(Q40489429)

English

Nonspecific interstitial pneumonia, alveolar proteinosis, and abnormal proprotein trafficking resulting from a spontaneous mutation in the surfactant protein C gene

scientific article

In more languages

Statements

scholarly article

1 reference

Europe PubMed Central

21 September 2017

Nonspecific interstitial pneumonia, alveolar proteinosis, and abnormal proprotein trafficking resulting from a spontaneous mutation in the surfactant protein C gene (English)

1 reference

Europe PubMed Central

21 September 2017

0 references

gene trafficking

1 reference

based on heuristic

inferred from title

nonspecific interstitial pneumonia

1 reference

based on heuristic

inferred from title

author name string

Paul A Stevens

1

1 reference

Europe PubMed Central

21 September 2017

Andrea Pettenazzo

2

1 reference

Europe PubMed Central

21 September 2017

Frank Brasch

3

1 reference

Europe PubMed Central

21 September 2017

Surafel Mulugeta

4

1 reference

Europe PubMed Central

21 September 2017

Aldo Baritussio

5

1 reference

Europe PubMed Central

21 September 2017

Matthias Ochs

6

1 reference

Europe PubMed Central

21 September 2017

Lake Morrison

7

1 reference

Europe PubMed Central

21 September 2017

Scott J Russo

8

1 reference

Europe PubMed Central

21 September 2017

Michael F Beers

9

1 reference

Europe PubMed Central

21 September 2017

language of work or name

0 references

publication date

19 November 2004

1 reference

Europe PubMed Central

21 September 2017

Pediatric Research

1 reference

Europe PubMed Central

21 September 2017

57

1 reference

Europe PubMed Central

21 September 2017

1

1 reference

Europe PubMed Central

21 September 2017

89-98

1 reference

Europe PubMed Central

21 September 2017

https://scigraph.springernature.com/pub.10.1203/01.pdr.0000147567.02473.5a

0 references

Pulmonary surfactant in health and human lung diseases: state of the art.

1 reference

https://api.crossref.org/works/10.1203%2F01.PDR.0000147567.02473.5A

21 January 2018

Total extracellular surfactant is increased but abnormal in a rat model of gram-negative bacterial pneumonia.

1 reference

https://api.crossref.org/works/10.1203%2F01.PDR.0000147567.02473.5A

21 January 2018

Aspergillus fumigatus-induced allergic airway inflammation alters surfactant homeostasis and lung function in BALB/c mice

1 reference

https://api.crossref.org/works/10.1203%2F01.PDR.0000147567.02473.5A

21 January 2018

Pulmonary alveolar proteinosis: progress in the first 44 years

1 reference

https://api.crossref.org/works/10.1203%2F01.PDR.0000147567.02473.5A

21 January 2018

The pulmonary collectins and surfactant metabolism

1 reference

https://api.crossref.org/works/10.1203%2F01.PDR.0000147567.02473.5A

21 January 2018

Function of surfactant proteins B and C

1 reference

https://api.crossref.org/works/10.1203%2F01.PDR.0000147567.02473.5A

21 January 2018

Synthesis and post-translational processing of surfactant protein C

1 reference

https://api.crossref.org/works/10.1203%2F01.PDR.0000147567.02473.5A

21 January 2018

Post-translational processing of surfactant protein-C proprotein: targeting motifs in the NH(2)-terminal flanking domain are cleaved in late compartments

1 reference

https://api.crossref.org/works/10.1203%2F01.PDR.0000147567.02473.5A

21 January 2018

Altered stability of pulmonary surfactant in SP-C-deficient mice

1 reference

https://api.crossref.org/works/10.1203%2F01.PDR.0000147567.02473.5A

21 January 2018

Pneumonitis and emphysema in sp-C gene targeted mice.

1 reference

https://api.crossref.org/works/10.1203%2F01.PDR.0000147567.02473.5A

21 January 2018

Heterozygosity for a surfactant protein C gene mutation associated with usual interstitial pneumonitis and cellular nonspecific interstitial pneumonitis in one kindred

1 reference

https://api.crossref.org/works/10.1203%2F01.PDR.0000147567.02473.5A

21 January 2018

A mutation in the surfactant protein C gene associated with familial interstitial lung disease

1 reference

https://api.crossref.org/works/10.1203%2F01.PDR.0000147567.02473.5A

21 January 2018

BRICHOS: a conserved domain in proteins associated with dementia, respiratory distress and cancer

1 reference

https://api.crossref.org/works/10.1203%2F01.PDR.0000147567.02473.5A

21 January 2018

Deletion of exon 4 from human surfactant protein C results in aggresome formation and generation of a dominant negative

1 reference

https://api.crossref.org/works/10.1203%2F01.PDR.0000147567.02473.5A

21 January 2018

Expression of a Human Surfactant Protein C Mutation Associated with Interstitial Lung Disease Disrupts Lung Development in Transgenic Mice

1 reference

https://api.crossref.org/works/10.1203%2F01.PDR.0000147567.02473.5A

21 January 2018

An ELISA technique for quantification of surfactant apoprotein (SP)-C in bronchoalveolar lavage fluid

