(Q42066758)

16 October 2017

Abnormalities in the pulmonary innate immune system in cystic fibrosis (English)

1 reference

16 October 2017

0 references

13

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16 October 2017

12

Sergio Grinstein

1 reference

16 October 2017

Theo J Moraes

1

1 reference

16 October 2017

Jonathan Plumb

2

1 reference

16 October 2017

Raiza Martin

3

1 reference

16 October 2017

Eric Vachon

4

1 reference

16 October 2017

Vera Cherepanov

5

1 reference

16 October 2017

Adeline Koh

6

1 reference

16 October 2017

Carola Loeve

7

1 reference

16 October 2017

Jenny Jongstra-Bilen

8

1 reference

16 October 2017

Joanna H Zurawska

9

1 reference

16 October 2017

Julianne V Kus

10

1 reference

16 October 2017

Lori L Burrows

11

1 reference

16 October 2017

language of work or name

1 reference

17 November 2005

1 reference

American Journal of Respiratory Cell and Molecular Biology

16 October 2017

1 reference

16 October 2017

34

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16 October 2017

3

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16 October 2017

364-374

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Potential for antioxidant therapy of cystic fibrosis

16 October 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2644201

Loss of microbicidal activity and increased formation of biofilm due to decreased lactoferrin activity in patients with cystic fibrosis.

5 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2644201

Increased airway epithelial Na+ absorption produces cystic fibrosis-like lung disease in mice

5 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2644201

New concepts of the pathogenesis of cystic fibrosis lung disease

5 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2644201

Abnormal surface liquid pH regulation by cultured cystic fibrosis bronchial epithelium

5 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2644201

Pathophysiology and Management of Pulmonary Infections in Cystic Fibrosis

5 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2644201

The role of regulated CFTR trafficking in epithelial secretion

5 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2644201

Points of control in inflammation

5 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2644201

Role of airway surface liquid and submucosal glands in cystic fibrosis lung disease

5 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2644201

The neutrophil NADPH oxidase

5 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2644201

Phagocytosis and innate immunity

5 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2644201

Early pulmonary infection, inflammation, and clinical outcomes in infants with cystic fibrosis

5 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2644201

Submucosal gland secretions in airways from cystic fibrosis patients have normal [Na(+)] and pH but elevated viscosity

5 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2644201

Rethinking cystic fibrosis pathology: the critical role of abnormal reduced glutathione (GSH) transport caused by CFTR mutation

5 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2644201

Role of the cystic fibrosis transmembrane conductance regulator in innate immunity to Pseudomonas aeruginosa infections

5 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2644201

Activity of abundant antimicrobials of the human airway

5 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2644201

Cystic fibrosis and the salt controversy

5 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2644201

Evidence for periciliary liquid layer depletion, not abnormal ion composition, in the pathogenesis of cystic fibrosis airways disease

5 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2644201

Human beta-defensin 2 is a salt-sensitive peptide antibiotic expressed in human lung

5 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2644201

Glutathione permeability of CFTR.

5 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2644201

Neutrophil adhesion molecule surface expression and responsiveness in cystic fibrosis.

5 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2644201

Mouse beta-defensin 1 is a salt-sensitive antimicrobial peptide present in epithelia of the lung and urogenital tract

5 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2644201

Current concepts about neutrophil granule physiology

5 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2644201

Lower airway inflammation in infants and young children with cystic fibrosis.

5 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2644201

Human beta-defensin-1 is a salt-sensitive antibiotic in lung that is inactivated in cystic fibrosis

5 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2644201

Increased DNA levels in bronchoalveolar lavage fluid obtained from infants with cystic fibrosis

5 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2644201

Cystic fibrosis airway epithelia fail to kill bacteria because of abnormal airway surface fluid.

