(Q38140444)

29 August 2017

Zebrafish as a model system for mitochondrial biology and diseases (English)

1 reference

29 August 2017

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Shelby L Steele

1

1 reference

PubMed ID

24055494

29 August 2017

Sergey V Prykhozhij

series ordinal

2

1 reference

PubMed ID

24055494

29 August 2017

Jason N Berman

series ordinal

3

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29 August 2017

20 September 2013

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29 August 2017

Translational Research

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29 August 2017

163

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29 August 2017

2

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29 August 2017

79-98

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The energetics of genome complexity

29 August 2017

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Mitochondria: in sickness and in health

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Sequence and organization of the human mitochondrial genome

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

A mitochondrial protein compendium elucidates complex I disease biology

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Apoptosis: a review of programmed cell death

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Mitochondrial formation of reactive oxygen species

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

How mitochondria produce reactive oxygen species

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Mitochondria in relation to cancer metastasis: introduction to a mini-review series

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Moving mitochondria: establishing distribution of an essential organelle

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

The axonal transport of mitochondria

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Fusion and fission: interlinked processes critical for mitochondrial health

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Human mitochondrial DNA: roles of inherited and somatic mutations

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Production of clones of homozygous diploid zebra fish (Brachydanio rerio)

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

The complete sequence of the zebrafish (Danio rerio) mitochondrial genome and evolutionary patterns in vertebrate mitochondrial DNA

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Mechanisms underlying metabolic and neural defects in zebrafish and human multiple acyl-CoA dehydrogenase deficiency (MADD).

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Complex I deficiency and dopaminergic neuronal cell loss in parkin-deficient zebrafish (Danio rerio).

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Discovery of genes essential for heme biosynthesis through large-scale gene expression analysis.

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Functional inhibition of UQCRB suppresses angiogenesis in zebrafish.

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

KBP is essential for axonal structure, outgrowth and maintenance in zebrafish, providing insight into the cellular basis of Goldberg-Shprintzen syndrome

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Loss of PINK1 function affects development and results in neurodegeneration in zebrafish

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Mutation of zebrafish dihydrolipoamide branched-chain transacylase E2 results in motor dysfunction and models maple syrup urine disease

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Mitochondrial trafficking in neurons

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Culling sick mitochondria from the herd

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

New insights into the function and regulation of mitochondrial fission

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Proton pump-rich cell secretes acid in skin of zebrafish larvae

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Oxidative stress and successful antioxidant treatment in models of RYR1-related myopathy

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Forward and reverse genetic approaches for the analysis of vertebrate development in the zebrafish

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Efficient target-selected mutagenesis in zebrafish

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Effective targeted gene 'knockdown' in zebrafish

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Heritable targeted gene disruption in zebrafish using designed zinc-finger nucleases

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Heritable gene targeting in zebrafish using customized TALENs.

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Efficient genome editing in zebrafish using a CRISPR-Cas system

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Simple and efficient transgenesis with meganuclease constructs in zebrafish.

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

The Tol2kit: a multisite gateway-based construction kit for Tol2 transposon transgenesis constructs

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Transposon-mediated BAC transgenesis in zebrafish.

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Transgenic zebrafish models of neurodegenerative diseases

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

The teleostean (zebrafish) dopaminergic system ascending to the subpallium (striatum) is located in the basal diencephalon (posterior tuberculum).

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Connections of the ventral telencephalon (subpallium) in the zebrafish (Danio rerio).

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Transgenic zebrafish expressing green fluorescent protein in dopaminergic neurons of the ventral diencephalon

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Dopaminergic cell damage and vulnerability to MPTP in Pink1 knockdown zebrafish

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Mitochondrial pathology in Parkinson's disease

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Mitochondrial function and morphology are impaired in parkin-mutant fibroblasts

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Mutant Parkin impairs mitochondrial function and morphology in human fibroblasts

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Down regulation of DJ-1 enhances cell death by oxidative stress, ER stress, and proteasome inhibition

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Leucine-rich repeat kinase 2 (LRRK2) interacts with parkin, and mutant LRRK2 induces neuronal degeneration

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Increased DJ-1 expression under oxidative stress and in Alzheimer's disease brains

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Impaired dopaminergic neuron development and locomotor function in zebrafish with loss of pink1 function

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Deletion of the WD40 domain of LRRK2 in Zebrafish causes Parkinsonism-like loss of neurons and locomotive defect

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Parkin is protective against proteotoxic stress in a transgenic zebrafish model

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Disruption of LRRK2 does not cause specific loss of dopaminergic neurons in zebrafish

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

A zebrafish model of PINK1 deficiency reveals key pathway dysfunction including HIF signaling

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Mutations of SURF-1 in Leigh disease associated with cytochrome c oxidase deficiency

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Early developmental pathology due to cytochrome c oxidase deficiency is revealed by a new zebrafish model

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

In vivo labeling of zebrafish motor neurons using an mnx1 enhancer and Gal4/UAS.

