(Q40000489)

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:18353897%20AND%20SRC:MED&resulttype=core&format=json

4 January 2020

title

Inherited complex I deficiency is associated with faster protein diffusion in the matrix of moving mitochondria (English)

1 reference

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4 January 2020

1 reference

Werner J H Koopman

1

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4 January 2020

Mark A Hink

3

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4 January 2020

Sjoerd Verkaart

4

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4 January 2020

Mietske Wijers

5

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:18353897%20AND%20SRC:MED&resulttype=core&format=json

4 January 2020

Jack Fransen

6

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4 January 2020

Jan A M Smeitink

7

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4 January 2020

publication date

19 March 2008

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:18353897%20AND%20SRC:MED&resulttype=core&format=json

American Journal of Physiology - Cell Physiology

4 January 2020

published in

1 reference

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4 January 2020

volume

294

1 reference

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4 January 2020

issue

5

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4 January 2020

page(s)

C1124-32

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Coupling membranes as energy-transmitting cables. I. Filamentous mitochondria in fibroblasts and mitochondrial clusters in cardiomyocytes

4 January 2020

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Mutant NDUFV2 subunit of mitochondrial complex I causes early onset hypertrophic cardiomyopathy and encephalopathy

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Mutant NDUFS3 subunit of mitochondrial complex I causes Leigh syndrome

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21 January 2018

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21 January 2018

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Human CIA30 is involved in the early assembly of mitochondrial complex I and mutations in its gene cause disease

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Fluorescence correlation spectroscopy in small cytosolic compartments depends critically on the diffusion model used

21 January 2018

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21 January 2018

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21 January 2018

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Intracellular applications of fluorescence correlation spectroscopy: prospects for neuroscience

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NDUFS6 mutations are a novel cause of lethal neonatal mitochondrial complex I deficiency

21 January 2018

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Evidence that Ca2+-waves in Xenopus melanotropes depend on calcium-induced calcium release: a fluorescence correlation microscopy and linescanning study

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Inhibition of complex I of the electron transport chain causes O2-. -mediated mitochondrial outgrowth.

21 January 2018

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Mitochondrial network complexity and pathological decrease in complex I activity are tightly correlated in isolated human complex I deficiency.

21 January 2018

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Simultaneous quantitative measurement and automated analysis of mitochondrial morphology, mass, potential, and motility in living human skin fibroblasts.

21 January 2018

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Partial complex I inhibition decreases mitochondrial motility and increases matrix protein diffusion as revealed by fluorescence correlation spectroscopy.

21 January 2018

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Human NADH:ubiquinone oxidoreductase deficiency: radical changes in mitochondrial morphology?

21 January 2018

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Cycles of mitochondrial energization driven by the ultradian clock in a continuous culture of Saccharomyces cerevisiae

21 January 2018

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The first nuclear-encoded complex I mutation in a patient with Leigh syndrome

21 January 2018

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Mutations in the complex I NDUFS2 gene of patients with cardiomyopathy and encephalomyopathy

21 January 2018

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21 January 2018

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ADP regulates movements of mitochondria in neurons

21 January 2018

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A molecular chaperone for mitochondrial complex I assembly is mutated in a progressive encephalopathy

21 January 2018

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Monte Carlo analysis of obstructed diffusion in three dimensions: application to molecular diffusion in organelles

21 January 2018

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Lactic acidemia and mitochondrial disease

21 January 2018

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Energy substrate modulates mitochondrial structure and oxidative capacity in cancer cells

21 January 2018

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Mitochondrial morphology is dynamic and varied

21 January 2018

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C6ORF66 is an assembly factor of mitochondrial complex I

21 January 2018

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Dynamics, structure, and function are coupled in the mitochondrial matrix

21 January 2018

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Mutant NDUFV1 subunit of mitochondrial complex I causes leukodystrophy and myoclonic epilepsy

21 January 2018

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Fluorescence correlation spectroscopy reveals fast optical excitation-driven intramolecular dynamics of yellow fluorescent proteins

21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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Demonstration of a new pathogenic mutation in human complex I deficiency: a 5-bp duplication in the nuclear gene encoding the 18-kD (AQDQ) subunit

21 January 2018

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Superoxide production is inversely related to complex I activity in inherited complex I deficiency.

21 January 2018

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Mitochondrial and cytosolic thiol redox state are not detectably altered in isolated human NADH:ubiquinone oxidoreductase deficiency.

21 January 2018

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21 January 2018

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Inhibition of mitochondrial Na+-Ca2+ exchange restores agonist-induced ATP production and Ca2+ handling in human complex I deficiency.

21 January 2018

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Decreased agonist-stimulated mitochondrial ATP production caused by a pathological reduction in endoplasmic reticulum calcium content in human complex I deficiency

21 January 2018

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Impaired mitochondrial Ca2+ homeostasis in respiratory chain-deficient cells but efficient compensation of energetic disadvantage by enhanced anaerobic glycolysis due to low ATP steady state levels.

21 January 2018

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Mitochondrial Ca2+ homeostasis in human NADH:ubiquinone oxidoreductase deficiency.

21 January 2018

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Control of mitochondrial motility and distribution by the calcium signal: a homeostatic circuit

21 January 2018

1 reference

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10.1152/AJPCELL.00079.2008

21 January 2018

Identifiers

DOI

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:18353897%20AND%20SRC:MED&resulttype=core&format=json

4 January 2020

1 reference