(Q41975415)

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:16686602%20AND%20SRC:MED&resulttype=core&format=json

21 January 2020

title

Secondary mitochondrial dysfunction in propionic aciduria: a pathogenic role for endogenous mitochondrial toxins (English)

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:16686602%20AND%20SRC:MED&resulttype=core&format=json

21 January 2020

5

1 reference

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21 January 2020

Ulrich Brandt

8

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:16686602%20AND%20SRC:MED&resulttype=core&format=json

21 January 2020

Lambert P van den Heuvel

6

object named as

Lambert P van den Heuvel

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:16686602%20AND%20SRC:MED&resulttype=core&format=json

21 January 2020

12

Jan A M Smeitink

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:16686602%20AND%20SRC:MED&resulttype=core&format=json

21 January 2020

10

Henk Ter Laak

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:16686602%20AND%20SRC:MED&resulttype=core&format=json

21 January 2020

4

Leo G J Nijtmans

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:16686602%20AND%20SRC:MED&resulttype=core&format=json

21 January 2020

author name string

Marina A Schwab

1

1 reference

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21 January 2020

Sven W Sauer

2

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:16686602%20AND%20SRC:MED&resulttype=core&format=json

21 January 2020

Jürgen G Okun

3

1 reference

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21 January 2020

Stefan Dröse

7

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:16686602%20AND%20SRC:MED&resulttype=core&format=json

21 January 2020

Georg F Hoffmann

9

1 reference

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21 January 2020

Stefan Kölker

11

1 reference

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21 January 2020

language of work or name

English

0 references

publication date

1 August 2006

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:16686602%20AND%20SRC:MED&resulttype=core&format=json

21 January 2020

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:16686602%20AND%20SRC:MED&resulttype=core&format=json

21 January 2020

volume

398

1 reference

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21 January 2020

issue

1

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:16686602%20AND%20SRC:MED&resulttype=core&format=json

21 January 2020

page(s)

107-112

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:16686602%20AND%20SRC:MED&resulttype=core&format=json

The mitochondrial genome in human adaptive radiation and disease: on the road to therapeutics and performance enhancement

21 January 2020

cites work

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1525008

Deficiency of the ADP-forming succinyl-CoA synthase activity is associated with encephalomyopathy and mitochondrial DNA depletion

5 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1525008

Methylmalonic acid--an endogenous toxin?

5 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1525008

Deoxyribonucleotides and disorders of mitochondrial DNA integrity.

5 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1525008

Protein measurement with the Folin phenol reagent

5 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1525008

Methylmalonic acid, a biochemical hallmark of methylmalonic acidurias but no inhibitor of mitochondrial respiratory chain

5 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1525008

Defects of pyruvate metabolism and the Krebs cycle.

5 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1525008

Blue Native electrophoresis to study mitochondrial and other protein complexes

5 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1525008

Neurodegeneration in methylmalonic aciduria involves inhibition of complex II and the tricarboxylic acid cycle, and synergistically acting excitotoxicity

5 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1525008

Fatal propionic acidemia in mice lacking propionyl-CoA carboxylase and its rescue by postnatal, liver-specific supplementation via a transgene

5 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1525008

CT and MR of the brain in disorders of the propionate and methylmalonate metabolism

5 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1525008

Disorders of the mitochondrial respiratory chain: clinical manifestations and diagnostic approach

5 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1525008

Effect of 2-Methylcitrate on Citrate Metabolism: Implications for the Management of Patients with Propionic acidemia and Methylmalonic aciduria

5 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1525008

Bioenergetics in glutaryl-coenzyme A dehydrogenase deficiency: a role for glutaryl-coenzyme A.

5 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1525008

Optimized spectrophotometric assay for the completely activated pyruvate dehydrogenase complex in fibroblasts

18 August 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1525008

On the mechanism of action of the antifungal agent propionate.

18 August 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1525008

Studies of propionate toxicity in Salmonella enterica identify 2-methylcitrate as a potent inhibitor of cell growth

18 August 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1525008

Propionic and L-methylmalonic acids induce oxidative stress in brain of young rats.

18 August 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1525008

Three classes of inhibitors share a common binding domain in mitochondrial complex I (NADH:ubiquinone oxidoreductase).

18 August 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1525008

The specific inhibition of the pyruvate dehydrogenase complex from pig kidney by propionyl-CoA and isovaleryl-Co-A

18 August 2018

1 reference

12 December 2020

Isolation of the eleven protein subunits of the bc1 complex from beef heart

1 reference

12 December 2020

Measurement of totally activated pyruvate dehydrogenase complex activity in human muscle: evaluation of a useful assay

1 reference

12 December 2020

Role of Deprotonation Events in Ubihydroquinone:CytochromecOxidoreductase from Bovine Heart and Yeast Mitochondria

1 reference

12 December 2020

Identifiers

DOI

10.1042/BJ20060221

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:16686602%20AND%20SRC:MED&resulttype=core&format=json

21 January 2020

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:16686602%20AND%20SRC:MED&resulttype=core&format=json

21 January 2020

1 reference