transmission of variant Creutzfeldt-Jakob disease by blood transfusion.

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Long-duration sCJD with PRNP codon 129 methionine homozygosity and cerebral cortical plaques

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Depleting neuronal PrP in prion infection prevents disease and reverses spongiosis.

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Exogenous induction of cerebral beta-amyloidogenesis is governed by agent and host

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Standards for the assay of Creutzfeldt-Jakob disease specimens

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

The prion strain phenomenon: molecular basis and unprecedented features

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Developmental expression of the prion protein gene in glial cells

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Efficient transmission and characterization of Creutzfeldt-Jakob disease strains in bank voles

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Effects of different experimental conditions on the PrPSc core generated by protease digestion: implications for strain typing and molecular classification of CJD.

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Characterization of truncated forms of abnormal prion protein in Creutzfeldt-Jakob disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Is Parkinson's disease a prion disorder?

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Molecular basis of phenotypic variability in sporadic Creutzfeldt-Jakob disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

21 January 2018

Typing prion isoforms.

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Genetic influence on the structural variations of the abnormal prion protein

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Inter-laboratory assessment of PrPSc typing in creutzfeldt-jakob disease: a Western blot study within the NeuroPrion Consortium

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Incidence and spectrum of sporadic Creutzfeldt-Jakob disease variants with mixed phenotype and co-occurrence of PrPSc types: an updated classification

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Agent strain variation in human prion disease: insights from a molecular and pathological review of the National Institutes of Health series of experimentally transmitted disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Phenotypic variability of sporadic human prion disease and its molecular basis: past, present, and future

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Preclinical vCJD after blood transfusion in a PRNP codon 129 heterozygous patient

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Sporadic Creutzfeldt-Jakob disease: co-occurrence of different types of PrP(Sc) in the same brain

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Presymptomatic detection of prions in blood.

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Sensitive detection of pathological prion protein by cyclic amplification of protein misfolding

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Analysis of prion strains by PrPSc profiling in sporadic Creutzfeldt-Jakob disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Compelling transgenetic evidence for transmission of bovine spongiform encephalopathy prions to humans

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Humanized knock-in mice expressing chimeric prion protein showed varied susceptibility to different human prions

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Evidence for the conformation of the pathologic isoform of the prion protein enciphering and propagating prion diversity

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Discriminating scrapie and bovine spongiform encephalopathy isolates by infrared spectroscopy of pathological prion protein

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

The physical relationship between infectivity and prion protein aggregates is strain-dependent

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Beyond PrP9res) type 1/type 2 dichotomy in Creutzfeldt-Jakob disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Human prion protein with valine 129 prevents expression of variant CJD phenotype

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Risk factors for variant Creutzfeldt-Jakob disease: a case-control study

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

21 January 2018

The state of the prion

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

A new variant of Creutzfeldt-Jakob disease in the UK.

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Clinical presentation and pre-mortem diagnosis of variant Creutzfeldt-Jakob disease associated with blood transfusion: a case report.

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Detection of type 1 prion protein in variant Creutzfeldt-Jakob disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

NMR solution structure of the human prion protein

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Identification of distinct N-terminal truncated forms of prion protein in different Creutzfeldt-Jakob disease subtypes.

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Novel prion protein conformation and glycotype in Creutzfeldt-Jakob disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Variably protease-sensitive prionopathy: a new sporadic disease of the prion protein.

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Beyond the prion principle

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

The same prion strain causes vCJD and BSE

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

Diagnosis of new variant Creutzfeldt-Jakob disease by tonsil biopsy

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

BSE transmission to macaques

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2011.07399.X

10.1111/J.1471-4159.2011.07399.X

21 January 2018

Identifiers

DOI

1 reference

25 August 2017

1 reference