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Developmental defects and neuromuscular alterations due to mitofusin 2 gene (MFN2) silencing in zebrafish: a new model for Charcot-Marie-Tooth type 2A neuropathy

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Mutations in the mitochondrial GTPase mitofusin 2 cause Charcot-Marie-Tooth neuropathy type 2A

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Mitofusins Mfn1 and Mfn2 coordinately regulate mitochondrial fusion and are essential for embryonic development

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

The novel protein KBP regulates mitochondria localization by interaction with a kinesin-like protein

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Subcellular distribution of superoxide dismutases (SOD) in rat liver: Cu,Zn-SOD in mitochondria

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Mitochondria in amyotrophic lateral sclerosis: a trigger and a target

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

A genetic model of amyotrophic lateral sclerosis in zebrafish displays phenotypic hallmarks of motoneuron disease

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Overexpression of mutant superoxide dismutase 1 causes a motor axonopathy in the zebrafish

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

An adverse property of a familial ALS-linked SOD1 mutation causes motor neuron disease characterized by vacuolar degeneration of mitochondria

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Alsin is a Rab5 and Rac1 guanine nucleotide exchange factor

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Alsin is partially associated with centrosome in human cells

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

The first ALS2 missense mutation associated with JPLS reveals new aspects of alsin biological function

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Loss of ALS2/Alsin exacerbates motor dysfunction in a SOD1-expressing mouse ALS model by disturbing endolysosomal trafficking

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Als2 mRNA splicing variants detected in KO mice rescue severe motor dysfunction phenotype in Als2 knock-down zebrafish.

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Expression of the Opa1 mitochondrial protein in retinal ganglion cells: its downregulation causes aggregation of the mitochondrial network

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

The human dynamin-related protein OPA1 is anchored to the mitochondrial inner membrane facing the inter-membrane space

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

OPA3, mutated in 3-methylglutaconic aciduria type III, encodes two transcripts targeted primarily to mitochondria

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Opa1 is required for proper mitochondrial metabolism in early development

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

A model of Costeff Syndrome reveals metabolic and protective functions of mitochondrial OPA3.

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Unidirectional startle responses and disrupted left-right co-ordination of motor behaviors in robo3 mutant zebrafish.

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Behavioral genetic approaches to visual system development and function in zebrafish

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

A mutation in PNPT1, encoding mitochondrial-RNA-import protein PNPase, causes hereditary hearing loss

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Loss of Hspa9b in zebrafish recapitulates the ineffective hematopoiesis of the myelodysplastic syndrome

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Mitochondria in hematopoiesis and hematological diseases.

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

T-lymphoblastic lymphoma cells express high levels of BCL2, S1P1, and ICAM1, leading to a blockade of tumor cell intravasation.

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Congenital dyserythropoietic anemia

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Animal models of Diamond Blackfan anemia

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

BCDO2 acts as a carotenoid scavenger and gatekeeper for the mitochondrial apoptotic pathway

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

A mammalian siderophore synthesized by an enzyme with a bacterial homolog involved in enterobactin production

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Mitoferrin is essential for erythroid iron assimilation

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Abnormal mitoferrin-1 expression in patients with erythropoietic protoporphyria

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Mutations in mitochondrial carrier family gene SLC25A38 cause nonsyndromic autosomal recessive congenital sideroblastic anemia

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Positional cloning of the zebrafish sauternes gene: a model for congenital sideroblastic anaemia.

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Deficiency of glutaredoxin 5 reveals Fe-S clusters are required for vertebrate haem synthesis

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Mitochondrial Atpif1 regulates haem synthesis in developing erythroblasts

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Zebrafish dracula encodes ferrochelatase and its mutation provides a model for erythropoietic protoporphyria.

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

montalcino, A zebrafish model for variegate porphyria

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

GLUT10 is required for the development of the cardiovascular system and the notochord and connects mitochondrial function to TGFβ signaling

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

A zebrafish model of human Barth syndrome reveals the essential role of tafazzin in cardiac development and function

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

A novel mitochondrial matrix serine/threonine protein phosphatase regulates the mitochondria permeability transition pore and is essential for cellular survival and development

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

The mitochondrial citrate transporter, CIC, is essential for mitochondrial homeostasis

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Iron-sulfur proteins in health and disease

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

The human counterpart of zebrafish shiraz shows sideroblastic-like microcytic anemia and iron overload.

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Ineffective hematopoiesis linked with a mitochondrial tRNA mutation (G3242A) in a patient with myelodysplastic syndrome

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Mitochondrial DNA mutations in patients with myelodysplastic syndromes

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Mitochondria in vascular health and disease

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Vascular morphogenesis in the zebrafish embryo

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Zebrafish embryo, a tool to study tumor angiogenesis.

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Terpestacin inhibits tumor angiogenesis by targeting UQCRB of mitochondrial complex III and suppressing hypoxia-induced reactive oxygen species production and cellular oxygen sensing

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Mitochondrial GLUT10 facilitates dehydroascorbic acid import and protects cells against oxidative stress: mechanistic insight into arterial tortuosity syndrome

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

The human mitochondrial citrate transporter gene (SLC20A3) maps to chromosome band 22q11 within a region implicated in DiGeorge syndrome, velo-cardio-facial syndrome and schizophrenia

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Localization of the human mitochondrial citrate transporter protein gene to chromosome 22Q11 in the DiGeorge syndrome critical region

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

The schizophrenia phenotype in 22q11 deletion syndrome

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Incidence and prevalence of the 22q11 deletion syndrome: a population-based study in Western Sweden

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Glutaric acidemia type II: gene structure and mutations of the electron transfer flavoprotein:ubiquinone oxidoreductase (ETF:QO) gene

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Multiple acyl-CoA dehydrogenase deficiency (glutaric aciduria type II) with transient hypersarcosinemia and sarcosinuria; possible inherited deficiency of an electron transfer flavoprotein

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

Neuroradiologic findings in glutaric aciduria type II.

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.TRSL.2013.08.008

10.1016/J.TRSL.2013.08.008

7 January 2021

Identifiers

DOI

1 reference

29 August 2017

1 reference

PubMed ID

24055494