(Q40108203)

17 September 2017

Chemical chaperones reduce endoplasmic reticulum stress and prevent mutant HFE aggregate formation (English)

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17 September 2017

endoplasmic reticulum

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1

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17 September 2017

Maria do Carmo Fonseca

4

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17 September 2017

Jorge E Azevedo

5

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Maria de Sousa

object named as

Maria de Sousa

6

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author name string

Gonçalo Picarote

2

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17 September 2017

John V Fleming

3

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17 September 2017

language of work or name

English

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publication date

11 July 2007

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Journal of Biological Chemistry

17 September 2017

8

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based on heuristic

inferred from page(s)

published in

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17 September 2017

282

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17 September 2017

38

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17 September 2017

27905-27912

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A novel MHC class I-like gene is mutated in patients with hereditary haemochromatosis

17 September 2017

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M702672200

The hemochromatosis founder mutation in HLA-H disrupts beta2-microglobulin interaction and cell surface expression

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M702672200

Hereditary hemochromatosis: effects of C282Y and H63D mutations on association with beta2-microglobulin, intracellular processing, and cell surface expression of the HFE protein in COS-7 cells

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M702672200

The hemochromatosis gene product complexes with the transferrin receptor and lowers its affinity for ligand binding

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M702672200

Influence of molecular and chemical chaperones on protein folding

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M702672200

Chemical chaperones correct the mutant phenotype of the delta F508 cystic fibrosis transmembrane conductance regulator protein

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M702672200

Protein-misfolding diseases and chaperone-based therapeutic approaches

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M702672200

Stimulation of an unfolded protein response impairs MHC class I expression

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M702672200

The mammalian unfolded protein response

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M702672200

Mammalian transcription factor ATF6 is synthesized as a transmembrane protein and activated by proteolysis in response to endoplasmic reticulum stress

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M702672200

ER stress regulation of ATF6 localization by dissociation of BiP/GRP78 binding and unmasking of Golgi localization signals

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M702672200

XBP1 mRNA is induced by ATF6 and spliced by IRE1 in response to ER stress to produce a highly active transcription factor

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M702672200

Human cytomegalovirus protein US2 interferes with the expression of human HFE, a nonclassical class I major histocompatibility complex molecule that regulates iron homeostasis

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M702672200

Mapping of catalytically important residues in the rat L-histidine decarboxylase enzyme using bioinformatic and site-directed mutagenesis approaches.

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M702672200

The production of 53-55-kDa isoforms is not required for rat L-histidine decarboxylase activity

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M702672200

Cleavage of Structural Proteins during the Assembly of the Head of Bacteriophage T4

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M702672200

Characterization and dynamics of aggresome formation by a cytosolic GFP-chimera

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M702672200

Protein misfolding, evolution and disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M702672200

Aggresomes, inclusion bodies and protein aggregation

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M702672200

In vitro pharmacologic restoration of CFTR-mediated chloride transport with sodium 4-phenylbutyrate in cystic fibrosis epithelial cells containing delta F508-CFTR.

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M702672200

Chemical chaperones mediate increased secretion of mutant alpha 1-antitrypsin (alpha 1-AT) Z: A potential pharmacological strategy for prevention of liver injury and emphysema in alpha 1-AT deficiency

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M702672200

Effect of tauroursodeoxycholic acid on endoplasmic reticulum stress-induced caspase-12 activation

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M702672200

Chemical chaperones reduce ER stress and restore glucose homeostasis in a mouse model of type 2 diabetes

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M702672200

Common structure and toxic function of amyloid oligomers implies a common mechanism of pathogenesis

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M702672200

Protofibrils, pores, fibrils, and neurodegeneration: separating the responsible protein aggregates from the innocent bystanders

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M702672200

Molecular chaperones and protein quality control

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M702672200

Molecular chaperones as modulators of polyglutamine protein aggregation and toxicity

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M702672200

Suppressive effects of 4-phenylbutyrate on the aggregation of Pael receptors and endoplasmic reticulum stress

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M702672200

21 January 2018

Identifiers

DOI

10.1074/JBC.M702672200

1 reference

17 September 2017

1 reference