(Q40290417)

19 September 2017

title

Cystamine and cysteamine prevent 3-NP-induced mitochondrial depolarization of Huntington's disease knock-in striatal cells (English)

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19 September 2017

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Zhengkuan Mao

1

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19 September 2017

Yeun Su Choo

series ordinal

2

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19 September 2017

Mathieu Lesort

series ordinal

3

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19 September 2017

language of work or name

English

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publication date

1 April 2006

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European Journal of Neuroscience

19 September 2017

published in

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19 September 2017

volume

23

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19 September 2017

issue

7

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19 September 2017

page(s)

1701-1710

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Identification of combinatorial drug regimens for treatment of Huntington's disease using Drosophila.

19 September 2017

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Tissue transglutaminase contributes to disease progression in the R6/2 Huntington's disease mouse model via aggregate-independent mechanisms

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Transglutaminase activity is related to CAG repeat length in patients with Huntington's disease

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Effect of exogenous and endogenous antioxidants on 3-nitropionic acid-induced in vivo oxidative stress and striatal lesions: insights into Huntington's disease

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Cystamine increases L-cysteine levels in Huntington's disease transgenic mouse brain and in a PC12 model of polyglutamine aggregation

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21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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'Tissue' transglutaminase ablation reduces neuronal death and prolongs survival in a mouse model of Huntington's disease

21 January 2018

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Treatment of YAC128 mice and their wild-type littermates with cystamine does not lead to its accumulation in plasma or brain: implications for the treatment of Huntington disease

21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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Cystamine treatment is neuroprotective in the YAC128 mouse model of Huntington disease.

21 January 2018

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21 January 2018

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10.1111/J.1460-9568.2006.04686.X

21 January 2018

Identifiers

DOI

1 reference

19 September 2017

1 reference