1 reference

https://api.crossref.org/works/10.1203%2F01.PDR.0000147567.02473.5A

21 January 2018

Human surfactant protein-C: genetic homogeneity and expression in RDS; comparison with other species

1 reference

https://api.crossref.org/works/10.1203%2F01.PDR.0000147567.02473.5A

21 January 2018

Low molecular weight human pulmonary surfactant protein (SP5): isolation, characterization, and cDNA and amino acid sequences

1 reference

https://api.crossref.org/works/10.1203%2F01.PDR.0000147567.02473.5A

21 January 2018

Tricine-sodium dodecyl sulfate-polyacrylamide gel electrophoresis for the separation of proteins in the range from 1 to 100 kDa

1 reference

https://api.crossref.org/works/10.1203%2F01.PDR.0000147567.02473.5A

21 January 2018

Involvement of cathepsin H in the processing of the hydrophobic surfactant-associated protein C in type II pneumocytes

1 reference

https://api.crossref.org/works/10.1203%2F01.PDR.0000147567.02473.5A

21 January 2018

Synthetic processing of surfactant protein C by alevolar epithelial cells. The COOH terminus of proSP-C is required for post-translational targeting and proteolysis

1 reference

https://api.crossref.org/works/10.1203%2F01.PDR.0000147567.02473.5A

21 January 2018

Biosynthesis of surfactant protein C (SP-C). Sorting of SP-C proprotein involves homomeric association via a signal anchor domain

1 reference

https://api.crossref.org/works/10.1203%2F01.PDR.0000147567.02473.5A

21 January 2018

Alpha1-antitrypsin deficiency--a model for conformational diseases

1 reference

https://api.crossref.org/works/10.1203%2F01.PDR.0000147567.02473.5A

21 January 2018

Conformational disease

1 reference

https://api.crossref.org/works/10.1203%2F01.PDR.0000147567.02473.5A

21 January 2018

Protein processing and degradation in pulmonary health and disease.

1 reference

https://api.crossref.org/works/10.1203%2F01.PDR.0000147567.02473.5A

21 January 2018

A decamer duplication in the 3' region of the BRI gene originates an amyloid peptide that is associated with dementia in a Danish kindred

1 reference

https://api.crossref.org/works/10.1203%2F01.PDR.0000147567.02473.5A

21 January 2018

Interstitial pneumonia in Hermansky-Pudlak syndrome: significance of florid foamy swelling/degeneration (giant lamellar body degeneration) of type-2 pneumocytes.

1 reference

https://api.crossref.org/works/10.1203%2F01.PDR.0000147567.02473.5A

21 January 2018

Interstitial lung disease in a baby with a de novo mutation in the SFTPC gene

1 reference

https://api.crossref.org/works/10.1203%2F01.PDR.0000147567.02473.5A

21 January 2018

Aggresomes, inclusion bodies and protein aggregation

1 reference

https://api.crossref.org/works/10.1203%2F01.PDR.0000147567.02473.5A

21 January 2018

Endocrinopathies in the family of endoplasmic reticulum (ER) storage diseases: disorders of protein trafficking and the role of ER molecular chaperones

1 reference

https://api.crossref.org/works/10.1203%2F01.PDR.0000147567.02473.5A

21 January 2018

Early endosomes are required for major histocompatiblity complex class II transport to peptide-loading compartments

1 reference

https://api.crossref.org/works/10.1203%2F01.PDR.0000147567.02473.5A

21 January 2018

Intracellular accumulation of amyloidogenic fragments of amyloid-beta precursor protein in neurons with Niemann-Pick type C defects is associated with endosomal abnormalities

1 reference

https://api.crossref.org/works/10.1203%2F01.PDR.0000147567.02473.5A

21 January 2018

Membrane properties and amyloid fibril formation of lung surfactant protein C.

1 reference

https://api.crossref.org/works/10.1203%2F01.PDR.0000147567.02473.5A

21 January 2018

Proteolytic generation and aggregation of peptides from transmembrane regions: lung surfactant protein C and amyloid beta-peptide

1 reference

https://api.crossref.org/works/10.1203%2F01.PDR.0000147567.02473.5A

21 January 2018

Identifiers

10.1203/01.PDR.0000147567.02473.5A

1 reference

Europe PubMed Central

21 September 2017

Dimensions Publication ID

0 references

release_tu4bsehp5fcahh35rvhxhk3a7y

1 reference

https://api.fatcat.wiki/v0/release/tu4bsehp5fcahh35rvhxhk3a7y

24 November 2022

based on heuristic

mapped directly with Wikidata item

1 reference

Europe PubMed Central

21 September 2017

Sitelinks

Wikipedia(0 entries)

Wikibooks(0 entries)

Wikinews(0 entries)

Wikiquote(0 entries)

Wikisource(0 entries)

Wikiversity(0 entries)

Wikivoyage(0 entries)

Wiktionary(0 entries)

Multilingual sites(0 entries)

Retrieved from "https://www.wikidata.org/w/index.php?title=Q40489429&oldid=1898124144"