5 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2644201

Desensitisation of neutrophil responses by systemic interleukin 8 in cystic fibrosis

5 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2644201

Increased sulfation of glycoconjugates by cultured nasal epithelial cells from patients with cystic fibrosis

5 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2644201

Identification of the cystic fibrosis gene: genetic analysis

5 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2644201

Generation and metabolism of leukotrienes in granulocytes of patients with cystic fibrosis

5 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2644201

Cystic fibrosis: current survival and population estimates to the year 2000.

5 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2644201

Expression of the cystic fibrosis transmembrane conductance regulator gene in cells of non-epithelial origin

5 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2644201

Increased Monocyte Oxidase Activity in Cystic Fibrosis Heterozygotes and Homozygotes

5 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2644201

Improvement of alveolar glutathione and lung function but not oxidative state in cystic fibrosis

5 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2644201

Inhibition of human surfactant protein A function by oxidation intermediates of nitrite

17 August 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2644201

An in vitro model of differentiated human airway epithelia. Methods for establishing primary cultures.

17 August 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2644201

Salt-independent abnormality of antimicrobial activity in cystic fibrosis airway surface fluid

17 August 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2644201

Antioxidant imbalance in the lungs of cystic fibrosis transmembrane conductance regulator protein mutant mice

17 August 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2644201

Role of CFTR in airway disease

17 August 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2644201

Cystic fibrosis: a multiple exocrinopathy caused by dysfunctions in a multifunctional transport protein

17 August 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2644201

Determinants of mortality from cystic fibrosis in Canada, 1970-1989.

17 August 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2644201

Decreased polymorphonuclear leucocyte chemotactic response to leukotriene B4 in cystic fibrosis

17 August 2018

1 reference

12 December 2020

Potentiation of the oxidative burst of human neutrophils. A signaling role for L-selectin

1 reference

12 December 2020

Bronchoalveolar lavage findings in cystic fibrosis patients with stable, clinically mild lung disease suggest ongoing infection and inflammation

1 reference

12 December 2020

Early pulmonary inflammation in infants with cystic fibrosis

1 reference

12 December 2020

Cystic fibrosis lung inflammation: early, sustained, and severe

1 reference

12 December 2020

Increased degranulation of eosinophil and neutrophil granulocytes in cystic fibrosis

1 reference

12 December 2020

Effects of sodium concentration on human neutrophil bactericidal functions

1 reference

12 December 2020

The relationship between infection and inflammation in the early stages of lung disease from cystic fibrosis

1 reference

12 December 2020

Distinct cytokine production by lung and blood neutrophils from children with cystic fibrosis

1 reference

12 December 2020

Normal alveolar epithelial lining fluid contains high levels of glutathione

1 reference

12 December 2020

Activation of permeabilized neutrophils: role of anions

1 reference

12 December 2020

Disturbed myeloperoxidase-dependent activity of neutrophils in cystic fibrosis homozygotes and heterozygotes, and its correction by amiloride

1 reference

12 December 2020

1 reference

12 December 2020

Nasal and bronchoalveolar lavage fluid cytokines in early cystic fibrosis

1 reference

12 December 2020

Bispecific antibodies overcome the opsonin-receptor mismatch of cystic fibrosis in vitro: restoration of neutrophil-mediated phagocytosis and killing of Pseudomonas aeruginosa

1 reference

12 December 2020

The effect of chloride concentration on human neutrophil functions: potential relevance to cystic fibrosis

1 reference

12 December 2020

Effects of ion composition and tonicity on human neutrophil antibacterial activity

1 reference

12 December 2020

Increased elastase release by CF neutrophils is mediated by tumor necrosis factor-alpha and interleukin-8

1 reference

12 December 2020

Altered intracellular pH regulation in neutrophils from patients with cystic fibrosis

1 reference

12 December 2020

1 reference

12 December 2020

Systemic deficiency of glutathione in cystic fibrosis

1 reference

12 December 2020

Identifiers

DOI

10.1165/RCMB.2005-0146OC

1 reference

16 October 2017

1 reference

16 October 2017

PubMed publication ID

16293782

1 reference