(Q41033190)

25 September 2017

title

Decreased membrane fluidity and unsaturated fatty acids in Niemann-Pick disease type C fibroblasts (English)

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Niemann-Pick disease, type C1

25 September 2017

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1

T Koike

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25 September 2017

G Ishida

2

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25 September 2017

M Taniguchi

3

1 reference

25 September 2017

K Higaki

4

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25 September 2017

Y Ayaki

5

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25 September 2017

M Saito

6

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25 September 2017

Y Sakakihara

7

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25 September 2017

M Iwamori

8

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25 September 2017

K Ohno

9

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25 September 2017

publication date

1 April 1998

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Biochimica et Biophysica Acta

25 September 2017

published in

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25 September 2017

volume

1406

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25 September 2017

issue

3

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25 September 2017

page(s)

327-335

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Complementation studies in Niemann-Pick disease type C indicate the existence of a second group

25 September 2017

cites work

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2898%2900019-2

7 January 2021

Linkage of Niemann-Pick disease type C to human chromosome 18

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2898%2900019-2

7 January 2021

Niemann-Pick C1 disease gene: homology to mediators of cholesterol homeostasis

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2898%2900019-2

7 January 2021

A lysosomal storage disorder in mice characterized by a dual deficiency of sphingomyelinase and glucocerebrosidase

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2898%2900019-2

7 January 2021

Sphingomyelinosis, a new mutation in the mouse: a model of Niemann-Pick disease in humans.

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2898%2900019-2

7 January 2021

Restoration of the cholesterol metabolism in 3T3 cell lines derived from the sphingomyelinosis mouse (spm/spm) by transfer of a human chromosome 18.

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2898%2900019-2

7 January 2021

A C57BL/KsJ mouse model of Niemann-Pick disease (spm) belongs to the same complementation group as the major childhood type of Niemann-Pick disease type C.

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2898%2900019-2

7 January 2021

Murine model of Niemann-Pick C disease: mutation in a cholesterol homeostasis gene

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2898%2900019-2

7 January 2021

Altered sensitivities to potential inhibitors of cholesterol biosynthesis in Niemann-Pick type C fibroblasts

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2898%2900019-2

7 January 2021

A collagen-binding glycoprotein on the surface of mouse fibroblasts is identified as dipeptidyl peptidase IV.

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2898%2900019-2

7 January 2021

A rapid and sensitive method for the quantitation of microgram quantities of protein utilizing the principle of protein-dye binding

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2898%2900019-2

7 January 2021

Evidence for de novo synthesis of phosphatidylinositol coupled with histamine release in activated rat mast cells

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2898%2900019-2

7 January 2021

Ganglioside-composition of brain in Tay-Sachs disease: increased amounts of GD2 and N-acetyl-beta-D-galactosaminyl GD1a ganglioside

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2898%2900019-2

7 January 2021

Preparation of methyl esters from the saponifiable fatty acids in small biological specimens for gas-liquid chromatographic analysis

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2898%2900019-2

7 January 2021

Effects of peroxisomal beta-oxidation antagonist on 2',3'-cyclic-nucleotide 3'-phosphohydrolase, membrane lipid compositions, and membrane fluidity in C-6 glial cells

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2898%2900019-2

7 January 2021

Dynamic structure of lipid bilayers studied by nanosecond fluorescence techniques

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2898%2900019-2

7 January 2021

Biochemical studies in Niemann-Pick disease. I. Major sphingolipids of liver and spleen

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2898%2900019-2

7 January 2021

Time course of hepatic lipids accumulation in a strain of mice with an inherited deficiency of sphingomyelinase

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2898%2900019-2

7 January 2021

Intracellular cholesterol transport and compartmentation

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2898%2900019-2

7 January 2021

Niemann-Pick type II fibroblasts exhibit impaired cholesterol esterification in response to sphingomyelin hydrolysis

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2898%2900019-2

7 January 2021

Increased expression of caveolin-1 in heterozygous Niemann-Pick type II human fibroblasts

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2898%2900019-2

7 January 2021

Free sphingoid bases in tissues from patients with type C Niemann-Pick disease and other lysosomal storage disorders

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2898%2900019-2

7 January 2021

Changes in the levels of dolichol and dolichyl phosphate in a murine model of Niemann-Pick's type C disease

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2898%2900019-2

7 January 2021

Peroxisomal impairment in Niemann-Pick type C disease.

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2898%2900019-2

7 January 2021

The modification of mammalian membrane polyunsaturated fatty acid composition in relation to membrane fluidity and function

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2898%2900019-2

7 January 2021

10.1016/S0925-4439(98)00019-2

Identifiers

DOI

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25 September 2017

1 reference