(Q40448063)

20 September 2017

title

Degradation of trafficking-defective long QT syndrome type II mutant channels by the ubiquitin-proteasome pathway. (English)

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ubiquitin-proteasome system

20 September 2017

main subject

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3

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20 September 2017

Qiuming Gong

1

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20 September 2017

David R Keeney

series ordinal

2

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20 September 2017

Zhengfeng Zhou

series ordinal

4

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20 September 2017

language of work or name

English

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publication date

10 March 2005

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Journal of Biological Chemistry

20 September 2017

number of pages

7

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based on heuristic

inferred from page(s)

published in

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20 September 2017

volume

280

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20 September 2017

issue

19

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20 September 2017

page(s)

19419-19425

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A molecular basis for cardiac arrhythmia: HERG mutations cause long QT syndrome

20 September 2017

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HERG, a Human Inward Rectifier in the Voltage-Gated Potassium Channel Family

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Long QT syndrome: cellular basis and arrhythmia mechanism in LQT2.

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EDEM as an acceptor of terminally misfolded glycoproteins released from calnexin

21 January 2018

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Degradation of CFTR by the ubiquitin-proteasome pathway

21 January 2018

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21 January 2018

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Newly synthesized human delta opioid receptors retained in the endoplasmic reticulum are retrotranslocated to the cytosol, deglycosylated, ubiquitinated, and degraded by the proteasome.

21 January 2018

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21 January 2018

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Pore formation is not associated with macroscopic redistribution of P2X7 receptors.

21 January 2018

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Intracellular disposal of incompletely folded human alpha1-antitrypsin involves release from calnexin and post-translational trimming of asparagine-linked oligosaccharides

21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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Sec61p mediates export of a misfolded secretory protein from the endoplasmic reticulum to the cytosol for degradation

21 January 2018

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Mutant analysis links the translocon and BiP to retrograde protein transport for ER degradation

21 January 2018

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Role of the proteasome in membrane extraction of a short-lived ER-transmembrane protein

21 January 2018

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Endoplasmic reticulum degradation of a mutated ATP-binding cassette transporter Pdr5 proceeds in a concerted action of Sec61 and the proteasome.

21 January 2018

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Protein dislocation from the ER requires polyubiquitination and the AAA-ATPase Cdc48.

21 January 2018

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The AAA ATPase Cdc48/p97 and its partners transport proteins from the ER into the cytosol

21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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Identification of proteins that interact with mammalian peptide:N-glycanase and implicate this hydrolase in the proteasome-dependent pathway for protein degradation

21 January 2018

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A role for N-glycanase in the cytosolic turnover of glycoproteins

21 January 2018

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A glycosylated type I membrane protein becomes cytosolic when peptide: N-glycanase is compromised

21 January 2018

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Episodic ataxia type-1 mutations in the Kv1.1 potassium channel display distinct folding and intracellular trafficking properties

21 January 2018

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Characterization and subcellular localization of KCNQ1 with a heterozygous mutation in the C terminus

21 January 2018

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New KCNQ1 mutations leading to haploinsufficiency in a general population; Defective trafficking of a KvLQT1 mutant.

21 January 2018

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21 January 2018

Identifiers

DOI

10.1074/JBC.M502327200

1 reference

20 September 2017

1 reference